Fast Progressing His-Purkinje Conduction Disturbances in a Myotonic Dystrophy Pacient.

Autor: Ciudin RN; 4th Clinic of Cardiology, 'C. C. Iliescu' Institute of Cardiovascular Diseases, Bucharest, Romania., Dragatoiu NC; 4th Clinic of Cardiology, 'C. C. Iliescu' Institute of Cardiovascular Diseases, Bucharest, Romania., Sipos S; 4th Clinic of Cardiology, 'C. C. Iliescu' Institute of Cardiovascular Diseases, Bucharest, Romania., Tesloianu DN; Cardiology Department, 'Sf. Spiridon' University Emergency Hospital, Iasi, Romania., Ursaru AM; Cardiology Department, 'Sf. Spiridon' University Emergency Hospital, Iasi, Romania., Brezeanu R; Cardiology Department, University and Emergency Hospital, Bucharest, Romania., Coman IM; 'Carol Davila' University of Medicine and Pharmacy, Bucharest, Romania.
Jazyk: angličtina
Zdroj: Maedica [Maedica (Bucur)] 2018 Jun; Vol. 13 (2), pp. 152-154.
DOI: 10.26574/maedica.2018.13.2.152
Abstrakt: Myotonic dystrophy leads to multiple systemic complications and the age of death is earlier in myotonic dystrophy patients than in the general population. These patients have a high frequency of sudden death related to respiratory failure, cardiac arrhythmias and in particular to cardiac conduction disturbances. Prophylactic pacemaker implantation should be considered in asymptomatic myotonic dystrophy patients, which in the early stages of disease present minor conduction disturbances in 12-leads ECG. Even if the rate of progression of conduction abnormalities is usually slow, fast progression has been often observed thus making the clinical course of individual patients rather unpredictable.
Databáze: MEDLINE