Zobrazeno 1 - 10
of 15
pro vyhledávání: '"Svetlana V. Mikhaylova"'
Autor:
Inga V. Anisimova, Svetlana B. Artemyeva, Elena D. Belousova, Nato D. Vashakmadze, Dmitriy V. Vlodavets, Tatiana A. Gremyakova, Olga S. Groznova, Valentina I. Guzeva, Elena V. Gusakova, Lyudmila M. Kuzenkova, Alexey L. Kurenkov, Sergey I. Kutsev, Svetlana V. Mikhaylova, Lyudmila P. Nazarenko, Sergey S. Nikitin, Artem Yu. Novikov, Tatiana V. Podkletnova, Elena V. Polevichenko, Alexander V. Polyakov, Gennady G. Prokopyev, Dmitry I. Rudenko, Svetlana A. Repina, Evgeniia V. Romanenko, Sergey O. Ryabykh, Gul’zhan E. Sakbaeva, Elena Yu. Sapego, Liliia R. Selimzyanova, Andrey A. Stepanov, Dmitry M. Subbotin, Vasiliy M. Suslov, Elena V. Tozliyan, Dmirty A. Feklistov, Nadezhda I. Shakhovskaya, Ekaterina V. Shreder
Publikováno v:
Педиатрическая фармакология, Vol 20, Iss 5, Pp 427-453 (2023)
Duchenne muscular dystrophy is one of the most common forms of childhood muscular dystrophies. Its incidence is 1 in 3.5–6 thousand newborn boys according to various sources. The disease is caused by the mutation in the DMD gene coding the dystroph
Externí odkaz:
https://doaj.org/article/376b5dfeb86d48aa82f78ab3af2f103f
Publikováno v:
Журнал медико-биологических исследований, Vol 11, Iss 3, Pp 265-277 (2023)
Биологический возраст определяется совокупностью обменных, структурных, функциональных, регуляторных и приспособительных особенност
Externí odkaz:
https://doaj.org/article/0dab368a71c84424b93d6bca2c459a71
Autor:
Aleksander A. Baranov, Tatiana T. Batysheva, Olga V. Bykova, Nato D. Vashakmadze, Elena V. Vislobokova, Alisa V. Vitebskaya, Elena A. Vishneva, Victoria Yu. Voynova, Natalia V. Zhurkova, Ekaterina Yu. Zakharova, Larisa P. Kisel'nikova, Mikhail M. Kostik, Sergey I. Kutsev, Tea V. Margieva, Leyla S. Namazova-Baranova, Svetlana V. Mikhaylova, Sergey V. Moiseev, Tatyana S. Nagornaya, Liliia R. Selimzyanova, Alla N. Semyachkina, Olga Ya. Smirnova, Marina V. Fedoseenko, Svetlana V. Pishchal'nikova
Publikováno v:
Педиатрическая фармакология, Vol 20, Iss 4, Pp 318-336 (2023)
Hypophosphatasia is rare genetic disease caused by tissue-nonspecific alkaline phosphatase deficiency due to the mutation in the ALPL gene. Disease can manifest in utero, in childhood or in adults depending on its form and severity. This article pres
Externí odkaz:
https://doaj.org/article/dd29ce8f7c954e10bb999e43b7ae4d52
Autor:
Alexander A. Baranov, Leyla S. Namazova-Baranova, Sergey I. Kutsev, Tea V. Margieva, Nato D. Vashakmadze, Elena A. Vishneva, Lilia R. Selimzyanova, Elena Yu. Voskoboeva, Ekaterina Yu. Zakharova, Ludmila M. Kuzenkova, Tina V. Lobzhanidze, Lyudmila K. Mikhaylova, Olga A. Polyakova, Svetlana V. Mikhaylova, Sergei V. Moiseev, Tatiana V. Podkletnova, Alla N. Semechkina, Olga V. Udalova, Alisa V. Vitebskaya, Larisa P. Kisel’nikova, Mikhail M. Kostik
Publikováno v:
Педиатрическая фармакология, Vol 17, Iss 6, Pp 519-528 (2021)
he authors present the latest data on the hypophosphatasia (HPP) management in children. Hypophosphatasia is a rare genetic disease caused by deficiency of tissue-specific alkaline phosphatase due to mutation in the ALPL gene. The article covers all
Externí odkaz:
https://doaj.org/article/59c9926ddedb497a80978dfe18b3fe30
Autor:
Svetlana V. Mikhaylova
Publikováno v:
Музыкальное искусство и образование, Vol 8, Iss 4, Pp 162-178 (2020)
In the article a brief historical review displays the process of appearance and development of general music education in the Republic of Sakha (Yakutia). Based on study of extensive range of sources significant changes of attitude to Yakut music
Externí odkaz:
https://doaj.org/article/3b05caf08a214e21b862153e4b2fdd8a
Autor:
Nato D. Vashakmadze, Leyla S. Namazova-Baranova, Natalia V. Zhurkova, Ekaterina Yu. Zakharova, Svetlana V. Mikhaylova, Grigory V. Revunenkov
Publikováno v:
Вопросы современной педиатрии, Vol 18, Iss 3, Pp 196-202 (2019)
Mucopolysaccharidosis type I (MPS I) is the hereditary disease characterized with alpha-L-iduronidase activity decrease and further accumulation of heparan and dermatan sulfate in lysosomes. MPS I is rare autosomal recessive disorder with incidence o
Externí odkaz:
https://doaj.org/article/5131c9e48c024b158a4c89f6e4f8d4d7
Autor:
Alexander A. Baranov, Leyla S. Namazova-Baranova, Tatyana E. Borovik, Tatyana V. Bushueva, Oksana V. Globa, Natalya V. Zhurkova, Elena A. Vishneva, Ekaterina Yu. Zakharova, Natalya G. Zvonkova, Ljudmila M. Kuzenkova, Sergey I. Kutsev, Svetlana V. Mikhaylova, Ekaterina A. Nikolaeva, Petr V. Novikov, Alexandr A. Pushkov, Kirill V. Savostyanov, Elena Yu. Voskoboeva, Liliia R. Selimzianova, Alla N. Semyachkina
Publikováno v:
Вопросы современной педиатрии, Vol 16, Iss 6, Pp 457-467 (2018)
Homocystinuria is a genetically heterogeneous hereditary disease from the group of aminoacidopathies caused by a metabolic disorder of sulphur-containing amino acids, primarily methionine. The article presents the etiopathogenetic, diagnostic and the
Externí odkaz:
https://doaj.org/article/5f29b37e5a434ef1a21f1a00fa3b8298
Autor:
Svetlana V. Mikhaylova
Publikováno v:
Musical Art and Education. 10:157-166
Autor:
Svetlana V. Mikhaylova
Publikováno v:
Journal of Medical and Biological Research. 8:149-156
Publikováno v:
Hygiene and sanitation. 97:642-647
The article presents the physiological and hygienic justification for the rating scale for biological age “Bio-age”, developed during preventive medical examinations in the Health Center of 602 students (253 boys and 349 girls) aged 18-22 years i