Cardiac Paraganglioma in a 14-Year-Old.

Autor: Bansal N; Division of Cardiology, 2969Children's Hospital of Michigan, Wayne State University School of Medicine, Detroit, MI, USA., Walters HL 3rd; Division of Cardiothoracic Surgery, 2969Children's Hospital of Michigan, Detroit, MI, USA., Aggarwal S; Division of Cardiology, 2969Children's Hospital of Michigan, Wayne State University School of Medicine, Detroit, MI, USA.
Jazyk: angličtina
Zdroj: World journal for pediatric & congenital heart surgery [World J Pediatr Congenit Heart Surg] 2021 May; Vol. 12 (3), pp. 433-436. Date of Electronic Publication: 2019 May 14.
DOI: 10.1177/2150135118824077
Abstrakt: Cardiac paraganglioma (PGL) is a rare catecholamine-secreting tumor forming 1% to 3% of cardiac tumors. Although most PGL occur sporadically, evidence exists that 40% of them may be related to familial cancer predisposition syndromes. We present a unique case of a 14-year-old female who presented with persistent hypertension and was found to have a cardiac PGL. During surgical resection, even though the main right coronary was preserved, the sinoatrial (SA) nodal artery was surrounded by the tumor and required resection with the tumor. The patient subsequently developed SA node dysfunction and is currently being evaluated for placement of a permanent pacemaker.
Databáze: MEDLINE