Zobrazeno 1 - 6
of 6
pro vyhledávání: '"complexes i–v"'
Autor:
Nath Sunil
Publikováno v:
Biomolecular Concepts, Vol 13, Iss 1, Pp 272-288 (2022)
Following structural determination by recent advances in electron cryomicroscopy, it is now well established that the respiratory Complexes I–IV in oxidative phosphorylation (OXPHOS) are organized into supercomplexes in the respirasome. Nonetheless
Externí odkaz:
https://doaj.org/article/e09c9650e24447a2a79640ece3186f70
Autor:
Markéta Tesařová, Alena Pecinová, Jan Janota, Jiří Zeman, Tomáš Mráček, Petr Pecina, Hana Houšťková, Hana Hansikova, Hana Nůsková, Josef Houštěk
Publikováno v:
BBA Clinical
Background Mitochondrial diseases belong to the most severe inherited metabolic disorders affecting pediatric population. Despite detailed knowledge of mtDNA mutations and progress in identification of affected nuclear genes, diagnostics of a substan
Akademický článek
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Autor:
Hana Nůsková, Josef Houštěk, Nikola Kovářová, Marek Vrbacký, Tomáš Mráček, Massimo Zeviani, Carlo Viscomi, Petr Pecina
Publikováno v:
Biochimica et Biophysica Acta
Mitochondrial protein SURF1 is a specific assembly factor of cytochrome c oxidase (COX), but its function is poorly understood. SURF1 gene mutations cause a severe COX deficiency manifesting as the Leigh syndrome in humans, whereas in mice SURF1−/
Kniha
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Autor:
Pecina P; Department of Bioenergetics, Institute of Physiology Academy of Sciences of the Czech Republic v.v.i., 142 20 Prague 4, Czech Republic., Houšťková H; Department of Pediatrics and Adolescent Medicine, Thomayer Hospital, 140 00 Prague 4, Czech Republic., Mráček T; Department of Bioenergetics, Institute of Physiology Academy of Sciences of the Czech Republic v.v.i., 142 20 Prague 4, Czech Republic., Pecinová A; Department of Bioenergetics, Institute of Physiology Academy of Sciences of the Czech Republic v.v.i., 142 20 Prague 4, Czech Republic., Nůsková H; Department of Bioenergetics, Institute of Physiology Academy of Sciences of the Czech Republic v.v.i., 142 20 Prague 4, Czech Republic., Tesařová M; Clinic of Pediatrics and Adolescent Medicine, General University Hospital in Prague, 128 08 Prague 2, Czech Republic., Hansíková H; Clinic of Pediatrics and Adolescent Medicine, General University Hospital in Prague, 128 08 Prague 2, Czech Republic., Janota J; Department of Neonatology, Thomayer Hospital, 140 00 Prague 4, Czech Republic., Zeman J; Clinic of Pediatrics and Adolescent Medicine, General University Hospital in Prague, 128 08 Prague 2, Czech Republic., Houštěk J; Department of Bioenergetics, Institute of Physiology Academy of Sciences of the Czech Republic v.v.i., 142 20 Prague 4, Czech Republic.
Publikováno v:
BBA clinical [BBA Clin] 2014 Oct 01; Vol. 2, pp. 62-71. Date of Electronic Publication: 2014 Oct 01 (Print Publication: 2014).