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pro vyhledávání: '"Terri L. Cameron"'
Autor:
Hong Du, Terri L. Cameron, Stephen J. Garger, Gregory P. Pogue, Lee A. Hamm, Earl White, Kathleen M. Hanley, Gregory A. Grabowski
Publikováno v:
Journal of Lipid Research, Vol 49, Iss 8, Pp 1646-1657 (2008)
Lysosomal acid lipase (LAL) is an essential enzyme that hydrolyzes triglycerides (TGs) and cholesteryl esters (CEs) in lysosomes. Genetic LAL mutations lead to Wolman disease (WD) and cholesteryl ester storage disease (CESD). An LAL-null (lal−/−)
Externí odkaz:
https://doaj.org/article/b29ac79e31b941a8aab0bc10a5eb7492
Autor:
Earl White, Gregory P. Pogue, Gregory A. Grabowski, Lee A. Hamm, Kathleen M. Hanley, Hong Du, Terri L. Cameron, Stephen J. Garger
Publikováno v:
Journal of Lipid Research, Vol 49, Iss 8, Pp 1646-1657 (2008)
Lysosomal acid lipase (LAL) is an essential enzyme that hydrolyzes triglycerides (TGs) and cholesteryl esters (CEs) in lysosomes. Genetic LAL mutations lead to Wolman disease (WD) and cholesteryl ester storage disease (CESD). An LAL-null (lal(-/-)) m