Development and initial validation of the macrophage activation syndrome/primary hemophagocytic lymphohistiocytosis score, a diagnostic tool that differentiates primary hemophagocytic lymphohistiocytosis from macrophage activation syndrome

Autor: Francesca Minoia, Francesca Bovis, Sergio Davì, Antonella Insalaco, Kai Lehmberg, Susan Shenoi, Sheila Weitzman, Graciela Espada, Yi-Jin Gao, Jordi Anton, Toshiyuki Kitoh, Ozgur Kasapcopur, Helga Sanner, Rosa Merino, Itziar Astigarraga, Maria Alessio, Michael Jeng, Vyacheslav Chasnyk, Kim E. Nichols, Zeng Huasong, Caifeng Li, Concetta Micalizzi, Nicolino Ruperto, Alberto Martini, Randy Q. Cron, Angelo Ravelli, AnnaCarin Horne, Mario Abinun, Amita Aggarwal, Jonathan Akikusa, Sulaiman Al-Mayouf, Maria Teresa Apaz, Tadej Avcin, Nuray Aktay Ayaz, Patrizia Barone, Bianca Bica, Isabel Bolt, Luciana Breda, Rolando Cimaz, Fabrizia Corona, Ruben Cuttica, Zane Davidsone, Carmen De Cunto, Jaime De Inocencio, Erkan Demirkaya, Eli M. Eisenstein, Sandra Enciso, Michel Fischbach, Michael Frosch, Romina Gallizzi, Maria Luz Gamir, Thomas Griffin, Alexei Grom, Soad Hashad, Teresa Hennon, Jan-Inge Henter, Gerd Horneff, Adam Huber, Norman Ilowite, Maka Ioseliani, Agneza Marija Kapović, Raju Khubchandani, Isabelle Koné-Paut, Sheila Knupp Feitosa de Oliveira, Bianca Lattanzi, Loredana Lepore, Jeffrey M. Lipton, Silvia Magni-Manzoni, Despoina Maritsi, Deborah McCurdy, Paivi Miettunen, Velma Mulaosmanovic, Susan Nielsen, Seza Ozen, Priyankar Pal, Sampath Prahalad, Donato Rigante, Ingrida Rumba-Rozenfelde, Ricardo Russo, Claudia Saad Magalhães, Wafaa Mohamed Saad Sewairi, Clovis Artur Silva, Valda Stanevicha, Gary Sterba, Kimo C. Stine, Gordana Susic, Flavio Sztajnbok, Syuji Takei, Ralf Trauzeddel, Elena Tsitsami, Erbil Unsal, Yosef Uziel, Olga Vougiouka, Carol A. Wallace, Lehn Weaver, Jennifer E. Weiss, Carine Wouters, Nico Wulffraat, Mabruka Zletni, Maurizio Arico, R. Maarten Egeler, Alexandra H. Filipovich, Helmut Gadner, Shinsaku Imashuku, Gritta Janka, Stephan Ladisch, Ken L. McClain, David Webb

Publikováno v: JOURNAL OF PEDIATRICS
r-FSJD. Repositorio Institucional de Producción Científica de la Fundació Sant Joan de Déu
instname
r-FSJD: Repositorio Institucional de Producción Científica de la Fundació Sant Joan de Déu
Fundació Sant Joan de Déu

OBJECTIVE: To develop and validate a diagnostic score that assists in discriminating primary hemophagocytic lymphohistiocytosis (pHLH) from macrophage activation syndrome (MAS) related to systemic juvenile idiopathic arthritis. STUDY DESIGN: The clin

Externí odkaz: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::d908099e02f637432862a51326748c61
http://hdl.handle.net/10807/104902

2016 Classification criteria for macrophage activation syndrome complicating systemic juvenile idiopathic arthritis : A European league against Rheumatism/American college of Rheumatology/Paediatric rheumatology international trials organisation collaborative initiative

Autor: Ravelli, Angelo, Minoia, Francesca, Davì, Sergio, Horne, Annacarin, Bovis, Francesca, Pistorio, Angela, Aricò, Maurizio, Avcin, Tadej, Behrens, Edward M., De Benedetti, Fabrizio, Filipovic, Lisa, Grom, Alexei A., Henter, Jan Inge, Ilowite, Norman T., Jordan, Michael B., Khubchandani, Raju, Kitoh, Toshiyuki, Lehmberg, Kai, Lovell, Daniel J., Miettunen, Paivi, Nichols, Kim E., Ozen, Seza, Pachlopnik Schmid, Jana, Ramanan, Athimalaipet V., Russo, Ricardo, Schneider, Rayfel, Sterba, Gary, Uziel, Yosef, Wallace, Carol, Wouters, Carine, Wulffraat, Nico, Demirkaya, Erkan, Brunner, Hermine I., Martini, Alberto, Ruperto, Nicolino, Cron, PARTICIPATING PHYSICIANS The following physicians contributed patient data for use in the study: Mario Abinun, Randy Q. APPENDIX A., Amita Aggarwal, Md, Jonathan Akikusa, Md, Sulaiman M. Al Mayouf, Md, Maria Alessio, Md, Jordi Anton, Md, Maria Teresa Apaz, Md, Itziar Astigarraga, Md, Nuray A. Ayaz, Md, Patrizia Barone, Md, Blanca Bica, Md, Isabel Bolt, Md, Luciana Breda, Md, Vyacheslav Chasnyk, Md, Rolando Cimaz, Md, Fabrizia Corona, Md, Ruben Cuttica, Md, Gianfranco D’Angelo, Md, Zane Davidsone, Md, Carmen De Cunto, Md, Jaime De Inocencio, Md, Eli Eisenstein, Md, Sandra Enciso, Md, Graciela Espada, Md, Michel Fischbach, Md, Michael Frosch, Md, Gallizzi, Romina, Maria Luz Gamir, Md, Yi Jin Gao, Md, Thomas Griffin, Md, Soad Hashad, Md, Teresa Hennon, Md, Gerd Horneff, Md, Zeng Huasong, Md, Adam Huber, Md, Norman Ilowite, Md, Antonella Insalaco, Md, Maka Ioseliani, Md, Marijia Jelusic Drazic, Md, Michael Jeng, Md, Agneza Kapovic, Md, Ozgur Kasapcopur, Md, Toshiyuki Kitoh, Md, Isabelle Kone Paut, Md, Sheila Knupp Feitosa de Oliveira, Md, Bianca Lattanzi, Md, Loredana Lepore, Md, Caifeng Li, Md, Jeffrey M. Lipton, Md, Silvia Magni Manzoni, Md, Despoina Maritsi, Md, Deborah McCurdy, Md, Rosa Merino, Md, Velma Mulaosmanovic, Md, Susan Nielsen, Md, Priyankar Pal, Md, Sampath Prahalad, Md, Donato Rigante, Md, Ingrida Rumba Rozenfelde, Md, Claudia Saad Magalhaes, Md, Helga Sanner, Md, Sujata Sawhney, Md, Wafaa M. Sewairi, Md, Bita Shakoory, Md, Susan Shenoi, Md, Artur Silva Clovis, Md, Valda Stanevicha, Md, Kimo C. Stine, Md, Gordana Susic, Md, Flavio Sztajnbok, Md, Syuji Takei, Md, Hasan Tezer, Md, Ralf Trauzeddel, Md, Elena Tsitsami, Md, Erbil Unsal, Md, Olga Vougiouka, Md, Lehn K. Weaver, Md, Jennifer Weiss, Md, Sheila Weitzman, Md, Mabruka Zletni, M. D.

Publikováno v: Annals of the Rheumatic Diseases, 75(3), 481. BMJ Publishing Group
ARTHRITIS & RHEUMATOLOGY
r-FSJD: Repositorio Institucional de Producción Científica de la Fundació Sant Joan de Déu
Fundació Sant Joan de Déu
r-FSJD. Repositorio Institucional de Producción Científica de la Fundació Sant Joan de Déu
instname
Arthritis & Rheumatology, 68(3), 566. John Wiley and Sons Ltd
Paediatrics Publications

Objective To develop criteria for the classification of macrophage activation syndrome (MAS) in patients with systemic juvenile idiopathic arthritis (JIA). Methods A multistep process, based on a combination of expert consensus and analysis of real p

Externí odkaz: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::8a28d35acb60717934205acf824732a0
https://dspace.library.uu.nl/handle/1874/335867