Zobrazeno 1 - 9
of 9
pro vyhledávání: '"Ryouji Kobayashi"'
Autor:
Taketomi Akinobu, Koichiro Uchida, Shohei Honda, Hisayuki Miyagi, Ryouji Kobayashi, Kanako Kubota, Tadao Okada, Akihiro Iguchi
Publikováno v:
Surgical Science. :564-567
Aim: There are a variety of malignant tumors related to neurofibromatosis type 1 (NF1). This report describes a rare pediatric NF1 case with an unresectable giant mediastinal tumor. Case: A 6-year-old girl with wheezing was admitted to our institutio
Autor:
Fumiaki Sasaki, Kazuaki Nakanishi, Satoru Todo, Toshiya Kamiyama, Tomoo Itoh, Takahito Nakagawa, Satoshi Ota, Tadao Okada, Ryouji Kobayashi
Publikováno v:
Journal of Pediatric Surgery. 40:E21-E25
This report describes the use of superparamagnetic iron oxide–enchanced magnetic resonance imaging to diagnose fibronodular hyperplasia of the liver in a 12-year-old girl.
Autor:
Yoshihisa Nagatoshi, Ryouji Kobayashi, David L. Nelson, Hiroyuki Katoh, Koji Yamaguchi, Yukio Sakiyama, Masafumi Yamada, Chie Kobayashi, Yasuhiko Ito, Yasushi Noguchi, Kenji Katamura, Tadashi Ariga, Satoshi Kondo
Publikováno v:
Blood. 100:1208-1214
Wiskott-Aldrich syndrome (WAS) is caused by defects in the WAS protein (WASP) gene on the X chromosome. We previously reported that flow cytometric analysis of intracellular WASP expression (FCM-WASP) was useful in the diagnosis of WAS in patients an
Publikováno v:
Journal of Chemical Software. 2:206-211
Autor:
Satoshi Takahashi, Yasuhiro Ogawa, Yoshinori Wagatuma, Akashi Ishikawa, Ryouji Kobayashi, Shihoko Tanaka, Aiko Takase, Naoki Fukushima, Kenji Kakuya
Publikováno v:
Nihon Shoni Arerugi Gakkaishi. The Japanese Journal of Pediatric Allergy and Clinical Immunology. 8:141-147
A 6-year-old boy with vitamin B1 deficiency, so called beriberi, who had had pared down and cored rice-based diet free of cow's milk, soy bean, egg, wheat, beaf, pork and chicken for 3 years was reported. This patient was admitted to the hospital bec
Autor:
Tadao Okada, Ryouji Kobayashi, Mitsuru Kubota, Satsuki Naito, Nozomi Minagawa, Satoru Todo, Fumiaki Sasaki
Publikováno v:
Pediatric surgery international. 21(11)
Postoperative portal and splenic vein thrombosis (PSVT) is a rare but potentially fatal complication after abdominal surgery. We present 2 infants with PSVT after splenectomy and total colectomy, respectively, and also provide a review of the literat
Autor:
Norikazu Hatano, Miyuki Kida, Tadashi Ariga, Osamu Tatsuzawa, Nariaki Toita, Fabio Candotti, Nobuaki Kawamura, Satoru Nakajima, Yukio Sakiyama, Makoto Otsu, Motohiko Okano, Michael S. Hershfield, Ryouji Kobayashi, Masafumi Onodera, Yoshihiro Maeyama
Publikováno v:
Molecular Therapy. 11:S14-S15
Severe combined immunodeficiency due to genetic defects of adenosine deaminase (ADA-SCID) has been a target disease of retroviral-mediated gene therapy. Recently, great success was reported in one of such clinical trials conducted in Italy aiming for
Autor:
Osamu Tatsuzawa, Norikazu Hatano, Nariaki Toita, Fabio Candotti, Masafumi Onodera, Satoru Nakajima, Makoto Otsu, Tadashi Ariga, Michael S. Hershfield, Nobuaki Kawamura, Yukio Sakiyama, Miyuki Kida, Ryouji Kobayashi, Yoshihiro Maeyama, Pawan Bali
Publikováno v:
Molecular Therapy. 13:S418
In the previous meeting, we reported the initial follow-up of the two patients with adenosine deaminase (ADA)-deficiency whom we had treated in a clinical trial of retroviral-mediated stem cell gene therapy (SCGT). Our protocol is unique in that pati
Autor:
Ryouji Kobayashi, Kunihiko Kobayashi, Yoshihiro Maeyama, Yukio Sakiyama, Makoto Otsu, Masafumi Onodera, Motohiko Okano, Norikazu Hatano, Osamu Tatsuzawa, Nobuaki Kawamura, Jukei Yoshida, Nariaki Toita, Miyuki Kida, Tadashi Ariga, Fabio Candotti, Satoru Nakajima
Publikováno v:
Molecular Therapy. 9:S67
For ADA-deficiency, a form of severe combined immunodeficiency, retroviral-mediated gene correction of peripheral T cells or hematopoietic stem/progenitor cells (HSCs) is a treatment of choice alternative to bone marrow (BM) transplantation. Recently