Alternative Method for Full Oral Rehabilitation in Patients with Pycnodysostosis Syndrome: A Case Report.
| Autor: | Costa MM; Federal University of Uberlândia, School of Dentistry, Uberlândia, MG, Brazil., Pennisi PRC; Federal University of Uberlândia, School of Dentistry, Uberlândia, MG, Brazil., de Oliveira ACZM; Private Clinic, Uberlândia, Brazil., de Oliveira JEC; Federal University of Uberlândia, School of Dentistry, Uberlândia, MG, Brazil., Oliveira GV; Federal University of Uberlândia, School of Mechanical Engineering, Uberlândia, MG, Brazil., Moffa EB; University Center - UNIFAE, School of Dentistry, São João da Boa Vista, SP, Brazil., Paranhos LR; Federal University of Uberlândia, School of Dentistry, Uberlândia, MG, Brazil. |
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| Jazyk: | angličtina |
| Zdroj: | Clinical, cosmetic and investigational dentistry [Clin Cosmet Investig Dent] 2020 Apr 15; Vol. 12, pp. 131-139. Date of Electronic Publication: 2020 Apr 15 (Print Publication: 2020). |
| DOI: | 10.2147/CCIDE.S247614 |
| Abstrakt: | Pycnodysostosis (PYCD) is a rare autosomal recessive skeletal dysplasia arising from a change in the production of the cathepsin K enzyme and it is also known as Maroteaux-Lamy Syndrome. The main changes in the buccal and maxillofacial region are modifications of the facial bones (leading to the loss of the mandibular angle due to micrognathia), deep palate, premature and/or delayed tooth eruption, hypopneumatization of the maxillary sinuses, chin hypoplasia, hypercementosis, enamel hypoplasia, hyperdontia, incomplete dentin calcification, root hypoplasia, pulp chamber obliteration, and increased free functional space. This paper aims to report a case of a patient with PYCD, in which are highlighted the oral manifestations of this syndrome and present an option of oral rehabilitative treatment through a removable overdenture made on natural tooth of the patient. The technique of dental coating through overdenture is a simple, viable and conservative alternative for oral rehabilitation of patients with large maxillomandibular discrepancies, as in cases of pycnodysostosis, especially in the presence of increased free space - characteristic of patients with this syndrome. The result was quite satisfactory both aesthetically and functionally and provided a better life quality for the patient. Competing Interests: The authors report no conflicts of interest in this work. (© 2020 Costa et al.) |
| Databáze: | MEDLINE |
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