Desmoid tumor in Gardner's Syndrome presented as acute abdomen.

Autor: Hatzimarkou A; 1st Department of General Surgery, GP Hospital Tzaneio, Pireaus, Tzani & Afentouli str, Pireaus, Athens, Greece. webdocgr@hotmail.com, Filippou D, Papadopoulos V, Filippou G, Rizos S, Skandalakis P
Jazyk: angličtina
Zdroj: World journal of surgical oncology [World J Surg Oncol] 2006 Mar 28; Vol. 4, pp. 18. Date of Electronic Publication: 2006 Mar 28.
DOI: 10.1186/1477-7819-4-18
Abstrakt: Background: Gardner's syndrome can occasionally be complicated with intra-abdominal desmoid tumor. These tumors usually remain asymptomatic but can exhibit symptoms due to intestinal, vascular and ureteral compression and obstruction.
Case Presentation: A rare case of a 41-year-old male patient with Gardner's syndrome complicated with intra-abdominal desmoid tumor, which first presented as acute abdomen, is presented.
Conclusion: Extra-abdominal manifestations of Gardner's syndrome along with a palpable abdominal mass would raise suspicion for the presence of a desmoid tumor in the majority of cases. In life-threatening cases, surgical treatment should be considered as a palliative approach, though the extent of excision remains debatable.
Databáze: MEDLINE