Natural history of liver disease in a large international cohort of children with Alagille syndrome: Results from the GALA study

Autor: Shannon M, Vandriel, Li-Ting, Li, Huiyu, She, Jian-She, Wang, Melissa A, Gilbert, Irena, Jankowska, Piotr, Czubkowski, Dorota, Gliwicz-Miedzińska, Emmanuel M, Gonzales, Emmanuel, Jacquemin, Jérôme, Bouligand, Nancy B, Spinner, Kathleen M, Loomes, David A, Piccoli, Lorenzo, D'Antiga, Emanuele, Nicastro, Étienne, Sokal, Tanguy, Demaret, Noelle H, Ebel, Jeffrey A, Feinstein, Rima, Fawaz, Silvia, Nastasio, Florence, Lacaille, Dominique, Debray, Henrik, Arnell, Björn, Fischler, Susan, Siew, Michael, Stormon, Saul J, Karpen, Rene, Romero, Kyung Mo, Kim, Woo Yim, Baek, Winita, Hardikar, Sahana, Shankar, Amin J, Roberts, Helen M, Evans, M Kyle, Jensen, Marianne, Kavan, Shikha S, Sundaram, Alexander, Chaidez, Palaniswamy, Karthikeyan, Maria Camila, Sanchez, Maria Lorena, Cavalieri, Henkjan J, Verkade, Way Seah, Lee, James E, Squires, Christina, Hajinicolaou, Chatmanee, Lertudomphonwanit, Ryan T, Fischer, Catherine, Larson-Nath, Yael, Mozer-Glassberg, Cigdem, Arikan, Henry C, Lin, Jesus Quintero, Bernabeu, Seema, Alam, Deirdre A, Kelly, Elisa, Carvalho, Cristina Targa, Ferreira, Giuseppe, Indolfi, Ruben E, Quiros-Tejeira, Pinar, Bulut, Pier Luigi, Calvo, Zerrin, Önal, Pamela L, Valentino, Dev M, Desai, John, Eshun, Maria, Rogalidou, Antal, Dezsőfi, Sabina, Wiecek, Gabriella, Nebbia, Raquel Borges, Pinto, Victorien M, Wolters, María Legarda, Tamara, Andréanne N, Zizzo, Jennifer, Garcia, Kathleen, Schwarz, Marisa, Beretta, Thomas Damgaard, Sandahl, Carolina, Jimenez-Rivera, Nanda, Kerkar, Jernej, Brecelj, Quais, Mujawar, Nathalie, Rock, Cristina Molera, Busoms, Wikrom, Karnsakul, Eberhard, Lurz, Ermelinda, Santos-Silva, Niviann, Blondet, Luis, Bujanda, Uzma, Shah, Richard J, Thompson, Bettina E, Hansen, Binita M, Kamath

Publikováno v: Hepatology
Vandriel, S M, Li, L T, She, H, Wang, J S, Gilbert, M A, Jankowska, I, Czubkowski, P, Gliwicz-Miedzińska, D, Gonzales, E M, Jacquemin, E, Bouligand, J, Spinner, N B, Loomes, K M, Piccoli, D A, D'Antiga, L, Nicastro, E, Sokal, É, Demaret, T, Ebel, N H, Feinstein, J A, Fawaz, R, Nastasio, S, Lacaille, F, Debray, D, Arnell, H, Fischler, B, Siew, S, Stormon, M, Karpen, S J, Romero, R, Kim, K M, Baek, W Y, Hardikar, W, Shankar, S, Roberts, A J, Evans, H M, Jensen, M K, Kavan, M, Sundaram, S S, Chaidez, A, Karthikeyan, P, Sanchez, M C, Cavalieri, M L, Verkade, H J, Lee, W S, Squires, J E, Hajinicolaou, C, Lertudomphonwanit, C, Fischer, R T, Sandahl, T D & The Global ALagille Alliance (GALA) Study Group 2023, ' Natural history of liver disease in a large international cohort of children with Alagille syndrome : Results from the GALA study ', Hepatology, vol. 77, no. 2 . https://doi.org/10.1002/hep.32761
Hepatology, Vol. 77, no. 2, p. 512-529 (2023)

Background and aims: Alagille syndrome (ALGS) is a multisystem disorder, characterized by cholestasis. Existing outcome data are largely derived from tertiary centers, and real-world data are lacking. This study aimed to elucidate the natural history

Externí odkaz: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::8fa081634c7928ab2481736e90c3d8a8
https://doi.org/10.1002/hep.32761

Chymase-positive Mast cells correlate with tumor angiogenesis: first report in pancreatic cancer patients

Autor: C, Laface, M, Laforgia, A F, Zito, D, Loisi, N, Zizzo, R, Tamma, C D, Gadaleta, M, Porcelli, G, Currò, M, Ammendola, G, Ranieri

Publikováno v: European review for medical and pharmacological sciences. 25(22)

Mast cells (MCs) are known to be involved in several physiological and pathological processes in humans and animals. Recently, their potential role in tumor development and angiogenesis has been investigated, arising interesting results to be potenti

Externí odkaz: https://explore.openaire.eu/search/publication?articleId=pmid________::f1a91f7941547a1f435da39b650b6c58
https://pubmed.ncbi.nlm.nih.gov/34859861

Oral administration of nucleotides in calves: Effects on oxidative status, immune response, and intestinal mucosa development

Autor: F.R. Dinardo, A. Maggiolino, T. Martinello, G.M. Liuzzi, G. Elia, N. Zizzo, T. Latronico, F. Mastrangelo, G.E. Dahl, P. De Palo

Publikováno v: Journal of dairy science. 105(5)

The present work aimed to investigate the effects of nucleotide oral administration on oxidative stress biomarkers, immune responses, gut morphology, serum biochemical parameters, and growth performance in calves from birth to 25 d of life. A total o

Externí odkaz: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::df781e28497e00c45030102f1ef3e835
https://pubmed.ncbi.nlm.nih.gov/35248380

Expression of Langerin/CD207 in airways, lung and associated lymph nodes of a stranded striped dolphin (Stenella coeruleoalba)

Autor: Maria Cristina Guerrera, Gioele Capillo, Michał Kuciel, Marialuisa Aragona, Eugenia Rita Lauriano, P. Lo Cascio, Simona Pergolizzi, N. Zizzo

The airways and lungs of vertebrates are an entrance way for several microbial pathogens. Cetaceans present an upper and lower respiratory anatomy that allows the rapid flow of large air volumes, which may lead to high susceptibility to respiratory i

Externí odkaz: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::90145c5bb1a7b0a719c6cc4ec260b27e
https://ruj.uj.edu.pl/xmlui/handle/item/256934

Similarity Network Fusion

Autor: Lauren Erdman, Brian M. Feldman, Anna Goldenberg, Andréanne N Zizzo

Publikováno v: Rheumatic Disease Clinics of North America. 44:285-293

Similarity Network Fusion (SNF) is a novel methodological tool that integrates multiple different types of data to identify homogeneous subsets of patients in whom disease classification may be otherwise unclear or challenging. In this review article

Externí odkaz: https://explore.openaire.eu/search/publication?articleId=doi_________::02f3d12d7a261fac7c2ef5bfd1fe911b
https://doi.org/10.1016/j.rdc.2018.01.005