A case of severe pulmonary exacerbation in a young patient with cystic fibrosis in the era of CFTR modulators

Autor: Chiara Lanfranchi, Carmela Rizza, Maria Chiara Russo, Irene Borzani, Salvatore Alessio Angileri, Erica Nazzari, Gianfranco Alicandro, Francesco Blasi, Valeria Daccò

Publikováno v: International Journal of Infectious Diseases, Vol 147, Iss , Pp 107190- (2024)

The introduction of CFTR modulator drugs like elexacaftor-tezacaftor-ivacaftor (ETI) has transformed the management of cystic fibrosis (CF), significantly improving symptoms, lung function, and quality of life, while reducing reliance on intravenous

Externí odkaz: https://doaj.org/article/16c9140f887340b1aa3f2a8d9ce36f1b

Perceived burden of respiratory physiotherapy in people with cystic fibrosis taking elexacaftor–tezacaftor–ivacaftor combination: a 1-year observational study

Autor: Chiara Blardone, Simone Gambazza, Alessandra Mariani, Rachele Galgani, Anna Brivio, Rita Maria Nobili, Carmela Rizza, Anna Luisa Tutino, Andrea Gramegna, Valeria Daccò, Martina Contarini, Francesco Blasi, Dario Laquintana

Publikováno v: Therapeutic Advances in Respiratory Disease, Vol 18 (2024)

Background: To limit the progression of disease, people with cystic fibrosis (pwCF) perform daily respiratory physiotherapy, which is perceived as the most burdensome routine in managing their condition. The elexacaftor–tezacaftor–ivacaftor (ETI)

Externí odkaz: https://doaj.org/article/826a5d5f03f5438f92a80eef04948035

Impact of COVID-19 on Lung Disease in People with Cystic Fibrosis: A 6-Month Follow-Up Study on Respiratory Outcomes

Autor: Paola Medino, Gianfranco Alicandro, Chiara Rosazza, Fabiana Ciciriello, Andrea Gramegna, Arianna Biffi, Valeria Daccò, Vincenzina Lucidi, Marco Cipolli, Mariaserena Boraso, Erica Nazzari, Carla Colombo

Publikováno v: Biomedicines, Vol 10, Iss 11, p 2771 (2022)

Background: The impact of COVID-19 on respiratory outcomes in people with cystic fibrosis (pwCF) has not been clearly characterized. We evaluated changes in respiratory function indicators derived from spirometry and pulmonary exacerbation rates 6 mo

Externí odkaz: https://doaj.org/article/df6600ddbdec4e1bac3711d4ac105076

Chronic infection by nontypeable Haemophilus influenzae fuels airway inflammation

Autor: Fabio Saliu, Giulia Rizzo, Alessandra Bragonzi, Lisa Cariani, Daniela M. Cirillo, Carla Colombo, Valeria Daccò, Daniela Girelli, Sara Rizzetto, Barbara Sipione, Cristina Cigana, Nicola I. Lorè

Publikováno v: ERJ Open Research, Vol 7, Iss 1 (2021)

Nontypeable Haemophilus influenzae (NTHi) is commonly isolated from airways of patients suffering from chronic respiratory diseases, such as COPD or cystic fibrosis (CF). However, to what extent NTHi long-term infection contributes to the lung inflam

Externí odkaz: https://doaj.org/article/9c2b82e34dd64dc38937c4711ab97fa6

Abstracts from the 23rd Italian congress of Cystic Fibrosis and the 13th National congress of Cystic Fibrosis Italian Society

Autor: Annamaria Bevivino, Alessandra Coiana, Annalisa Fogazzi, Fabiana Timelli, Sandra Signorini, Marco Lucarelli, Patrizia Morelli, Rita Padoan, Barbara Giordani, Annalisa Amato, Fabio Majo, Gianluca Ferrari, Serena Quattrucci, Laura Minicucci, Giovanna Floridia, Gianna Puppo Fornaro, Domenica Taruscio, Marco Salvatore, Manuela Seia, Silvia Pierandrei, Giovanna Blaconà, Valentina Salvati, Giovanni Sette, Giuseppe Cimino, Federica Sangiuolo, Adriana Eramo, Mirella Collura, Elisa Parisi, Annalisa Ferlisi, Gabriella Traverso, Marcella Bertolino, Lisa Termini, Maria A. Orlando, Caterina Di Girgenti, Valeria Pavone, Maria A. Calamia, Maria G. Silvestro, Caterina Lo Piparo, Francesca Ficili, Carla Colombo, Elizabeth Tullis, Jane C. Davies, Charlotte McKee, Cynthia DeSouza, David Waltz, Jessica Savage, Marc Fisher, Rebecca Shilling, Sam Moskowitz, Sarah Robertson, Simon Tian, Jennifer L. Taylor-Cousar, Steven M. Rowe, Elisa Beccia, Annalucia Carbone, Maria Favia, Stefano Castellani, Antonella Angiolillo, Valeria Casavola, Massimo Conese, Bruno M. Cesana, Diego Falchetti, Fiorella Battistini, Elisabetta Bignamini, Cesare Braggion, Natalia Cirilli, Maria C. Lucanto, Vincenzina Lucidi, Antonio Manca, Valeria Raia, Novella Rotolo, Donatello Salvatore, Sonia Volpi, Erica Nazzari, Riccardo Guarise, Palmiro Mileto, Francesca Garbarino, Gianfranco Alicandro, Alberto Battezzati, Antonella M. Di Lullo, Marika Comegna, Felice Amato, Paola Iacotucci, Vincenzo Carnovale, Elena Cantone, Maurizio Iengo, Giuseppe Castaldo, Claudio Orlando, Alida Casale, Angela Sepe, Fabiola De Gregorio, Antonia De Matteo, Alice Castaldo, Chiara Cimbalo, Antonella Tosco, Daniela Savi, Michela Mordenti, Enea Bonci, Patrizia Troiani, Viviana D’Alù, Paolo Rossi, Monica Varchetta, Tamara Perelli, Serenella Bertasi, Paolo Palange, Lucia Tardino, Giuseppe F. Parisi, Anna Portale, Chiara Franzonello, Maria Papale, Salvatore Leonardi, Francesca Pennisi, Sabina M. Bruno, Giulia Licciardello, Giampiero Ferraguti, Manuela Sterrantino, Giancarlo Testino, Roberto Buzzetti, Cecilia Surace, Valentina M. Sofia, Nicola Ullmann, Antonio Novelli, Adriano Angioni, Renato Liguori, Francesca Manzoni, Chiara Di Palma, Sabrina Maietta, Federica Zarrilli, Vito Terlizzi, Federico Alghisi, Giuseppe Tuccio, Valentina Tradati, Eliana di Stefano, Patrizia Dato, Maria G. Sciarrabone, Carmela Fondacaro, Federico Cresta, Valentina Baglioni, Silvia Garuti, Isabella Buffoni, Francesca Landi, Rosaria Casciaro, Daniela Girelli, Antonio Teri, Samantha Sottotetti, Arianna Biffi, Chiara Vignati, Monica D’accico, Anna Maraschini, Milena Arghittu, Giovanna Pizzamiglio, Elisa Cariani, Daniela Dolce, Novella Ravenni, Silvia Campana, Erica Camera, Carlo Castellani, Giovanni Taccetti, Eleonora Calderone, Roberto Bandettini, Chiara Degli Innocenti, Chiara Castellani, Eleonora Masi, Maria Chiara Cavicchi, Beatrice Ferrari, Ramona Pezzotta, Piercarlo Poli, Serena Messali, Silvana Timpano, Erika Scaltriti, Stefano Pongolini, Simona Fiorentini, Silvia Bresci, Lorenzo Corsi, Beatrice Borchi, Annalisa Cavallo, Filippo Bartalesi, Massimo Pistolesi, Alessandro Bartoloni, Federica Arcoleo, Tiziana Pensabene, Giovanni Bacci, Federica Armanini, Ersilia V. Fiscarelli, Nicola Segata, Alessio Mengoni, Maria V. Di Toppa, Nicoleta Popa, Francesco Felicetti, Sonia Graziano, Riccardo Ciprandi, Rita Pescini, Guendalina Graffigna, Serena Barello, Paola Catastini, Salvatore De Masi, C. Braggion, Lucia Guarnuto, Emanuela Di Liberti, Valentina Patti, Massimo Luca Castellazzi, Valeria Daccò, Laura Claut, Matteo Giuliari, Luana Vicentini, Fausto Tilotta, Antonella Paciaroni, Sabino Della Sala, Cristina Guerzoni, Elisa Andreatta, Grazia Dinnella, Orazia M. Granata, Tommaso S. Aronica, Mimì Crapisi, Donatella Fogazza, Luca Alessi, Flavia Mulè, Marcello Vitaliti, Mariarosaria Maresi, Andrea Catzola, Laura Salvadori, Carmela Colangelo, Giovanni Marsicovetere, Michele D’Andria, Domenica Passarella, Carmela Genovese, Mari A. Orlando, Stefania Barrale, Maria R. Bonaccorso, Annalisa D’Arpa

Publikováno v: Italian Journal of Pediatrics, Vol 44, Iss S1, Pp 1-23 (2018)

Externí odkaz: https://doaj.org/article/cb1eab39ef9746eba4b93120a34a2ea2