Zobrazeno 1 - 10
of 38
pro vyhledávání: '"Sanjay Rajwal"'
Autor:
Berna Seker Yilmaz, Julien Baruteau, Anupam Chakrapani, Michael Champion, Efstathia Chronopoulou, Lee C. Claridge, Anne Daly, Catherine Davies, James Davison, Anil Dhawan, Stephanie Grunewald, Girish L. Gupte, Nigel Heaton, Hugh Lemonde, Pat McKiernan, Philippa Mills, Andrew A.M. Morris, Helen Mundy, Germaine Pierre, Sanjay Rajwal, Siyamini Sivananthan, Srividya Sreekantam, Karolina M. Stepien, Roshni Vara, Mildrid Yeo, Paul Gissen
Publikováno v:
Molecular Genetics and Metabolism Reports, Vol 37, Iss , Pp 101020- (2023)
Ornithine transcarbamylase deficiency (OTCD) is an X-linked defect of ureagenesis and the most common urea cycle disorder. Patients present with hyperammonemia causing neurological symptoms, which can lead to coma and death. Liver transplantation (LT
Externí odkaz:
https://doaj.org/article/4b378179f00043a097ba2e977f075d5f
Autor:
Kathleen M. Loomes, Robert H. Squires, Deirdre Kelly, Sanjay Rajwal, Nisreen Soufi, Alain Lachaux, Irena Jankowska, Cara Mack, Kenneth D. R. Setchell, Palaniswamy Karthikeyan, Ciara Kennedy, Alejandro Dorenbaum, Nirav K. Desai, Will Garner, Thomas Jaecklin, Pamela Vig, Alexander Miethke, Richard J. Thompson
Publikováno v:
Hepatology Communications, Vol 6, Iss 9, Pp 2379-2390 (2022)
Abstract Children with progressive familial intrahepatic cholestasis, including bile salt export pump (BSEP) and familial intrahepatic cholestasis–associated protein 1 (FIC1) deficiencies, suffer debilitating cholestatic pruritus that adversely aff
Externí odkaz:
https://doaj.org/article/b1254fad7eda4d029fb251fe1e6c2b23
Autor:
Benjamin L. Shneider, Catherine A. Spino, Binita M. Kamath, John C. Magee, Rosalinda V. Ignacio, Suiyuan Huang, Simon P. Horslen, Jean P. Molleston, Alexander G. Miethke, Rohit Kohli, Daniel H. Leung, M. Kyle Jensen, Kathleen M. Loomes, Saul J. Karpen, Cara Mack, Philip Rosenthal, Robert H. Squires, Alastair Baker, Sanjay Rajwal, Deirdre Kelly, Ronald J. Sokol, Richard J. Thompson, for ChiLDReN and UK IMAGO/IMAGINE Investigators
Publikováno v:
Hepatology Communications, Vol 6, Iss 8, Pp 1922-1933 (2022)
Abstract There is growing interest in, but limited data about, intestinal bile acid transport inhibitors as treatment for cholestatic liver disease. The current analyses combine two similar randomized placebo‐controlled trials with subsequent exten
Externí odkaz:
https://doaj.org/article/ff927fac8c8f49b3872a5335a74a6819
Autor:
Alex Pinto, Catherine Ashmore, Spyros Batzios, Anne Daly, Charlotte Dawson, Marjorie Dixon, Sharon Evans, Diane Green, Joanna Gribben, Inderdip Hunjan, Elisabeth Jameson, Camille Newby, Germaine Pierre, Sanjay Rajwal, Louise Robertson, Si Santra, Mark Sharrard, Roshni Vara, Lucy White, Gisela Wilcox, Ozlem Yilmaz, Anita MacDonald
Publikováno v:
Nutrients, Vol 12, Iss 11, p 3313 (2020)
Background: Little is known about the optimal dietary treatment for citrin deficiency. Our aim is to describe the management of UK citrin deficiency patients. Methods: A longitudinal retrospective review was performed. Data were collected from medica
Externí odkaz:
https://doaj.org/article/cf173d55e3a841debdf3b7c52027165d
Autor:
Amr M Alnagar, Abdul R Hakeem, Khaled Daradka, Eirini Kyrana, Marumbo Methga, Karthikeyan Palaniswamy, Sanjay Rajwal, Jamila Mulla, Moira O'meara, Vivek Upasani, Dhakshinamoorthy Vijayanand, Raj Prasad, Magdy S Attia
Publikováno v:
World Journal of Transplantation. 13:96-106
Autor:
Adam Arshad, Alastair Sutcliffe, Vandana Jain, Naved Alizai, Sanjay Rajwal, Deidre A. Kelly, Anil Dhawan, Khalid Sharif, Julian Gardiner, Mark Davenport, Alastair Baker
Publikováno v:
Journal of Pediatric Gastroenterology & Nutrition. 76:424-427
Autor:
Shweta Dixit, Miss Rhiannon Taylor, Miss Julie Whitney, Doctor Jane Hartley, Doctor Raj Prasad, Doctor Darius Mirza, Doctor Sanjay Rajwal, Miss Sarah Watson, Doctor John Isaac, Derek Manas, Nigel Heaton, Anil Dhawan, John Forsythe, Doug Thorburn, Tassos Grammatikopoulos
Publikováno v:
Abstracts.
L8 Acute liver failure and hepatitis associated aplastic anaemia: a 17-year single centre experience
Autor:
Vaia Zouzo, Kavitha Jayaprakash, Barath Jagadisan, Palaniswamy Karthikeyan, Marumbo Mtegha, Sanjay Rajwal
Publikováno v:
Liver.
Autor:
Shweta Dixit, Rhiannon Taylor, Julie Whitney, Jane Hartley, Magdy Attia, Darius Mirza, Sanjay Rajwal, Sarah Watson, John Isaac, Derek Manas, Nigel Heaton, Anil Dhawan, John Forsythe, Douglas Thorburn, Tassos Grammatikopoulos
Publikováno v:
Tuesday 25th April 2022.
Autor:
Kavitha Jayaprakash, Sanjay Rajwal, Jens Stahlschmidt, Terry Humphrey, Helen Woodley, J Bernadette Moore, Eirini Kyrana
Publikováno v:
Liver.