Zobrazeno 1 - 9
of 9
pro vyhledávání: '"Yoshinori Satomura"'
Autor:
Yoshinori Satomura, Kazuhiko Bessho, Nobutoshi Nawa, Hidehito Kondo, Shogo Ito, Takao Togawa, Masanao Yano, Yuki Yamano, Taisuke Inoue, Miho Fukui, Shinsuke Onuma, Tomoya Fukuoka, Kie Yasuda, Takeshi Kimura, Makiko Tachibana, Taichi Kitaoka, Shin Nabatame, Keiichi Ozono
Publikováno v:
Journal of Medical Case Reports, Vol 16, Iss 1, Pp 1-6 (2022)
Abstract Background Arthrogryposis, renal dysfunction, and cholestasis syndrome (ARCS) is a rare autosomal recessive disorder caused by mutations in VPS33B (ARCS1) and VIPAS39 (ARCS2). As per literature, most patients with ARCS died of persistent inf
Externí odkaz:
https://doaj.org/article/ac1143801be74e5f85e9d7f8ee61ab4c
Autor:
Kie Yasuda, Shinsuke Onuma, Yoko Miyoshi, Miho Fukui, Yoshinori Satomura, Kazuhiko Bessho, Makiko Tachibana, Takeshi Kimura, Tomoya Fukuoka, Keiichi Ozono
Publikováno v:
Journal of Pediatric Endocrinology and Metabolism. 34:1411-1418
Objectives Iodine deficiency and excess both cause thyroid dysfunction. Few data describe the relationship between iodine status and outcomes of congenital hypothyroidism (CH) in iodine-sufficient areas. We investigated urinary iodine (UI) concentrat
Autor:
Yasuhisa Ohata, Takuo Kubota, Taichi Kitaoka, Kazuhiko Bessho, Keiichi Ozono, Yoshinori Satomura, Shinji Takeyari
Publikováno v:
World Journal of Clinical Pediatrics
Background McCune-Albright syndrome (MAS) is caused by postzygotic somatic mutations of the GNAS gene. It is characterized by the clinical triad of fibrous dysplasia, cafe-au-lait skin spots, and endocrinological dysfunction. Myriad complications in
Autor:
Takeshi Kimura, Yoko Miyoshi, Kazuhiko Bessho, Hiroyuki Tanaka, Tomonobu Hasegawa, Makiko Tachibana, Kie Yasuda, Takehisa Yamamoto, Noriyuki Katsumata, Shinsuke Onuma, Yoshinori Satomura, Keiichi Ozono, Maki Fukami, Miho Fukui, Tomoya Fukuoka
Publikováno v:
Clinical Pediatric Endocrinology
Herein, we report two girls with a neonatal screening (NS)-negative 21-hydroxylase deficiency (21-OHD) requiring treatment with hydrocortisone due to virilization that developed in late childhood. Patient 1 was born prematurely on the 30th gestationa
Autor:
Kazuhiko Bessho, Yoshinori Satomura
Publikováno v:
Introduction to Biliary Atresia ISBN: 9789811621598
Biliary atresia (BA) is a progressive fibroinflammatory obstruction affecting both the intra- and extrahepatic bile ducts, and 25%–30% of neonatal cholestasis cases are caused by BA. Despite intensive research, the precise pathogenesis of BA remain
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_________::5c1e5d8054225b1d48582af54c51c354
https://doi.org/10.1007/978-981-16-2160-4_7
https://doi.org/10.1007/978-981-16-2160-4_7
Autor:
Shinsuke Onuma, Tomoya Fukuoka, Yoko Miyoshi, Miho Fukui, Yoshinori Satomura, Kie Yasuda, Takeshi Kimura, Makiko Tachibana, Kazuhiko Bessho, Takehisa Yamamoto, Hiroyuki Tanaka, Noriyuki Katsumata, Maki Fukami, Tomonobu Hasegawa, Keiichi Ozono
Publikováno v:
Clinical Pediatric Endocrinology; 2021, Vol. 30 Issue 3, p143-148, 6p
Autor:
Takehisa Ueno, Kazuhiko Bessho, Yoko Miyoshi, Yasuhiro Hasegawa, Akiko Konishi, Yoshinori Satomura, Tomoya Fukuoka, Makiko Tachibana, Keiichi Ozono, Kie Yasuda, Takeshi Kimura
Publikováno v:
Journal of pediatric gastroenterology and nutrition. 67(3)
Objectives Duodenal tube test (DTT) is used as a preoperative screening to rule out biliary atresia (BA). In previous reports, DTT was assessed by the color of the duodenal fluid, but there were no quantitative criteria. The aim of this study was to
Autor:
Hiroki Kondou, Kayo Ikeda, Yoko Miyoshi, Masanobu Kawai, Takehisa Ueno, Yasuhiro Hasegawa, Makiko Tachibana, Keiichi Ozono, Takeshi Kimura, Yoshinori Satomura, Kie Yasuda, Akiko Konishi, Kazuhiko Bessho, Toshimi Michigami
Publikováno v:
Hepatology research : the official journal of the Japan Society of Hepatology. 49(3)
Aim Bile acid biosynthesis is strictly regulated under physiological conditions. The expression of fibroblast growth factor (FGF) 19 is induced when bile acids bind to the farnesoid X receptor in the intestinal epithelium. Fibroblast growth factor 19
Autor:
Tomoya Fukuoka, Kazuhiko Bessho, Makiko Tachibana, Yoshinori Satomura, Akiko Konishi, Kie Yasuda, Takeshi Kimura, Yasuhiro Hasegawa, Takehisa Ueno, Yoko Miyoshi, Keiichi Ozono, Fukuoka, Tomoya, Bessho, Kazuhiko, Tachibana, Makiko, Satomura, Yoshinori, Konishi, Akiko, Yasuda, Kie, Kimura, Takeshi, Hasegawa, Yasuhiro, Ueno, Takehisa
Publikováno v:
Journal of Pediatric Gastroenterology & Nutrition; Sep2018, Vol. 67 Issue 3, p383-387, 5p