Zobrazeno 1 - 10
of 1 636
pro vyhledávání: '"Neonatal cholestasis"'
Autor:
Sunayana Misra, Sonia Badwal, Shashi Dhawan, Arpita Mittal, Naimish Mehta, Nishant Wadhwa, Arjun Maria
Publikováno v:
Autopsy and Case Reports, Vol 14 (2024)
Biliary atresia (BA) is a progressive inflammatory cholangiopathy of infancy that results in fibrous obliteration of the extrahepatic and intrahepatic bile ducts. In untreated patients, this leads to biliary-type cirrhosis within the first two years
Externí odkaz:
https://doaj.org/article/667e2eed71bb4f81b94e6d70cea01873
Publikováno v:
RUHS Journal of Health Sciences (2024)
Introduction: Neonatal cholestasis (NC) affect one in 2500 live births and is an important cause of chronic liver disease in young children. Biliary atresia (BA) and neonatal hepatitis (NH) are the two major causes of NC. However, both conditions hav
Externí odkaz:
https://doaj.org/article/dcf54d006bf14748898389e1f2e0265a
Autor:
Alif Abdelhakim Allam, Mohammed Ahmed Khedr, Shimaa Saad Elkholy, Takwa Abd El Rahman Yassin, Ola Ahmed Fouad
Publikováno v:
Egyptian Liver Journal, Vol 14, Iss 1, Pp 1-7 (2024)
Abstract Background Biliary atresia (BA) is an obliterative cholangiopathy of infancy that results in cholestasis and liver fibrosis. This fibrosis is due to an imbalance in extracellular matrix (ECM) breakdown and deposition. The mechanism by which
Externí odkaz:
https://doaj.org/article/63a8e24876f84e96b8507f55df45ff82
Autor:
Homoud Alhebbi, Mohammed El-Edreesi, Mohammed Abanemai, Omar Saadah, Maher Alhatlani, Hana Halabi, Razan Bader, Ahmed Al Sarkhy, Ahmed Aladsani, Sami Wali, Talal Alguofi, Nawaf Alkhathran, Amira NasserAllah, Muhammed Salman Bashir, Abdulrahman Al-Hussaini
Publikováno v:
The Saudi Journal of Gastroenterology, Vol 30, Iss 2, Pp 89-95 (2024)
Background: We utilized the data from the Saudi national biliary atresia (BA) study (2000–2018) to describe the clinical, biochemical, imaging, and histopathological features of BA and the perioperative clinical practices among local pediatric gast
Externí odkaz:
https://doaj.org/article/0719f0c11b474f27ad72af045f30df34
Autor:
Federico Beati, Antonella Mosca, Andrea Pietrobattista, Daniela Liccardo, Sara Ronci, Lidia Monti, Paola Francalanci, Marco Spada, Giuseppe Maggiore, Pietro Bagolan, Fabio Fusaro
Publikováno v:
Frontiers in Surgery, Vol 11 (2024)
IntroductionThe diagnosis of biliary atresia (BA) remains challenging, and there is still uncertainty regarding the optimal time to perform a Kasai portoenterostomy (KPE). Little is known about the difficulties in the diagnosis and outcomes of BA in
Externí odkaz:
https://doaj.org/article/e00dc5e68438413cadbb215806e95669
Publikováno v:
Egyptian Liver Journal, Vol 13, Iss 1, Pp 1-8 (2023)
Abstract Background Alagille syndrome is a rare autosomal-dominant disorder, representing 10 to 15% of the causes of neonatal cholestasis with no gender predominance. The diagnosis is based on the association of liver, heart, eye, skeleton abnormalit
Externí odkaz:
https://doaj.org/article/b93a2d68f90d4028a017786210e22ffb
Publikováno v:
BMC Pediatrics, Vol 23, Iss 1, Pp 1-7 (2023)
Abstract Background and aims Early diagnosis of biliary atresia (BA), particularly distinguishing it from other causes of neonatal cholestasis (NC), is challenging. This study aimed to design and validate a predictive model for BA by using the data a
Externí odkaz:
https://doaj.org/article/616a698aed144c7e86141d0d86961de4
Publikováno v:
Pakistan Armed Forces Medical Journal, Vol 73, Iss 5 (2023)
Objective: To determine the frequencies of various etiologies of neonatal cholestasis diagnosed by clinical findings and laboratory investigations at the Pak Emirates Military Hospital, Rawalpindi, Pakistan. Study Design: Cross-sectional study. P
Externí odkaz:
https://doaj.org/article/10e76c61bff54569b4d37d8c5514ef19
Publikováno v:
Clinical Case Reports, Vol 12, Iss 2, Pp n/a-n/a (2024)
Abstract Farnesoid X receptor (FXR) is a nuclear bile acid receptor encoded by the NR1H4 gene, a vital regulator of bile acid homeostasis. Pathogenic mutations of NR1H4 manifest as low gamma‐glutamyl transferase (GGT) cholestasis with rapid progres
Externí odkaz:
https://doaj.org/article/a41a91df022e4e288190c29660cf935d
Publikováno v:
Frontiers in Pediatrics, Vol 11 (2023)
AimThis study aimed to summarize and show the characteristics and evolutionary process of neonatal cholestasis caused by McCune–Albright syndrome (MAS), as neonatal cholestasis may be the initial manifestation of MAS before other classic clinical f
Externí odkaz:
https://doaj.org/article/90807bb4212843c38ccd20968c95969e