Histopathological Evaluation of Skeletal Muscle with Specific Reference to Mouse Models of Muscular Dystrophy

Autor: R L Terry, Dominic J. Wells

Publikováno v: Current Protocols in Mouse Biology

The muscular dystrophies are a diverse group of degenerative diseases for which many mouse models are available. These models are frequently used to assess potential therapeutic interventions and histological evaluation of multiple muscles is an impo

Externí odkaz: https://explore.openaire.eu/search/publication?articleId=doi_________::4f44c5c608b2cb43df6fb147453b3781
https://doi.org/10.1002/cpmo.19

Preventing phosphorylation of dystroglycan ameliorates the dystrophic phenotype in mdx mouse

Autor: Steve J. Winder, Christopher I. Moore, Tracy La Riviere, Dominic J. Wells, A Mitchell, T. Neil Dear, Robert W. Piggott, Gaynor Miller, R L Terry

Publikováno v: Human Molecular Genetics. 21:4508-4520

Loss of dystrophin protein due to mutations in the DMD gene causes Duchenne muscular dystrophy. Dystrophin loss also leads to the loss of the dystrophin glycoprotein complex (DGC) from the sarcolemma which contributes to the dystrophic phenotype. Tyr

Externí odkaz: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::c5149c22028ccae9183d1ae7b0dd509a
https://doi.org/10.1093/hmg/dds293

Macrophages (PP-047)

Autor: Y. Kobayashi, E. Brabcova, T. Seya, F. Hanihara, T. Kim, C. Deffrasnes, L. Gao, E. Hara, M. Imamura, S. Shimizu, S. I. Rennard, M. Arai, Héctor M. Mora-Montes, L. Kolesar, T. Ogasawara, J. Morimoto, P. Aguilar-Ramirez, K. Morimoto, Paola Italiani, T. Fukazawa, M. Hayashi, S. Tsuru, K. Tanaka, T. B. Nutman, Y. I. Kawashima, C. van Vreden, T. Ishiwata, M. Rees, K. Ito, G. Marone, Neil A. R. Gow, J. S. Silva-Vasconcellos, U. Holmskov, H. Tsutsui, Cristina Battaglia, Z. Liu, N. J. C. King, U. Yamashita, T. Kishimoto, J. Tashiro-Yamaji, T. Shen, G. Song, J. R. Jensen, M. Frydrychowicz, L. Zhang, H. A. Silva-Souza, M. A. Blahoianu, M. Jaresova, H. Tanaka, S. P. Hogan, T. Ohba, T. Muta, H. Ogita-Nakanishi, K. Saito, S. Konjar, Y. Chen, Y. Watanabe, A. V. Zavialov, M. Okada, B. Turk, Leanne E. Lewis, K. Iwata, R. Yoshida, A. Nowicka, Y. Otoyo, K. Masuda, J. Sohn, V. Sanprasert, Y. Habu, Y. Fujihara, D. N. Herndon, D. Saitoh, F. Suzuki, T. Negoro, H. Low, T. Iwasa, A. Roloson, C. D. Gregory, M. Triggiani, P. De Baetselier, I. Striz, R. I. Staiano, T. Okada, S. Ono, S. Ghisletti, L. Melville, J. Woo, D. Yan, H. Takenaka, K. Bae, J. Jun, Ingrid Cifola, J. Cho, A. Sato, J. Schachter, M. Bogyo, G. Smulian, Diana Boraschi, A. Kabakov, J. Ji, Claudia Gemelli, X. Liang, B. Rubiś, S. Byeon, O. G. Ribeiro, M. Miskinyte, A. Takahashi, I. Caramalho, A. Arruda, M. T. Getts, A. Kanazawa, K. Ueda, A. Mabuchi, J. Chen, O. Nielsen, B. Kim, H. Kaji, A. Sekerkova, S. Petrova, D. Kurotaki, A. Schlosser, Y. Tohyama, I. Chinen, Alexis Grande, E. Watanabe, S. Hirose, S. Park, T. Oshio, Y. Ijiri, C. Y. Tsai, X. Zhu, M. L. Bergman, T. Sugiura, Judith M. Bain, P. Liu, Y. Miki, J. Demengeot, R. Kato, T. Doi, Silvio Bicciato, C. Ma, N. Li, T. Takato, L. Wang, S. R. Thomas, T. Takahashi, M. Ibata, C. Yang, G. Raes, Y. Huang, H. Shime, B. Lee, A. Kimura, L. Huynh, A. Frattini, P. Mauri, M. Kobayashi, H. Akiyama, R. Rossi, Y. Tsai, W. Wongchana, K. Hoshi, H. Tsurui, S. Choi, P. Zhao, A. Wheatley, N. Nguyen, T. Uede, Y. Kim, B. Liu, D. R. Herbert, A. Ishigami, A. Yamatodani, R. Parsa, J. B. Moeller, R. A. Harris, S. Shono, T. Takagi, P. M. Persechini, M. Kozłowska, R. Kawashima, D. Greaves, R. Takahashi, T. Shimizu, K. Yasuda, K. Cheng, Davide Lucchesi, A. Mantovani, J. Grønlund, I. Gordo, O. Viklicky, L. Brys, T. Kubota, Y. Tanaka, N. Starobinas, S. Totsuka, L. Mahapatra, U. Koser, Y. Inoue, M. Emoto, T. Palaga, V. Pucino, N. Kopitar-Jerala, K. Watanabe, J. Żeromski, M. P. Reichhardt, M. Rimoldi, K. Takahashi, S. Magalhães, F. Granata, R. L. Terry, G. Natoli, G. Park, Y. Lee, T. Nakahama, H. Y. Lei, P. Liang, L. Pirdel, T. Witte, J. Sikora, V. Phongsisay, H. Batura-Gabryel, M. Matsumoto, S. Yumikura-Futatsugi, S. Seki, D. Yoo, R. Uchiyama, A. Takuma, H. Sato, A. Asai, N. Tanigawa, R. E. Schmidt, S. Mizobuchi, Lars Erwig, D. Rodriguez, H. Nakashima, J. Kim, Y. Gion, R. Tolouei Semnani, T. Uchida, Christopher G J McKenzie, E. Tsuru, K. Maher, H. Lin, M. Nakashima, H. Miyazaki, S. Loffredo, M. Kanayama, T. Murotani, Y. Wang, M. De Franco, K. Nagata, Luciana C. C. Leite, M. Kinoshita, A. Kumar, S. Hsieh, K. Suzuki, M. Kaczmarek, X. Zhao, K. Nakanishi, L. Xu, M. Yabu, Emilia Maria Cristina Mazza, M. Hirano, Y. Makarova, P. Andresen, T. Akazawa, J. Żurawski, T. Dohi, D. R. Getts, Robert N. Barker, M. Yamaguchi, S. Mise, Y. Emoto, D. Dunbar, A. Sica, C. Porta, O. M. Ibañez, Y. Nakano, T. Kimura, W. H. K. Cabrera, X. T. Cao, N. Inoue, T. Tsai, Y. Tsuda, C. Taniwaki, T. Kakiuchi, T. Fumon, I. L. Campbell

Publikováno v: International Immunology. 22:iii31-iii42

Externí odkaz: https://explore.openaire.eu/search/publication?articleId=doi_________::3788c0b236e35d24343f354f4bfbb34f
https://doi.org/10.1093/intimm/dxq227

The transgenic expression of LARGE exacerbates the muscle phenotype of dystroglycanopathy mice

Autor: Dominic J. Wells, H. Booler, R L Terry, Callum Parr, M.R. Ackroyd, M. Fernandez-Fuente, J. Kim, Manoli Kavishwar, E. Lacey, K E Wells, C. Whitmore, Attia Ashraf, Francesco Muntoni, Susan C. Brown

Publikováno v: Human molecular genetics. 23(7)

Mutations in fukutin-related protein (FKRP) underlie a group of muscular dystrophies associated with the hypoglycosylation of α-dystroglycan (α-DG), a proportion of which show central nervous system involvement. Our original FKRP knock-down mouse (

Externí odkaz: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::8fb1d45834892130b9187ffd12480cbe
https://pubmed.ncbi.nlm.nih.gov/24234655

Pharmacokinetic profile and behavioral effects of gabapentin in the horse

Autor: R L, Terry, S M, McDonnell, A W, Van Eps, L R, Soma, Y, Liu, C E, Uboh, P J, Moate, B, Driessen

Publikováno v: Journal of veterinary pharmacology and therapeutics. 33(5)

Gabapentin is being used in horses although its pharmacokinetic (PK) profile, pharmacodynamic (PD) effects and safety in the equine are not fully investigated. Therefore, we characterized PKs and cardiovascular and behavioral effects of gabapentin in

Externí odkaz: https://explore.openaire.eu/search/publication?articleId=pmid________::0c49dafea27d929cf0a6d20cc86ce4c0
https://pubmed.ncbi.nlm.nih.gov/20840393