Zobrazeno 1 - 10
of 12
pro vyhledávání: '"Tania Tiepolo"'
Autor:
Paolo Bonaldo, Elena Palma, Tania Tiepolo, Chiara Pellegrini, Patrizia Sabatelli, Alessia Angelin, Francesca Gualandi, Sergio Squarzoni, Paolo Bernardi, Nadir M. Maraldi, Luciano Merlini, Anna Urciuolo
Publikováno v:
Journal of Cellular Physiology
Collagen VI myopathies (Ullrich congenital muscular dystrophy (UCMD), Bethlem myopathy (BM), and myosclerosis myopathy) share a common pathogenesis, that is, mitochondrial dysfunction due to deregulation of the permeability transition pore (PTP). Thi
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::97c4d4d14df2b375e416cffde2aa80a0
http://europepmc.org/articles/PMC3415679
http://europepmc.org/articles/PMC3415679
Autor:
Tania Tiepolo, Nadir M. Maraldi, Patrizia Sabatelli, Paolo Bernardi, Luciano Merlini, Paolo Bonaldo, Paola Braghetta, Alessandra Ferlini, Alessandra Zamparelli, Alessia Angelin
Publikováno v:
Proceedings of the National Academy of Sciences. 105:5225-5229
Ullrich congenital muscular dystrophy and Bethlem myopathy are skeletal muscle diseases that are due to mutations in the genes encoding collagen VI, an extracellular matrix protein forming a microfibrillar network that is particularly prominent in th
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::d64e8f124f25dcaadbba87435a3ed800
https://doi.org/10.1073/pnas.0800962105
https://doi.org/10.1073/pnas.0800962105
Oxidative stress by monoamine oxidases is causally involved in myofiber damage in muscular dystrophy
Autor:
Fabio Di Lisa, Marcella Canton, Bert Blaauw, Tania Tiepolo, Paolo Bonaldo, Paola Braghetta, Carlo Reggiani, Luana Toniolo, Barbara Spolaore, Sara Menazza
Several studies documented the key role of oxidative stress and abnormal production of reactive oxygen species (ROS) in the pathophysiology of muscular dystrophies (MDs). The sources of ROS, however, are still controversial as well as their major mol
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::45e14426cecde71de6064e4aaa77c151
http://hdl.handle.net/11577/2481881
http://hdl.handle.net/11577/2481881
Autor:
Patrizia Sabatelli, Luisa Coletto, Paolo Grumati, Paolo Bonaldo, Enrico Bertaggia, Matilde Cescon, Luciano Merlini, Anna Urciuolo, Tania Tiepolo, Nadir M. Maraldi, Bert Blaauw, Paolo Bernardi, Alessia Angelin, Marco Sandri
Publikováno v:
Nature Medicine; Vol 16
Autophagy is crucial in the turnover of cell components, and clearance of damaged organelles by the autophagic-lysosomal pathway is essential for tissue homeostasis. Defects of this degradative system have a role in various diseases, but little is kn
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::dabdb24fb691ffd05caf1d18bdd669f2
http://hdl.handle.net/11585/99331
http://hdl.handle.net/11585/99331
Autor:
M.E. Michelini, Tania Tiepolo, Annarita Armaroli, Luciano Merlini, Paolo Bonaldo, N.M. Maraldi, Paola Braghetta, Paolo Bernardi, Alessandra Ferlini, Patrizia Sabatelli, Alessia Angelin, Alessandra Zamparelli
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::743300b333aa1462dfa408e231f8d535
http://hdl.handle.net/11577/2534138
http://hdl.handle.net/11577/2534138
Autor:
Paolo Bonaldo, Patrizia Sabatelli, Tania Tiepolo, Michael Forte, Nadir M. Maraldi, Elena Palma, Emy Basso, Alessia Angelin, Paolo Bernardi
1 Department of Biomedical Sciences, 2 Department of Histology, Microbiology and Medical Biotechnologies, University of Padova, 35121 Padova, Italy, 3 IGM-CNR, Unit of Bologna c/o IOR, 40136, Bologna, Italy and 4 Vollum Institute, Oregon Health and S
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::d02ee97083c2fb00dab0e643c583256c
http://hdl.handle.net/11577/2430667
http://hdl.handle.net/11577/2430667
Autor:
Paolo Bonaldo, J.M. Dumont, Luciano Merlini, Patrizia Sabatelli, Elena Palma, Tania Tiepolo, Alessia Angelin, Paola Braghetta, Francesca Finetti, G. Vuagniaux, Paolo Bernardi, Luca Nicolosi, Cosima T. Baldari
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::493b8edf14079a8f3e636101821fcef9
http://hdl.handle.net/11577/2534141
http://hdl.handle.net/11577/2534141
Autor:
Patrizia Sabatelli, Paola Braghetta, Alessia Angelin, Tania Tiepolo, Paolo Bernardi, Elena Palma, Mike Forte, Paolo Bonaldo, Nadir M. Maraldi, Emy Basso
Publikováno v:
Biochimica et Biophysica Acta (BBA) - Bioenergetics. 1777
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::9299601e37048955e644d2bb1c27883b
Autor:
Alessandra Ferlini, Tania Tiepolo, Francesca Gualandi, Elisabetta Mattioli, Patrizia Sabatelli, Paolo Grumati, Alessia Angelin, Natascha Bergamin, Nadir M. Maraldi, Paolo Bonaldo, Cristina Golfieri, Paolo Bernardi, Luciano Merlini
Ullrich congenital muscular dystrophy is a severe genetically and clinically heterogeneous muscle disorder linked to collagen VI deficiency. The pathogenesis of the disease is unknown. To assess the potential role of mitochondrial dysfunction in the
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::2c04a1ee015144dcba921d408d454ff2
https://hdl.handle.net/11588/900185
https://hdl.handle.net/11588/900185
Autor:
N.M. Maraldi, M. Vasso, Cecilia Gelfi, Tania Tiepolo, S. De Palma, Francesca Gualandi, Paolo Bonaldo, Paolo Bernardi, Patrizia Sabatelli, Alessandra Ferlini, Matteo Bovolenta, Luciano Merlini
Publikováno v:
Neuromuscular Disorders. 19:630
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_________::857a00d71c5743256e8b6642b9e9f283
https://doi.org/10.1016/j.nmd.2009.06.268
https://doi.org/10.1016/j.nmd.2009.06.268