Zobrazeno 1 - 10
of 215
pro vyhledávání: '"S. Goldfischer"'
Autor:
R. J. A. Wanders, S. Goldfischer, Lodewijk IJlst, Simone Denis, C. W. T. van Roermund, E. G. van Grunsven, Sacha Ferdinandusse, Hans R. Waterham, Eveline M. Hogenhout, W. Oostheim
Publikováno v:
American Journal of Human Genetics, 70, 1589-1593. Cell Press
American journal of human genetics, 70(6), 1589-1593. Cell Press
American journal of human genetics, 70(6), 1589-1593. Cell Press
In this report, we reinvestigate the only patient ever reported with a deficiency of peroxisomal 3-ketoacyl-CoA thiolase (THIO). At the time when they were described, the abnormalities in this patient, which included accumulation of very-long-chain f
Publikováno v:
International review of experimental pathology. 31
Researchers have been able to demonstrate the cytotoxicity of copper overload in animal models. This has allowed them to not only localize the intracellular distribution of copper but also to study directly the subsequent organelle injury at the ultr
Autor:
D Katz, Sylvia Wassertheil-Smoller, H Wolinsky, R Markle, Bernice Coltoff-Schiller, L Gidez, S Goldfischer
Publikováno v:
Circulation Research. 45:546-553
It is possible that one of the consequences of regular physical activity could be a change of vascular metabolism. We studied the effects of regular swimming activity on specific activities of aortic hydrolases of male rats. Enzymes included: neutral
Autor:
S Goldfischer
Publikováno v:
Journal of Histochemistry & Cytochemistry. 30:717-733
Its topography is one of the most characteristic features of the Golgi apparatus and the reticular nature of this organelle is evident in Golgi's first drawings, in light microscopic enzyme cytochemical preparations, and in high voltage electron micr
Publikováno v:
Journal of Histochemistry & Cytochemistry. 29:1105-1111
Primary fixation in an osmium-potassium ferrocyanide (K4Fe(CN)6) mixture combines selective fixation, staining, and extraction of various cellular components; membranes, glycogen, glycoproteins, and elastin are preserved and stained. An intranuclear
Publikováno v:
Veterinary Pathology. 21:57-60
Sections of paraffin-embedded specimens of liver obtained from Bedlington terriers were stained with rhodanine for copper and examined and graded by two pathologists. Their results correlated well with each other, as well as with the results of quant
Publikováno v:
Circulation Research. 46:520-530
Autor:
Joseph M. Tager, S. Goldfischer, Elisabeth M. Brouwer-Kelder, Hugo S. A. Heymans, AndréW. Schram, Janna C. Collins, C. W. T. van Roermund, H. van den Bosch, Ruud B.H. Schutgens, Takashi Hashimoto
Publikováno v:
Proceedings of the National Academy of Sciences. 84:2494-2496
We investigated the peroxisomal beta-oxidation system in liver from a patient with clinical features similar to those in the cerebrohepatorenal (Zellweger) syndrome and with elevated levels in body fluids of very-long-chain fatty acids and intermedia
Autor:
Hugo S. A. Heymans, H. van den Bosch, Ruud B.H. Schutgens, C. W. T. van Roermund, Janna C. Collins, AndréW. Schram, Elisabeth M. Brouwer-Kelder, R. J. A. Wanders, Takashi Hashimoto, Joseph M. Tager, S. Goldfischer
Publikováno v:
Journal of Inherited Metabolic Disease. 10:214-216
Publikováno v:
Archives of pathologylaboratory medicine. 101(9)
Intralysosomal accumulation of lipid has been implicated as an important mechanism in the pathogenesis of atherosclerosis. Although atherosclerosis develops frequently in organ transplants maintained on a long-term basis, to our knowledge no studies