Zobrazeno 1 - 10
of 59
pro vyhledávání: '"Steven Law"'
Autor:
Yousuf Razvi, Aldostefano Porcari, Concetta Di Nora, Rishi K. Patel, Adam Ioannou, Muhammad U. Rauf, Ambra Masi, Steven Law, Liza Chacko, Tamer Rezk, Sriram Ravichandran, Janet Gilbertson, Dorota Rowczenio, Iona J. Blakeney, Nandita Kaza, David F. Hutt, Helen Lachmann, Ashutosh Wechalekar, William Moody, Sern Lim, Colin Chue, Carol Whelan, Lucia Venneri, Ana Martinez-Naharro, Marco Merlo, Gianfranco Sinagra, Ugolino Livi, Philip Hawkins, Marianna Fontana, Julian D. Gillmore
Publikováno v:
Frontiers in Cardiovascular Medicine, Vol 9 (2023)
AimsTransthyretin cardiac amyloidosis (ATTR-CM) is a progressive and fatal cardiomyopathy. Treatment options in patients with advanced ATTR-CM are limited to cardiac transplantation (CT). Despite case series demonstrating comparable outcomes with CT
Externí odkaz:
https://doaj.org/article/dcd42138c72146719916644456120435
Impact of early response on outcomes in AL amyloidosis following treatment with frontline Bortezomib
Autor:
Sriram Ravichandran, Oliver C. Cohen, Steven Law, Darren Foard, Marianna Fontana, Ana Martinez-Naharro, Carol Whelan, Julian D. Gillmore, Helen J. Lachmann, Sajitha Sachchithanantham, Shameem Mahmood, Philip N. Hawkins, Ashutosh D. Wechalekar
Publikováno v:
Blood Cancer Journal, Vol 11, Iss 6, Pp 1-9 (2021)
Abstract The outcomes in systemic AL amyloidosis are dependent on the depth of haematologic response. However, there is limited data on the impact of the speed of response on outcomes. Here we report the impact of speed of response in a cohort of AL
Externí odkaz:
https://doaj.org/article/b337fd1300e6447c92566346cf8407bf
Autor:
Steven Law, Aviva Petrie, Liza Chacko, Oliver C. Cohen, Sriram Ravichandran, Janet A. Gilbertson, Dorota Rowczenio, Ashutosh Wechalekar, Ana Martinez‐Naharro, Helen J. Lachmann, Carol J. Whelan, David F. Hutt, Philip N. Hawkins, Marianna Fontana, Julian D. Gillmore
Publikováno v:
ESC Heart Failure, Vol 7, Iss 6, Pp 3942-3949 (2020)
Abstract Aims Cardiac transthyretin amyloidosis (ATTR‐CM) is a progressive and fatal condition. Prognosis can be determined at diagnosis according to the National Amyloidosis Centre (NAC) transthyretin amyloidosis (ATTR) stage. We sought to examine
Externí odkaz:
https://doaj.org/article/5ca588ecccb047eab238fa32476e0c62
Publikováno v:
BMC Nephrology, Vol 21, Iss 1, Pp 1-4 (2020)
Abstract Background Karyomegalic interstitial nephritis (KIN) is a rare hereditary cause of chronic kidney disease. It typically causes progressive renal impairment with haemoproteinuria requiring renal replacement therapy before 50 years of age. It
Externí odkaz:
https://doaj.org/article/e88a00bf59274e8c82f896f788643786
Autor:
Steven Law, Julia Arnold, Muhammad U. Rauf, Lauren Heptinstall, Janet Gilbertson, Dorota Rowczenio, Jyoti Baharani, Gerald Langman, Marianna Fontana, Julian D. Gillmore
Publikováno v:
American Journal of Kidney Diseases. 81:606-610
Autor:
Adam Ioannou, Paolo Massa, Rishi K Patel, Yousuf Razvi, Aldostefano Porcari, Muhammad U Rauf, Anita Jiang, Giacomo Cabras, Stefano Filisetti, Roos E Bolhuis, Francesco Bandera, Lucia Venneri, Ana Martinez-Naharro, Steven Law, Tushar Kotecha, Ruta Virsinskaite, Daniel S Knight, Michele Emdin, Aviva Petrie, Helen Lachmann, Ashutosh Wechelakar, Mark Petrie, Alun Hughes, Nick Freemantle, Philip N Hawkins, Carol Whelan, John JV McMurray, Julian D Gillmore, Marianna Fontana
Publikováno v:
European Heart Journal.
Background and Aims The aims of this study were to assess prescription patterns, dosages, discontinuation rates and association with prognosis of conventional heart failure (HF) medications in patients with transthyretin cardiac amyloidosis (ATTR-CA)
Autor:
Ana Martinez-Naharro, Rishi Patel, Tushar Kotecha, Nina Karia, Adam Ioannou, Aviva Petrie, Liza A Chacko, Yousuf Razvi, Sriram Ravichandran, James Brown, Steven Law, Cristina Quarta, Shameem Mahmood, Brendan Wisniowski, Silvia Pica, Sajitha Sachchithanantham, Helen J Lachmann, James C Moon, Daniel S Knight, Carol Whelan, Lucia Venneri, Hui Xue, Peter Kellman, Julian D Gillmore, Philip N Hawkins, Ashutosh D Wechalekar, Marianna Fontana
Publikováno v:
European Heart Journal. 43:4722-4735
Aims To assess the ability of cardiovascular magnetic resonance (CMR) to (i) measure changes in response to chemotherapy; (ii) assess the correlation between haematological response and changes in extracellular volume (ECV); and (iii) assess the asso
Autor:
Oliver C Cohen, Ananth Sathyanath, Aviva Petrie, Sriram Ravichandran, Steven Law, Richa Manwani, Darren Foard, Sajitha Sachchithanantham, Shameem Mahmood, Ana Martinez-Naharro, Marianna Fontana, Carol J Whelan, Philip N Hawkins, Helen J Lachmann, Julian D Gillmore, Ashutosh D Wechalekar
Publikováno v:
Heart. 108:1616-1622
ObjectivesIn AL amyloidosis, organ response assessment is based on surrogates (eg, cardiac biomarkers). An objective functional test, such as the 6 min walk test (6MWT), capturing overall clinical improvement, is required. We aimed to evaluate the pr
Autor:
Muhammad Umaid Rauf, Philip N Hawkins, Francesco Cappelli, Federico Perfetto, Mattia Zampieri, Alessia Argiro, Aviva Petrie, Steven Law, Aldostefano Porcari, Yousuf Razvi, Joshua Bomsztyk, Sriram Ravichandran, Adam Ioannou, Rishi Patel, Neasa Starr, David F Hutt, Shameem Mahmood, Brendan Wisniowski, Ana Martinez–Naharro, Lucia Venneri, Carol Whelan, Dorota Roczenio, Janet Gilbertson, Helen J Lachmann, Ashutosh D Wechalekar, Claudio Rapezzi, Matteo Serenelli, Paolo Massa, Angelo Giuseppe Caponetti, Alberto Ponziani, Antonella Accietto, Alessandro Giovannetti, Giulia Saturi, Maurizio Sguazzotti, Christian Gagliardi, Elena Biagini, Simone Longhi, Marianna Fontana, Julian D Gillmore
Publikováno v:
European Heart Journal.
Aims To perform evaluation of widely embraced bone scintigraphy-based non-biopsy diagnostic criteria (NBDC) for ATTR amyloid cardiomyopathy (ATTR-CM) in clinical practice, and to refine serum free light chain (sFLC) ratio cut-offs that reliably exclu
Autor:
Steven Law, Andrew Davenport
Publikováno v:
Artificial organs.
Most haemodialysis machines deliver a fixed bicarbonate concentration. Higher concentrations may improve acidosis, but risk post-haemodialysis alkalosis, whereas lower concentrations potentially increase acidosis but reduce alkalosis. We reviewed the