Zobrazeno 1 - 10
of 495
pro vyhledávání: 'Lüllmann-Rauch, Renate'
Autor:
Matthias Petersen, Nesrin Schmiedel, Franziska Dierck, Susanne Hille, Anca Remes, Frauke Senger, Inga Schmidt, Renate Lüllmann-Rauch, Oliver J. Müller, Derk Frank, Ashraf Y. Rangrez, Norbert Frey, Christian Kuhn
Publikováno v:
Frontiers in Molecular Biosciences, Vol 10 (2023)
Despite the identification of numerous molecular pathways modulating cardiac hypertrophy its pathogenesis is not completely understood. In this study we define an unexpected role for Fibin (“fin bud initiation factor homolog”) in cardiomyocyte hy
Externí odkaz:
https://doaj.org/article/6a575afc00444393a65dd76ec25bfb68
Autor:
Lüningschrör, Patrick, Werner, Georg, Stroobants, Stijn, Kakuta, Soichiro, Dombert, Benjamin, Sinske, Daniela, Wanner, Renate, Lüllmann-Rauch, Renate, Wefers, Benedikt, Wurst, Wolfgang, D’Hooge, Rudi, Uchiyama, Yasuo, Sendtner, Michael, Haass, Christian, Saftig, Paul, Knöll, Bernd, Capell, Anja, Damme, Markus
Publikováno v:
In Cell Reports 10 March 2020 30(10):3506-3519
Autor:
Kuhn, Christian, Menke, Maja, Senger, Frauke, Mack, Claudia, Dierck, Franziska, Hille, Susanne, Schmidt, Inga, Brunke, Gabriele, Bünger, Pia, Schmiedel, Nesrin, Will, Rainer, Sossalla, Samuel, Frank, Derk, Eschenhagen, Thomas, Carrier, Lucie, Lüllmann-Rauch, Renate, Rangrez, Ashraf Yusuf, Frey, Norbert
Publikováno v:
In JACC: Basic to Translational Science April 2021 6(4):365-380
Autor:
Saskia Heybrock, Kristiina Kanerva, Ying Meng, Chris Ing, Anna Liang, Zi-Jian Xiong, Xialian Weng, Young Ah Kim, Richard Collins, William Trimble, Régis Pomès, Gilbert G. Privé, Wim Annaert, Michael Schwake, Joerg Heeren, Renate Lüllmann-Rauch, Sergio Grinstein, Elina Ikonen, Paul Saftig, Dante Neculai
Publikováno v:
Nature Communications, Vol 10, Iss 1, Pp 1-12 (2019)
Cholesterol transport is tightly regulated in the cell and in lysosomes is regulated by NPC1/2. Here, Heybrock et al. use molecular modeling, knockout mice and cell based studies to show that LIMP-2 also mediates lysosomal cholesterol transport.
Externí odkaz:
https://doaj.org/article/7ad18a0cfcb742e09b108e2916ba4cfd
Akademický článek
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Autor:
Patrick Lüningschrör, Georg Werner, Stijn Stroobants, Soichiro Kakuta, Benjamin Dombert, Daniela Sinske, Renate Wanner, Renate Lüllmann-Rauch, Benedikt Wefers, Wolfgang Wurst, Rudi D’Hooge, Yasuo Uchiyama, Michael Sendtner, Christian Haass, Paul Saftig, Bernd Knöll, Anja Capell, Markus Damme
Publikováno v:
Cell Reports, Vol 30, Iss 10, Pp 3506-3519.e6 (2020)
Summary: Genetic variations in TMEM106B, coding for a lysosomal membrane protein, affect frontotemporal lobar degeneration (FTLD) in GRN- (coding for progranulin) and C9orf72-expansion carriers and might play a role in aging. To determine the physiol
Externí odkaz:
https://doaj.org/article/6a9f42b14fca4fb8a5526634d9334b2c
Autor:
David Massa López, Melanie Thelen, Felix Stahl, Christian Thiel, Arne Linhorst, Marc Sylvester, Irm Hermanns-Borgmeyer, Renate Lüllmann-Rauch, Winnie Eskild, Paul Saftig, Markus Damme
Publikováno v:
eLife, Vol 8 (2019)
Lysosomes are major sites for intracellular, acidic hydrolase-mediated proteolysis and cellular degradation. The export of low-molecular-weight catabolic end-products is facilitated by polytopic transmembrane proteins mediating secondary active or pa
Externí odkaz:
https://doaj.org/article/74b437a01c4045349afd71c5702c4170
Autor:
Heike Wolf, Markus Damme, Stijn Stroobants, Rudi D'Hooge, Hans Christian Beck, Irm Hermans-Borgmeyer, Renate Lüllmann-Rauch, Thomas Dierks, Torben Lübke
Publikováno v:
Disease Models & Mechanisms, Vol 9, Iss 9, Pp 1015-1028 (2016)
Fucosidosis is a rare lysosomal storage disorder caused by the inherited deficiency of the lysosomal hydrolase α-L-fucosidase, which leads to an impaired degradation of fucosylated glycoconjugates. Here, we report the generation of a fucosidosis mou
Externí odkaz:
https://doaj.org/article/138a1d71f754489d931af1f83c6469a3
Autor:
Mareninova, Olga A., Sendler, Matthias, Malla, Sudarshan Ravi, Yakubov, Iskandar, French, Samuel W., Tokhtaeva, Elmira, Vagin, Olga, Oorschot, Viola, Lüllmann-Rauch, Renate, Blanz, Judith, Dawson, David, Klumperman, Judith, Lerch, Markus M., Mayerle, Julia, Gukovsky, Ilya, Gukovskaya, Anna S.
Publikováno v:
In Cellular and Molecular Gastroenterology and Hepatology November 2015 1(6):678-694
Autor:
Ankush Borlepawar, Nesrin Schmiedel, Matthias Eden, Lynn Christen, Alexandra Rosskopf, Derk Frank, Renate Lüllmann-Rauch, Norbert Frey, Ashraf Yusuf Rangrez
Publikováno v:
Cells, Vol 9, Iss 11, p 2390 (2020)
Dysbindin, a schizophrenia susceptibility marker and an essential constituent of BLOC-1 (biogenesis of lysosome-related organelles complex-1), has recently been associated with cardiomyocyte hypertrophy through the activation of Myozap-RhoA-mediated
Externí odkaz:
https://doaj.org/article/ff1ba9050db645b4970ab5f703d06d13