Zobrazeno 1 - 10
of 20
pro vyhledávání: '"Svetlana Smirnikhina"'
Autor:
Anna Demchenko, Lyubava Belova, Maxim Balyasin, Konstantin Kochergin-Nikitsky, Ekaterina Kondrateva, Ekaterina Voronina, Victoria Pozhitnova, Vyacheslav Tabakov, Diana Salikhova, Tatiana Bukharova, Dmitry Goldshtein, Elena Kondratyeva, Tatiana Kyian, Elena Amelina, Olga Zubkova, Olga Popova, Tatiana Ozharovskaia, Alexander Lavrov, Svetlana Smirnikhina
Publikováno v:
Frontiers in Cell and Developmental Biology, Vol 12 (2024)
Human-induced airway basal cells (hiBCs) derived from human-induced pluripotent stem cells (hiPSCs) offer a promising cell model for studying lung diseases, regenerative medicine, and developing new gene therapy methods. We analyzed existing differen
Externí odkaz:
https://doaj.org/article/1ffcfffd8dc841cf9b884642048ec158
Autor:
Ekaterina Kondrateva, Olga Grigorieva, Irina Panchuk, Igor Bychkov, Ekaterina Zakharova, Vyacheslav Tabakov, Victoria Pozhitnova, Ekaterina Voronina, Olga Shchagina, Alexander Lavrov, Svetlana Smirnikhina, Sergey Kutsev
Publikováno v:
Stem Cell Research, Vol 73, Iss , Pp 103259- (2023)
Skin fibroblasts obtained from a 5-year-old girl with genetically proven (two heterozygous mutations in ARSB gene) and clinically manifested mucopolysaccharidosis type VI were successfully transformed into induced pluripotent stem cells by using Send
Externí odkaz:
https://doaj.org/article/1284f0a760894ca98c3c93f0fbd1179f
Autor:
Ekaterina Kondrateva, Olga Grigorieva, Elizaveta Kurshakova, Irina Panchuk, Victoria Pozhitnova, Ekaterina Voronina, Vyacheslav Tabakov, Maria Orlova, Alexander Lavrov, Svetlana Smirnikhina, Sergey Kutsev
Publikováno v:
Stem Cell Research, Vol 70, Iss , Pp 103133- (2023)
Urine cells obtained from a 14-year-old man with genetically proven (ACVR1: c.6176G > A) and clinically manifested fibrodysplasia ossificans progressiva were successfully transformed into induced pluripotent stem cells by using Sendai virus-based rep
Externí odkaz:
https://doaj.org/article/9a6e25fd826248969e58a1e427c2ad38
Autor:
Irina Panchuk, Ekaterina Kondrateva, Anna Demchenko, Olga Grigorieva, Anastasija Erofeeva, Elena Amelina, Vyacheslav Tabakov, Maria Orlova, Ekaterina Voronina, Victoria Pozhitnova, Alexander Lavrov, Svetlana Smirnikhina, Sergey Kutsev
Publikováno v:
Stem Cell Research, Vol 64, Iss , Pp 102896- (2022)
Induced pluripotent stem cells (iPSCs) was successfully generated from skin fibroblast obtained from patient with cystic fibrosis by using non-integrating, viral CytoTune™-iPS 2.0 Sendai Reprogramming Kit, which contain three vectors preparation: p
Externí odkaz:
https://doaj.org/article/23c487f034f94f5bbd0282f50f67ea83
Autor:
Ekaterina Kondrateva, Irina Panchuk, Anna Demchenko, Olga Grigorieva, Diana Zheglo, Ekaterina Voronina, Anastasija Erofeeva, Vyacheslav Tabakov, Maria Orlova, Alexander Lavrov, Svetlana Smirnikhina, Sergey Kutsev
Publikováno v:
Stem Cell Research, Vol 63, Iss , Pp 102854- (2022)
Skin fibroblasts obtained from a 20-year-old woman with clinically manifested and genetically proven (F508del/CFTRdele2.3) cystic fibrosis were successfully transformed into induced pluripotent stem cells (iPSCs) by using Sendai virus-based reprogram
Externí odkaz:
https://doaj.org/article/cc2b6a7b950f4303a3c1ac1d40314be5
Autor:
Anna Demchenko, Ekaterina Kondrateva, Vyacheslav Tabakov, Anna Efremova, Diana Salikhova, Tatiana Bukharova, Dmitry Goldshtein, Maxim Balyasin, Natalia Bulatenko, Elena Amelina, Alexander Lavrov, Svetlana Smirnikhina
Publikováno v:
International Journal of Molecular Sciences, Vol 24, Iss 7, p 6293 (2023)
Airway and lung organoids derived from human-induced pluripotent stem cells (hiPSCs) are current models for personalized drug screening, cell–cell interaction studies, and lung disease research. We analyzed the existing differentiation protocols an
Externí odkaz:
https://doaj.org/article/12217ea1d7ec41f992402fa7185941d7
Autor:
Ekaterina Kondrateva, Anna Demchenko, Yana Slesarenko, Matvey Yasinovsky, Elena Amelina, Viacheslav Tabakov, Ekaterina Voronina, Alexander Lavrov, Svetlana Smirnikhina
Publikováno v:
Stem Cell Research, Vol 53, Iss , Pp 102251- (2021)
Cystic fibrosis is one of the most common inherited diseases caused by mutations in CFTR gene, of which F508del is the most frequent. Currently, the possibility of cell therapy including genome editing is widely discussed. We generated induced plurip
Externí odkaz:
https://doaj.org/article/a10925b754e245ec98ba7dd00a5c8f02
Autor:
Ekaterina Kondrateva, Anna Demchenko, Yana Slesarenko, Victoria Pozhitnova, Matvey Yasinovsky, Elena Amelina, Vyacheslav Tabakov, Ekaterina Voronina, Alexander Lavrov, Svetlana Smirnikhina
Publikováno v:
Stem Cell Research, Vol 52, Iss , Pp 102232- (2021)
Skin fibroblasts obtained from a 28-year-old man with clinically manifested and genetically proven (F508del/W1282X) cystic fibrosis were successfully transformed into induced pluripotent stem cells (iPSCs) by using non-viral, non-integrating, self-re
Externí odkaz:
https://doaj.org/article/b7c5d0ec4d1b4e829167628b4d5a3c65
Autor:
Ekaterina Kondrateva, Elmira Adilgereeva, Elena Amelina, Vyacheslav Tabakov, Anna Demchenko, Kirill Ustinov, Matvey Yasinovsky, Ekaterina Voronina, Alexander Lavrov, Svetlana Smirnikhina
Publikováno v:
Stem Cell Research, Vol 48, Iss , Pp 101933- (2020)
Skin fibroblasts obtained from a 27-year-old man with clinically manifested and genetically proven (F508del/F508del) cystic fibrosis were successfully transformed into induced pluripotent stem cells (iPSCs) by using Sendai virus-based reprogramming v
Externí odkaz:
https://doaj.org/article/976fe7d5d5984f329d09574c2a4aa43c
Publikováno v:
Clinical Genetics. 102:465-473
Dysferlinopathies are a clinically heterogeneous group of diseases caused by mutations in the DYSF gene encoding the dysferlin protein. Dysferlin is mostly expressed in muscle tissues and is localized in the sarcolemma, where it performs its main fun