Zobrazeno 1 - 10
of 27
pro vyhledávání: '"Pierre De Rossi"'
Autor:
Marco Losa, Marc Emmenegger, Pierre De Rossi, Patrick M Schürch, Tetiana Serdiuk, Niccolò Pengo, Danaëlle Capron, Dimitri Bieli, Niklas Bargenda, Niels J Rupp, Manfredi C Carta, Karl J Frontzek, Veronika Lysenko, Regina R Reimann, Petra Schwarz, Mario Nuvolone, Gunilla T Westermark, K Peter R Nilsson, Magdalini Polymenidou, Alexandre PA Theocharides, Simone Hornemann, Paola Picotti, Adriano Aguzzi
Publikováno v:
EMBO Molecular Medicine, Vol 16, Iss 9, Pp 2024-2042 (2024)
Abstract Extracellularly released molecular inflammasome assemblies -ASC specks- cross-seed Aβ amyloid in Alzheimer’s disease. Here we show that ASC governs the extent of inflammation-induced amyloid A (AA) amyloidosis, a systemic disease caused b
Externí odkaz:
https://doaj.org/article/361701b3ccf5457e8ccf997a37e06f01
Autor:
Pierre De Rossi, Virginie Buggia-Prévot, Benjamin L. L. Clayton, Jared B. Vasquez, Carson van Sanford, Robert J. Andrew, Ruben Lesnick, Alexandra Botté, Carole Deyts, Someya Salem, Eshaan Rao, Richard C. Rice, Angèle Parent, Satyabrata Kar, Brian Popko, Peter Pytel, Steven Estus, Gopal Thinakaran
Publikováno v:
Molecular Neurodegeneration, Vol 18, Iss 1, Pp 1-1 (2023)
Externí odkaz:
https://doaj.org/article/ddafc8cc4fce4f2296415a22e72b3b17
Autor:
Jelena Scekic-Zahirovic, Inmaculada Sanjuan-Ruiz, Vanessa Kan, Salim Megat, Pierre De Rossi, Stéphane Dieterlé, Raphaelle Cassel, Marguerite Jamet, Pascal Kessler, Diana Wiesner, Laura Tzeplaeff, Valérie Demais, Sonu Sahadevan, Katharina M. Hembach, Hans-Peter Muller, Gina Picchiarelli, Nibha Mishra, Stefano Antonucci, Sylvie Dirrig-Grosch, Jan Kassubek, Volker Rasche, Albert Ludolph, Anne-Laurence Boutillier, Francesco Roselli, Magdalini Polymenidou, Clotilde Lagier-Tourenne, Sabine Liebscher, Luc Dupuis
Publikováno v:
Nature Communications, Vol 12, Iss 1, Pp 1-19 (2021)
Mutations in the RNA binding protein FUS are associated with ALS. Here the authors show that in FUS knock-in mice there is a progressive increase in neuronal activity in the frontal cortex which is associated with altered synaptic gene expression.
Externí odkaz:
https://doaj.org/article/81d53965ba1c4f5cbe4fa11bc13113fd
Autor:
Sonu Sahadevan, Katharina M. Hembach, Elena Tantardini, Manuela Pérez-Berlanga, Marian Hruska-Plochan, Salim Megat, Julien Weber, Petra Schwarz, Luc Dupuis, Mark D. Robinson, Pierre De Rossi, Magdalini Polymenidou
Publikováno v:
Nature Communications, Vol 12, Iss 1, Pp 1-17 (2021)
Mutations in the RNA-binding protein FUS contribute to ALS. Here the authors use CLIP-seq on synaptoneurosomes to identify proteins associated with synapse organization and plasticity that are differentially regulated in a knock-in ALS mouse model.
Externí odkaz:
https://doaj.org/article/e9c043534e61495b8e1dfb249245ca1e
Autor:
Marc Emmenegger, Elena De Cecco, Marian Hruska‐Plochan, Timo Eninger, Matthias M Schneider, Melanie Barth, Elena Tantardini, Pierre de Rossi, Mehtap Bacioglu, Rebekah G Langston, Alice Kaganovich, Nora Bengoa‐Vergniory, Andrès Gonzalez‐Guerra, Merve Avar, Daniel Heinzer, Regina Reimann, Lisa M Häsler, Therese W Herling, Naunehal S Matharu, Natalie Landeck, Kelvin Luk, Ronald Melki, Philipp J Kahle, Simone Hornemann, Tuomas P J Knowles, Mark R Cookson, Magdalini Polymenidou, Mathias Jucker, Adriano Aguzzi
Publikováno v:
EMBO Molecular Medicine, Vol 13, Iss 9, Pp n/a-n/a (2021)
Abstract While the initial pathology of Parkinson’s disease and other α‐synucleinopathies is often confined to circumscribed brain regions, it can spread and progressively affect adjacent and distant brain locales. This process may be controlled
Externí odkaz:
https://doaj.org/article/7994f076bf964ea9bf26f7f4ba6a434a
Autor:
Pierre De Rossi, Toshihiro Nomura, Robert J. Andrew, Nicolas Y. Masse, Vandana Sampathkumar, Timothy F. Musial, Ari Sudwarts, Aleksandra J. Recupero, Thomas Le Metayer, Mitchell T. Hansen, Ha-Na Shim, Sofia V. Krause, David J. Freedman, Vytas P. Bindokas, Narayanan Kasthuri, Daniel A. Nicholson, Anis Contractor, Gopal Thinakaran
Publikováno v:
Cell Reports, Vol 30, Iss 10, Pp 3520-3535.e7 (2020)
Summary: BIN1, a member of the BAR adaptor protein family, is a significant late-onset Alzheimer disease risk factor. Here, we investigate BIN1 function in the brain using conditional knockout (cKO) models. Loss of neuronal Bin1 expression results in
Externí odkaz:
https://doaj.org/article/3ee20aa26dbb4398a318c588047a8aa8
Autor:
Melanie, Jambeau, Kevin D, Meyer, Marian, Hruska-Plochan, Ricardos, Tabet, Chao-Zong, Lee, Ananya, Ray-Soni, Corey, Aguilar, Kitty, Savage, Nibha, Mishra, Nicole, Cavegn, Petra, Borter, Chun-Chia, Lin, Karen R, Jansen-West, Jie, Jiang, Fernande, Freyermuth, Nan, Li, Pierre, De Rossi, Manuela, Pérez-Berlanga, Xin, Jiang, Lilian M, Daughrity, João, Pereira, Sarav, Narayanan, Yuanzheng, Gu, Shekhar, Dhokai, Isin, Dalkilic-Liddle, Zuzanna, Maniecka, Julien, Weber, Michael, Workman, Melissa, McAlonis-Downes, Eugene, Berezovski, Yong-Jie, Zhang, James, Berry, Brian J, Wainger, Mark W, Kankel, Mia, Rushe, Christoph, Hock, Roger M, Nitsch, Don W, Cleveland, Leonard, Petrucelli, Tania F, Gendron, Fabio, Montrasio, Jan, Grimm, Magdalini, Polymenidou, Clotilde, Lagier-Tourenne
Publikováno v:
Proceedings of the National Academy of Sciences of the United States of America. 119(49)
Hexanucleotide G
Publikováno v:
Developmental Cell. 55:45-68
Protein aggregation is the main hallmark of neurodegenerative diseases. Many proteins found in pathological inclusions are known to undergo liquid-liquid phase separation, a reversible process of molecular self-assembly. Emerging evidence supports th
Autor:
Pierre De Rossi, Johanna Furrer, Tammaryn Lashley, Magdalini Polymenidou, Stefano Scaramuzza, Weijia Zhong, Amanda J Lewis, Ashraf Al-Amoudi, Vera I. Wiersma, Daniel Castaño-Díez, Carolin Böing, Julien Weber, Tomas Demeter, Henning Stahlberg, Manuela Pérez-Berlanga, Zhongning Guo, Marta Di Fabrizio, Carlo Scialo, Laura De Vos, Aurélie Zbinden
Publikováno v:
EMBO Reports
Morphologically distinct TDP‐43 aggregates occur in clinically different FTLD‐TDP subtypes, yet the mechanism of their emergence and contribution to clinical heterogeneity are poorly understood. Several lines of evidence suggest that pathological
Autor:
Adriano Aguzzi, Mathias Jucker, Magdalini Polymenidou, Mark R. Cookson, Tuomas P. J. Knowles, Simone Hornemann, Philipp J. Kahle, Ronald Melki, Kelvin Luk, Natalie Landeck, Naunehal S. Matharu, Therese W. Herling, Lisa M. Häsler, Regina Reimann, Daniel Heinzer, Merve Avar, Andrès Gonzalez-Guerra, Nora Bengoa-Vergniory, Alice Kaganovich, Rebekah G. Langston, Mehtap Bacioglu, Pierre de Rossi, Elena Tantardini, Melanie Barth, Matthias M. Schneider, Timo Eninger, Marian Hruska-Plochan, Elena De Cecco, Marc Emmenegger
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_________::7fcdc8bbb95533537cf9843e591965a2
https://doi.org/10.15252/rc.2022275692
https://doi.org/10.15252/rc.2022275692