Zobrazeno 1 - 5
of 5
pro vyhledávání: '"Steffen Hermans"'
Autor:
Sofia Ahola, Pablo Rivera Mejías, Steffen Hermans, Srikanth Chandragiri, Patrick Giavalisco, Hendrik Nolte, Thomas Langer
Publikováno v:
Cell Metab
Cardiomyopathy and heart failure are common manifestations in mitochondrial disease caused by deficiencies in the oxidative phosphorylation (OXPHOS) system of mitochondria. Here, we demonstrate that the cardiac-specific loss of the assembly factor Co
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::8e1d2307e66ad98732d671d033abd30d
https://pubmed.ncbi.nlm.nih.gov/36113464
https://pubmed.ncbi.nlm.nih.gov/36113464
Autor:
Elena I. Rugarli, Steffen Hermans, Aleksandra Trifunovic, Marijana Aradjanski, Shuaiyu Wang, Stephan Lotter, Rolf Wibom, Sukru Anil Dogan
Publikováno v:
Human Molecular Genetics. 26:4181-4189
Although mitochondria are ubiquitous, each mitochondrial disease has surprisingly distinctly different pattern of tissue and organ involvement. Congruently, mutations in genes encoding for different mitochondrial tRNA synthetases result in the develo
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::0134266539ef8057d785b3e7b683d2e7
https://doi.org/10.1093/hmg/ddx307
https://doi.org/10.1093/hmg/ddx307
Autor:
Karolina Szczepanowska, Alexandra Kukat, Tim König, Priyanka Maiti, Katharina Senft, Christina Becker, Steffen Hermans, Aleksandra Trifunovic, Dominic Seiferling
Publikováno v:
EMBO reports. 17:953-964
The mitochondrial matrix protease CLPP plays a central role in the activation of the mitochondrial unfolded protein response (UPRmt) in Caenorhabditis elegans . Far less is known about mammalian UPRmt signaling, although similar roles were assumed fo
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::d03182e2af2da9e7abe6081125d268eb
https://doi.org/10.15252/embr.201642077
https://doi.org/10.15252/embr.201642077
Autor:
Simon Hess, Elena I. Rugarli, Susanne Brodesser, Désirée Schatton, Steffen Hermans, Peter Kloppenburg, Esther Barth, Thomas Langer, Eva R. Almajan, Sara Murru
Publikováno v:
Glia
Mitochondrial dysfunction causes neurodegeneration but whether impairment of mitochondrial homeostasis in astrocytes contributes to this pathological process remains largely unknown. The m‐AAA protease exerts quality control and regulatory function
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::353e19b5f5aa2c191603b661a2d87b38
https://pubmed.ncbi.nlm.nih.gov/30989755
https://pubmed.ncbi.nlm.nih.gov/30989755
Autor:
Alexandra Kukat, Steffen Hermans, Katharina Senft, Aleksandra Trifunovic, Priyanka Maiti, Christoph Paul Brandscheid, Christina Becker, Karolina Szczepanowska
Publikováno v:
EMBO reports. 19
Mitochondria are fundamental for cellular metabolism as they are both a source and a target of nutrient intermediates originating from converging metabolic pathways, and their role in the regulation of systemic metabolism is increasingly recognized.
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_________::e71e19b0ce4a8092b66c21768b7e71b7
https://doi.org/10.15252/embr.201745126
https://doi.org/10.15252/embr.201745126