Zobrazeno 1 - 10
of 18
pro vyhledávání: '"Simona Casarini"'
Autor:
Giovanni Palladini, Bruno Paiva, Ashutosh Wechalekar, Margherita Massa, Paolo Milani, Marta Lasa, Sriram Ravichandran, Isabel Krsnik, Marco Basset, Leire Burgos, Mario Nuvolone, Ramón Lecumberri, Andrea Foli, Noemi Puig, Melania Antonietta Sesta, Margherita Bozzola, Pasquale Cascino, Alice Nevone, Jessica Ripepi, Pierpaolo Berti, Simona Casarini, Ombretta Annibali, Alberto Orfao, Jesus San-Miguel, Giampaolo Merlini
Publikováno v:
Blood Cancer Journal, Vol 11, Iss 2, Pp 1-7 (2021)
Abstract Light chain (AL) amyloidosis is caused by a small B-cell clone producing light chains that form amyloid deposits and cause organ dysfunction. Chemotherapy aims at suppressing the production of the toxic light chain (LC) and restore organ fun
Externí odkaz:
https://doaj.org/article/1af0c29e396946d49b7a958dc256ed9f
Autor:
Paola Rognoni, Francesca Lavatelli, Simona Casarini, Giovanni Palladini, Laura Verga, Paolo Pedrazzoli, Giovanna Valentini, Giampaolo Merlini, Vittorio Perfetti
Publikováno v:
PLoS ONE, Vol 8, Iss 9, p e76022 (2013)
Monoclonal immunoglobulin light chains are normally synthesized in excess compared to the heavy chain partners and can be detected in serum and urine ("free" LC). Occasionally free LC are per se cause of organ toxicity, as in free LC-related disorder
Externí odkaz:
https://doaj.org/article/8c96f91cf2294f1993418b6f49e21eef
Autor:
Alice Nevone, Maria Girelli, Silvia Mangiacavalli, Bruno Paiva, Paolo Milani, Pasquale Cascino, Maggie Piscitelli, Valentina Speranzini, Claudio Salvatore Cartia, Pietro Benvenuti, Ibai Goicoechea, Francesca Fazio, Marco Basset, Andrea Foli, Martina Nanci, Giulia Mazzini, Serena Caminito, Melania Antonietta Sesta, Simona Casarini, Paola Rognoni, Francesca Lavatelli, Maria Teresa Petrucci, Pier Paolo Olimpieri, Stefano Ricagno, Luca Arcaini, Giampaolo Merlini, Giovanni Palladini, Mario Nuvolone
Publikováno v:
Leukemia. 36:2076-2085
Immunoglobulin light chain (AL) amyloidosis is caused by a small, minimally proliferating B-cell/plasma-cell clone secreting a patient-unique, aggregation-prone, toxic light chain (LC). The pathogenicity of LCs is encrypted in their sequence, yet mol
Autor:
Ombretta Annibali, Marta Lasa, Mario Nuvolone, Leire Burgos, Pasquale Cascino, Isabel Krsnik, Sriram Ravichandran, Alice Nevone, Paolo Milani, Andrea Foli, Ashutosh D. Wechalekar, Jesús F. San-Miguel, Margherita Massa, Bruno Paiva, Ramón Lecumberri, Melania Antonietta Sesta, Giampaolo Merlini, Alberto Orfao, Pierpaolo Berti, Marco Basset, Simona Casarini, Margherita Bozzola, Giovanni Palladini, Jessica Ripepi, Noemi Puig
Publikováno v:
Digital.CSIC. Repositorio Institucional del CSIC
instname
Blood Cancer Journal, Vol 11, Iss 2, Pp 1-7 (2021)
Blood Cancer Journal
instname
Blood Cancer Journal, Vol 11, Iss 2, Pp 1-7 (2021)
Blood Cancer Journal
© The Author(s) 2021.
Light chain (AL) amyloidosis is caused by a small B-cell clone producing light chains that form amyloid deposits and cause organ dysfunction. Chemotherapy aims at suppressing the production of the toxic light chain (LC) an
Light chain (AL) amyloidosis is caused by a small B-cell clone producing light chains that form amyloid deposits and cause organ dysfunction. Chemotherapy aims at suppressing the production of the toxic light chain (LC) an
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::e87246b18b34091d1e3d6be6bf093d22
http://hdl.handle.net/10261/261841
http://hdl.handle.net/10261/261841
Autor:
Giovanni Palladini, Margherita Massa, Enrico Milan, Mario Nuvolone, Melania Antonietta Sesta, Francesca Fazio, Alice Nevone, Andrea Foli, Giampaolo Merlini, Paolo Milani, Stefano Ricagno, Serena Caminito, Jessica Ripepi, Pasquale Cascino, Marica De Cicco, Paola Rognoni, Simona Casarini, Giulia Mazzini, Francesca Lavatelli, Margherita Bozzola, Gloria Acquafredda, Antonia Moretta, Giancarlo Russo, Maria Girelli, Marco Basset, Catherine Klersy, Claudia Scopelliti, Maria Teresa Petrucci
Publikováno v:
Blood. 138:2673-2673
Introduction In patients affected by monoclonal gammopathies, tumoral B cells or plasma cells secrete a monoclonal antibody (termed M protein), which can be used to track the presence of the tumor itself. Moreover, the M protein can directly cause po
Autor:
Enrico Milan, Silvia Mangiacavalli, Paola Rognoni, Simona Casarini, Giampaolo Merlini, Paolo Milani, Fulvia Cerruti, Magda Marcatti, Thierry Touvier, Simone Cenci, Ugo Orfanelli, Alessandro Corso, Paolo Cascio, Massimo Resnati, Andrea Orsi, Giovanni Palladini, Laura Oliva, Fabio Ciceri, Andrea Raimondi
Publikováno v:
Blood. 129(15)
Systemic light chain (AL) amyloidosis is caused by the clonal production of an unstable immunoglobulin light chain (LC), which affects organ function systemically. Although pathogenic LCs have been characterized biochemically, little is known about t
Autor:
Vittorio Perfetti, Paola Rognoni, Catherine Klersy, Giovanni Palladini, Rosangela Invernizzi, Giampaolo Merlini, Valentina Navazza, Simona Casarini, Stefano Perlini, Laura Obici
Publikováno v:
Blood. 119:144-150
Monoclonal Ig light chains (LC) can be responsible for pathologic conditions in humans, as in systemic amyloid light amyloidosis. Protean clinical manifestations characterize this disorder with the most varied combination of symptoms generated by dif
Autor:
Enrico Alfonsi, Alessandro Lozza, Stefano Perlini, Andrea Cortese, Simona Casarini, Laura Obici, Giampaolo Merlini
Publikováno v:
Orphanet Journal of Rare Diseases
Results 24 patients (20 males) affected by FAP associated with 7 different mutations were treated for a median of 24 months (range 12-60). Median age at baseline was 69 years (range 57-82), disease duration 43 months (range 17-90), PND score IIIA (ra
Publikováno v:
Leukemia. 15:195-202
Primary light chain-associated amyloidosis (AL) is a plasma cell dyscrasia that causes morbidity via systemic tissue deposition of monoclonal light chains in the form of fibrils (amyloid). It is the most common form of systemic amyloidosis in Western
Autor:
Remigio Moratti, Simona Casarini, Stefano Perlini, Francesca Lavatelli, Andrea Foli, Laura Obici, Giampaolo Merlini, Gian Vico Melzi d’Eril, Riccardo Albertini, Alessandra Barassi, Paolo Milani, Giovanni Palladini, Gabriele Sarais, Paola Russo
Publikováno v:
Amyloid : the international journal of experimental and clinical investigation : the official journal of the International Society of Amyloidosis. 18(4)
Cardiac biomarkers play a major role in the identification of patients at risk of early death in AL amyloidosis, and a staging system based on amino-terminal pro-natriuretic peptide type-B (NT-proBNP) and troponins (cTn) is used for prognostic strati