Zobrazeno 1 - 10
of 41
pro vyhledávání: '"Natássia M. Vieira"'
Autor:
Genri Kawahara, Matthew S. Alexander, Mayana Zatz, Lillian Mead, Yuri B Moreira, Sergio Verjovski-Almeida, Natássia M. Vieira, Janelle M. Spinazzola, Louis M. Kunkel, Devin E. Gibbs
Publikováno v:
Repositório Institucional da USP (Biblioteca Digital da Produção Intelectual)
Universidade de São Paulo (USP)
instacron:USP
Universidade de São Paulo (USP)
instacron:USP
Duchenne muscular dystrophy (DMD) is a progressive muscle wasting disease caused by X-linked inherited mutations in the DYSTROPHIN (DMD) gene. Absence of dystrophin protein from the sarcolemma causes severe muscle degeneration, fibrosis, and inflamma
Autor:
Jeffrey J. Widrick, Omar Moukha-Chafiq, Angela Lek, Daniela Garcia-Perez, Michael J. Feyder, Devin E. Gibbs, Corinne E. Augelli-Szafran, Rylie M Hightower, Natássia M. Vieira, Louis M. Kunkel, Genri Kawahara, Matthew S. Alexander, Peter R. Serafini
Publikováno v:
JCI insight. 3(18)
Zebrafish are a powerful tool for studying muscle function owing to their high numbers of offspring, low maintenance costs, evolutionarily conserved muscle functions, and the ability to rapidly take up small molecular compounds during early larval st
Autor:
Norio Motohashi, Angela Lek, Peter B. Kang, Fedik Rahimov, Louis M. Kunkel, Jeffrey J. Widrick, Jamie L. Marshall, Frederic Shapiro, Molly Gasperini, Elicia Estrella, Genri Kawahara, Matthew S. Alexander, Natássia M. Vieira, Jennifer Myers, Iris Eisenberg, Juan Carlos Casar
Publikováno v:
Journal of Clinical Investigation. 124:2651-2667
Duchenne muscular dystrophy (DMD) is caused by mutations in the gene encoding dystrophin, which results in dysfunctional signaling pathways within muscle. Previously, we identified microRNA-486 (miR-486) as a muscle-enriched microRNA that is markedly
Autor:
Carlos Roberto Bueno, Natássia M. Vieira, Tatiana Jazedje, M. Valadares, Eder Zucconi, Mariane Secco, Mayana Zatz, Paolo Bartolini, Miriam F. Suzuki, Mariz Vainzof
Publikováno v:
Journal of Biomedicine and Biotechnology
Journal of Biomedicine and Biotechnology, Vol 2011 (2011)
Repositório Institucional da USP (Biblioteca Digital da Produção Intelectual)
Universidade de São Paulo (USP)
instacron:USP
Journal of Biomedicine and Biotechnology, Vol 2011 (2011)
Repositório Institucional da USP (Biblioteca Digital da Produção Intelectual)
Universidade de São Paulo (USP)
instacron:USP
Umbilical cord mesenchymal stromal cells (MSC) have been widely investigated for cell-based therapy studies as an alternative source to bone marrow transplantation. Umbilical cord tissue is a rich source of MSCs with potential to derivate at least mu
Autor:
Daniela Franco Bueno, Maria Rita Passos-Bueno, Mariane Secco, Maria Angélica Miglino, Tatiana Jazedje, Mayana Zatz, Natássia M. Vieira, Eder Zucconi, Carlos Eduardo Ambrósio
Publikováno v:
Repositório Institucional da USP (Biblioteca Digital da Produção Intelectual)
Universidade de São Paulo (USP)
instacron:USP
Universidade de São Paulo (USP)
instacron:USP
The canine model provides a large animal system to evaluate many treatment modalities using stem cells (SCs). However, only bone marrow (BM) protocols have been widely used in dogs for preclinical approaches. BM donation consists of an invasive proce
Autor:
V. Brandalise, Mayana Zatz, Paolo Bartolini, Mariane Secco, Patricia Chakur Brum, Mariz Vainzof, Maristela M. de Camargo, Luciana Vieira de Moraes, Eder Zucconi, Miriam F. Suzuki, Carlos Roberto Bueno, Natássia M. Vieira
Publikováno v:
Stem Cells. 26:2391-2398
Limb-girdle muscular dystrophies (LGMDs) are a heterogeneous group of disorders characterized by progressive degeneration of skeletal muscle caused by the absence of or defective muscular proteins. The murine model for limb-girdle muscular dystrophy
Autor:
Yuri B Moreira, J. Gomes, Kerstin Lindblad-Toh, Natássia M. Vieira, Matthew S. Alexander, Elinor K. Karlsson, Ingegerd Elvers, Sergio Verjovski-Almeida, Alal Eran, Jamie L. Marshall, Mayana Zatz, Louis M. Kunkel
Publikováno v:
Repositório Institucional da USP (Biblioteca Digital da Produção Intelectual)
Universidade de São Paulo (USP)
instacron:USP
Universidade de São Paulo (USP)
instacron:USP
SummaryDuchenne muscular dystrophy (DMD), caused by mutations at the dystrophin gene, is the most common form of muscular dystrophy. There is no cure for DMD and current therapeutic approaches to restore dystrophin expression are only partially effec
Autor:
J. Gomes, Mariz Vainzof, M.C. Garcia Otaduy, Mayana Zatz, A.B. Martins-Bach, V. Landini, Mayra Pelatti, G. Bento dos Santos, Telma Gonçalves Carneiro Spera de Andrade, Eder Zucconi, Natássia M. Vieira, Edson Amaro
Publikováno v:
Repositório Institucional da USP (Biblioteca Digital da Produção Intelectual)
Universidade de São Paulo (USP)
instacron:USP
Universidade de São Paulo (USP)
instacron:USP
Here we summarize the clinical history of Ringo, a golden retriever muscular dystrophy (GRMD) dog, who had a mild phenotype despite the absence of muscle dystrophin. Ringo died of cardiac arrest at age 11 and therefore displayed a normal lifespan. On
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::10a9a95e24b9e604a2520255e9baddc2
Autor:
Rita de Cássia M. Pavanello, Maya Schuldiner, Luciana Licinio, João Paulo Kitajima, Natássia M. Vieira, Vincenzo Nigro, Michel S Naslavsky, Louis M. Kunkel, Mariz Vainzof, Cristina Vasquez, Peter R. Serafini, Nury Sanchez, David Schlesinger, Lihi Gal, Natale Cavaçana, Fernando Kok, Adriana Mimbacas, Mayana Zatz, Silvia G. Chuartzman
Publikováno v:
Repositório Institucional da USP (Biblioteca Digital da Produção Intelectual)
Universidade de São Paulo (USP)
instacron:USP
Universidade de São Paulo (USP)
instacron:USP
Limb-girdle muscular dystrophies (LGMD) are a heterogeneous group of genetically determined muscle disorders with a primary or predominant involvement of the pelvic or shoulder girdle musculature. More than 20 genes with autosomal recessive (LGMD2A t
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::01f3f1a967780123abc4a358b4e7e055
http://hdl.handle.net/11591/195476
http://hdl.handle.net/11591/195476
Autor:
Lineu Cesar Werneck, Rosana Herminia Scola, Ana Lucila Moreira Carsten, Natássia M. Vieira, Mariz Vainzof, Paulo José Lorenzoni
Publikováno v:
Muscle & Nerve. 36:258-260
Rippling muscle disease (RMD) is a benign myopathy with symptoms and signs of muscular hyperirritability. We report a 17-year-old patient who presented with muscular hypertrophy, local mounding on percussion, and a rippling phenomenon. Needle electro