Zobrazeno 1 - 10
of 25
pro vyhledávání: '"Tzu Wen Yeh"'
Autor:
Chenyang Zhang, Ben Raveney, Fumio Takahashi, Tzu-wen Yeh, Hirohiko Hohjoh, Takashi Yamamura, Shinji Oki
Publikováno v:
Cells, Vol 12, Iss 6, p 868 (2023)
In addition to disease-associated microglia (DAM), microglia with MHC-II and/or IFN-I signatures may form additional pathogenic subsets that are relevant to neurodegeneration. However, the significance of such MHC-II and IFN-I signatures remains elus
Externí odkaz:
https://doaj.org/article/ab091121f12347cc96b9ac31e45933b2
Autor:
Hirokazu Kanegane, Akihiro Hoshino, Tsubasa Okano, Takahiro Yasumi, Taizo Wada, Hidetoshi Takada, Satoshi Okada, Motoi Yamashita, Tzu-wen Yeh, Ryuta Nishikomori, Masatoshi Takagi, Kohsuke Imai, Hans D. Ochs, Tomohiro Morio
Publikováno v:
Allergology International, Vol 67, Iss 1, Pp 43-54 (2018)
Primary immunodeficiencies (PIDs) are a heterogeneous group of inherited diseases of the immune system. The definite diagnosis of PID is ascertained by genetic analysis; however, this takes time and is costly. Flow cytometry provides a rapid and high
Externí odkaz:
https://doaj.org/article/8ebd6cfe06e64dfcbe7cf81567adaa1c
Autor:
Chih-Yuan Lee, Ting-Yu Lai, Meng-Kun Tsai, Yung-Chi Chang, Yu-Hsin Ho, I-Shing Yu, Tzu-Wen Yeh, Chih-Chang Chou, You-Sheng Lin, Toby Lawrence, Li-Chung Hsu
Publikováno v:
Nature Communications, Vol 8, Iss 1, Pp 1-14 (2017)
Caveolae and their major constituent Caveolin-1 (CAV1) play an important role in signalling pathways involved in inflammation, but regulators of CAV1 protein stability are unknown. Here, the authors show that E3 ubiquitin ligase ZNRF1 induces degrada
Externí odkaz:
https://doaj.org/article/c30b0e30686342fe9db885694ae7780d
Autor:
Kay Tanita, Akihiro Hoshino, Ken-Ichi Imadome, Takahiro Kamiya, Kento Inoue, Tsubasa Okano, Tzu-wen Yeh, Masakatsu Yanagimachi, Akira Shiraishi, Masataka Ishimura, Tilmann Schober, Meino Rohlfs, Masatoshi Takagi, Kohsuke Imai, Hidetoshi Takada, Shouichi Ohga, Christoph Klein, Tomohiro Morio, Hirokazu Kanegane
Publikováno v:
Frontiers in Pediatrics, Vol 7 (2019)
Chronic active Epstein-Barr virus (EBV) infection (CAEBV) is an EBV-associated lymphoproliferative disease characterized by repeated or sustainable infectious mononucleosis (IM)-like symptoms. EBV is usually detected in B cells in patients who have I
Externí odkaz:
https://doaj.org/article/f9fa48da9746493b9db8dbcd6a868420
Autor:
Aoi Morishita, Tzu‐Wen Yeh, Kouki Tomari, Mihoko Furuichi, Kenichi Kashimada, Tomohiro Morio, Masatoshi Takagi, Kohsuke Imai
Publikováno v:
Pediatrics International. 65
CBL plays a critical role in cellular proliferation. Germline heterozygous CBL variants give rise to CBL syndrome, which is phenotypically similar to RASopathy. Somatic mutations in CBL have been reported in patients with juvenile myelomonocytic leuk
Autor:
Osamu Ohara, Kohsuke Imai, Taizo Wada, Kunio Hashimoto, Akira Shimada, Kanako Mitsui-Sekinaka, Tzu-Wen Yeh, Takaki Asano, Youjiro Ichinose
Publikováno v:
Frontiers in Immunology, Vol 9 (2018)
Activated PI3Kδ syndrome (APDS) is a primary immunodeficiency characterized by recurrent respiratory tract infections, lymphoproliferation, and defective IgG production. Heterozygous mutations in PIK3CD, PIK3R1, or PTEN, which are related to the hyp
Externí odkaz:
https://doaj.org/article/6ada6c9333d2423db340754668339554
Autor:
Miko Okamura, Seishi Ogawa, Tzu-Wen Yeh, Hirokazu Kanegane, Eri Kumaki-Matsumoto, Kohsuke Imai, Keisuke Okamoto, Motoi Yamashita, Masatoshi Takagi, Satoshi Okada, Shintaro Ono, Takuya Naruto, Hiroo Ueno, Keisuke Tanaka, Tomohiro Morio, Etsushi Toyofuku, Tsubasa Okano, Kazuaki Matsumoto, Osamu Ohara, Kay Tanita
Publikováno v:
Journal of Clinical Immunology. 40:729-740
Purpose Owing to recent technological advancements, using next-generation sequencing (NGS) and the accumulation of clinical experiences worldwide, more than 420 genes associated with inborn errors of immunity (IEI) have been identified, which exhibit
Autor:
Tomohiro Morio, Tsubasa Okano, Yujin Sekinaka, Eri Endo, Katsuyuki Hanabusa, Ikuya Tsuge, Shiann Tarng Jou, Masataka Ishimura, Hsin-Hui Yu, Yoshihiro Maruo, Tomiko Kimoto, Tomoaki Kunitsu, Hiroshi Yagasaki, Masami Inoue, Kenichi Yoshida, Yuki Tsujita, Taizo Wada, Kohsuke Imai, Kyoko Suzuki, Seiji Kojima, Sven Kracker, Tetsuzo Tauchi, Yuko Hashimoto, Takehiro Takashima, Yuzaburo Inoue, Toru Uchiyama, Hidetoshi Takada, Kenichi Honma, Motohiro Kato, Masakazu Nagahori, Takashi Kaneko, Yoshiaki Shikama, Naohiko Moriguchi, Tomoko Waragai, Daiei Kojima, Haruka Hiroki, Tamaki Kato, Kanako Mitsui-Sekinaka, Keisuke Tanaka, Anne Durandy, Yuki Bando, Hideki Muramatsu, Kazuhiro Tasaki, Seishi Ogawa, Hirokazu Kanegane, Fuminori Iwasaki, Shigeaki Nonoyama, Tzu Wen Yeh, Chikako Kamae, Toshihiko Shirakawa, Osamu Suzuki, Tomoyo Matsubara, Hideki Sano, Yuki Yuza, Osamu Ohara, Noriko Mitsuiki
Publikováno v:
Journal of Allergy and Clinical Immunology. 143:266-275
Background Activated phosphatidylinositol-3-OH kinase δ syndrome type 1 (APDS1) is a recently described primary immunodeficiency syndrome characterized by recurrent respiratory tract infections, lymphoid hyperplasia, and Herpesviridae infections cau
Autor:
Akira Ohara, Tomohiro Morio, Hirokazu Kanegane, Kenichi Honma, Tomonari Shigemura, Shigeaki Nonoyama, Chikako Kamae, Emiko Noguchi, Hiroyuki Sasaki, Tzu Wen Yeh, Shunichi Takakura, Aoi Honma, Tamaki Kato, Tomoko Shigemori, Kohsuke Imai, Masatoshi Hayashi, Osamu Ohara, Tsubasa Okano, Noriko Nakagawa, Watanabe Seiichi, Hiroshi Takahashi, Takeo Kubota
Publikováno v:
Journal of Clinical Immunology. 38:927-937
Immunodeficiency, centromeric instability, and facial anomalies (ICF) syndrome is a rare autosomal recessive primary immunodeficiency. Hypogammaglobulinemia is a major manifestation of ICF syndrome, but immunoglobulin replacement therapy does not see
Autor:
Likun Du, Kohsuke Imai, Tsubasa Okano, Qiang Pan-Hammarström, Tomohiro Morio, Noriko Mitsuiki, Miko Okamura, Takuya Naruto, Satoshi Okada, Motoi Yamashita, Tzu-Wen Yeh, Kay Tanita, Hirokazu Kanegane
Publikováno v:
The Journal of allergy and clinical immunology. 146(5)
Background Interactions between the tumor necrosis factor (TNF) ligand superfamily and TNF receptor superfamily play critical roles in B-cell development and maturation. A proliferation-inducing ligand (APRIL), a member of the TNF ligand superfamily,