Zobrazeno 1 - 10
of 46
pro vyhledávání: '"Silvio Notari"'
Autor:
Sandra Pritzkow, Frank Ramirez, Adam Lyon, Paul E. Schulz, Brian Appleby, Fabio Moda, Santiago Ramirez, Silvio Notari, Pierluigi Gambetti, Claudio Soto
Publikováno v:
Annals of Clinical and Translational Neurology, Vol 10, Iss 12, Pp 2316-2323 (2023)
Abstract Objective Currently, it is unknown whether infectious prions are present in peripheral tissues and biological fluids of patients affected by sporadic Creutzfeldt–Jakob disease (sCJD), the most common prion disorder in humans. This represen
Externí odkaz:
https://doaj.org/article/8980ba6a7d6b43f795c57fad378d2d1e
Autor:
Satish K. Nemani, Xiangzhu Xiao, Ignazio Cali, Laura Cracco, Gianfranco Puoti, Massimiliano Nigro, Jody Lavrich, Anuradha Bharara Singh, Brian S. Appleby, Valerie L. Sim, Silvio Notari, Witold K. Surewicz, Pierluigi Gambetti
Publikováno v:
Acta Neuropathologica Communications, Vol 8, Iss 1, Pp 1-12 (2020)
Abstract One of remarkable features of sporadic Creutzfeldt-Jakob disease (sCJD) is the great phenotypic variability. Understanding the molecular basis of this variability has important implications for the development of therapeutic approaches. It i
Externí odkaz:
https://doaj.org/article/c9ed097c798c49debd92f73c5be253e7
Autor:
Laura Cracco, Xiangzhu Xiao, Satish K. Nemani, Jody Lavrich, Ignazio Cali, Bernardino Ghetti, Silvio Notari, Witold K. Surewicz, Pierluigi Gambetti
Publikováno v:
Acta Neuropathologica Communications, Vol 7, Iss 1, Pp 1-9 (2019)
Abstract Despite their phenotypic heterogeneity, most human prion diseases belong to two broadly defined groups: Creutzfeldt-Jakob disease (CJD) and Gerstmann-Sträussler-Scheinker disease (GSS). While the structural characteristics of the disease-re
Externí odkaz:
https://doaj.org/article/ea9329de289a415c88f3286c662ceb27
Autor:
Romolo Nonno, Silvio Notari, Michele Angelo Di Bari, Ignazio Cali, Laura Pirisinu, Claudia d’Agostino, Laura Cracco, Diane Kofskey, Ilaria Vanni, Jody Lavrich, Piero Parchi, Umberto Agrimi, Pierluigi Gambetti
Publikováno v:
Emerging Infectious Diseases, Vol 25, Iss 1, Pp 73-81 (2019)
Variably protease-sensitive prionopathy (VPSPr), a recently described human sporadic prion disease, features a protease-resistant, disease-related prion protein (resPrPD) displaying 5 fragments reminiscent of Gerstmann-Sträussler-Scheinker disease.
Externí odkaz:
https://doaj.org/article/ad97e37aa0e14c208f6fcf1cda0903b4
Autor:
Satish Kumar Nemani, Silvio Notari, Ignazio Cali, Victor E Alvarez, Diane Kofskey, Mark Cohen, Robert A. Stern, Brian Appleby, Joseph Abrams, Lawrence Schonberger, Ann McKee, Pierluigi Gambetti
Publikováno v:
Acta Neuropathologica Communications, Vol 6, Iss 1, Pp 1-14 (2018)
Abstract Chronic traumatic encephalopathy (CTE) is a neurodegenerative disease associated with repetitive traumatic brain injury (TBI). CTE is generally found in athletes participating in contact sports and military personnel exposed to explosive bla
Externí odkaz:
https://doaj.org/article/1fe87befe49f4fa68e43dcf39d4af548
Autor:
Silvio Notari, Xiangzhu Xiao, Juan Carlos Espinosa, Yvonne Cohen, Liuting Qing, Patricia Aguilar-Calvo, Diane Kofskey, Ignazio Cali, Laura Cracco, Qingzhong Kong, Juan Maria Torres, Pierluigi Gambetti
Publikováno v:
Emerging Infectious Diseases, Vol 20, Iss 12, Pp 2006-2014 (2014)
Variably protease-sensitive prionopathy (VPSPr), a recently identified and seemingly sporadic human prion disease, is distinct from Creutzfeldt-Jakob disease (CJD) but shares features of Gerstmann-Sträussler-Scheinker disease (GSS). However, contrar
Externí odkaz:
https://doaj.org/article/465f8e92c0614bcda5457745a06f4d4f
Autor:
Silvio Notari, Liuting Qing, Maurizio Pocchiari, Ayuna Dagdanova, Kristin Hatcher, Arend Dogterom, Jose F. Groisman, Ib Bo Lumholtz, Maria Puopolo, Corinne Lasmezas, Shu G. Chen, Qingzhong Kong, Pierluigi Gambetti
Publikováno v:
Emerging Infectious Diseases, Vol 18, Iss 1, Pp 21-28 (2012)
Prion diseases are neurodegenerative conditions associated with a misfolded and infectious protein, scrapie prion protein (PrPSc). PrPSc propagate prion diseases within and between species and thus pose risks to public health. Prion infectivity or Pr
Externí odkaz:
https://doaj.org/article/78c7e218ad8142579bbdf9b6b081a0b3
Autor:
Silvio Notari, Francisco J Moleres, Stephen B Hunter, Ermias D Belay, Lawrence B Schonberger, Ignazio Cali, Piero Parchi, Wun-Ju Shieh, Paul Brown, Sherif Zaki, Wen-Quan Zou, Pierluigi Gambetti
Publikováno v:
PLoS ONE, Vol 5, Iss 1, p e8765 (2010)
BackgroundVariant Creutzfeldt-Jakob disease (vCJD) is a prion disease thought to be acquired by the consumption of prion-contaminated beef products. To date, over 200 cases have been identified around the world, but mainly in the United Kingdom. Thre
Externí odkaz:
https://doaj.org/article/28fe48923f9445478b550bf34da11624
Autor:
Fabio Moda, Claudio Soto, Fabrizio Tagliavini, Satish K. Nemani, Jody Lavrich, Diane Kofskey, Pierluigi Gambetti, Silvio Notari, Ignazio Cali, Brian S. Appleby
Publikováno v:
Scientific Reports, Vol 9, Iss 1, Pp 1-7 (2019)
Scientific Reports
Scientific Reports
The presence of abnormal, disease-related prion protein (PrPD) has recently been demonstrated by protein misfolding cyclic amplification (PMCA) in urine of patients affected with variant Creutzfeldt-Jakob disease (vCJD), a prion disease typically acq
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::60650f79f7ba6fefb68460538696a18c
http://link.springer.com/article/10.1038/s41598-019-41694-0
http://link.springer.com/article/10.1038/s41598-019-41694-0
Autor:
Ilaria Vanni, Silvio Notari, Laura Cracco, Pierluigi Gambetti, Piero Parchi, Diane Kofskey, Ignazio Cali, Claudia D'Agostino, Jody Lavrich, Umberto Agrimi, Romolo Nonno, Michele Angelo Di Bari, Laura Pirisinu
Publikováno v:
Emerging Infectious Diseases, Vol 25, Iss 1, Pp 73-81 (2019)
Emerging Infectious Diseases
Emerging Infectious Diseases
Variably protease-sensitive prionopathy (VPSPr), a recently described human sporadic prion disease, features a protease-resistant, disease-related prion protein (resPrPD) displaying 5 fragments reminiscent of Gerstmann-Sträussler-Scheinker disease.
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::d18ddcf6cbf018b51b33ba4b8e6c6d42
https://wwwnc.cdc.gov/eid/article/25/1/18-0807_article
https://wwwnc.cdc.gov/eid/article/25/1/18-0807_article