Zobrazeno 1 - 10
of 18
pro vyhledávání: '"Monica M. Sousa"'
Autor:
Sandra O. Braz, Marlene M. Morgado, Marta I. Pereira, Ana C. Monteiro, Olga Golonzhka, Matthew Jarpe, Pedro Brites, Monica M. Sousa, Joana Nogueira-Rodrigues
Publikováno v:
Frontiers in Molecular Neuroscience, Vol 16 (2023)
IntroductionIn Krabbe disease (KD), mutations in β-galactosylceramidase (GALC), a lysosomal enzyme responsible for the catabolism of galactolipids, leads to the accumulation of its substrates galactocerebroside and psychosine. This neurologic condit
Externí odkaz:
https://doaj.org/article/938f42549aee43a6a1c0e96cc3ea2a06
Publikováno v:
Frontiers in Cellular Neuroscience, Vol 14 (2020)
Externí odkaz:
https://doaj.org/article/cebde4125d344c7abb2a7e6bd64e6aa4
Autor:
Ana Rita Costa, Monica M. Sousa
Publikováno v:
Cells, Vol 9, Iss 9, p 1961 (2020)
By binding to actin filaments, non-muscle myosin II (NMII) generates actomyosin networks that hold unique contractile properties. Their dynamic nature is essential for neuronal biology including the establishment of polarity, growth cone formation an
Externí odkaz:
https://doaj.org/article/f423543bc21c4c2a8745af58ffad3a39
Sensory neurons have an axon initial segment that initiates spontaneous activity in neuropathic pain
Autor:
Ana I. Nascimento, Tiago F. Da Silva, Elisabete C. Fernandes, Liliana L. Luz, Fernando M. Mar, Boris V. Safronov, Monica M. Sousa
Publikováno v:
Brain. 145:1632-1640
The axon initial segment is a specialized compartment of the proximal axon of CNS neurons where action potentials are initiated. However, it remains unknown whether this domain is assembled in sensory dorsal root ganglion neurons, in which spikes are
Autor:
Marta Vitorino, Sónia Simão, João B. Moreira, Joana Nogueira‐Rodrigues, Joana Silva, Ana Sofia Lourenço, Vítor Fernandes, Monica M. Sousa, Gustavo Tiscornia, Inês M. Araújo
Publikováno v:
Journal of Comparative Neurology. 530:2215-2237
The African spiny mouse (Acomys cahirinus) is an emerging model of mammalian epimorphic regeneration that has aroused the interest of the scientific community in the last decade. To date, studies on brain repair have been hindered by the lack of know
Autor:
Pedro Brites, Monica M. Sousa
Publikováno v:
PLOS Biology. 20:e3001706
In this issue of PLOS Biology, Kreher and colleagues show in a mouse model that in vivo, neurons and not only myelinating glia are primary effectors of disease progression in Krabbe disease. The neuron-specific model generated allows the unprecedente
Autor:
Jessica Eira, Joana Magalhães, Nídia Macedo, Maria Elena Pero, Thomas Misgeld, Mónica M. Sousa, Francesca Bartolini, Márcia A. Liz
Publikováno v:
Frontiers in Cell and Developmental Biology, Vol 9 (2021)
Transthyretin (TTR), a plasma and cerebrospinal fluid protein, increases axon growth and organelle transport in sensory neurons. While neurons extend their axons, the microtubule (MT) cytoskeleton is crucial for the segregation of functional compartm
Externí odkaz:
https://doaj.org/article/ce9b46661bcc43f9ac485b03657d5a43
Autor:
Pedro M.D. Moreno, Ana R. Ferreira, Daniela Salvador, Maria T. Rodrigues, Marília Torrado, Eva D. Carvalho, Ulf Tedebark, Mónica M. Sousa, Isabel F. Amaral, Jesper Wengel, Ana P. Pêgo
Publikováno v:
Molecular Therapy: Nucleic Acids, Vol 11, Iss C, Pp 393-406 (2018)
After spinal cord injury (SCI), nerve regeneration is severely hampered due to the establishment of a highly inhibitory microenvironment at the injury site, through the contribution of multiple factors. The potential of antisense oligonucleotides (AO
Externí odkaz:
https://doaj.org/article/b4a65d46d57a47d3873ab1bc90af99e7
Autor:
Ana Rita Costa, Sara C Sousa, Rita Pinto-Costa, José C Mateus, Cátia DF Lopes, Ana Catarina Costa, David Rosa, Diana Machado, Luis Pajuelo, Xuewei Wang, Feng-quan Zhou, António J Pereira, Paula Sampaio, Boris Y Rubinstein, Inês Mendes Pinto, Marko Lampe, Paulo Aguiar, Monica M Sousa
Publikováno v:
eLife, Vol 9 (2020)
Neurons have a membrane periodic skeleton (MPS) composed of actin rings interconnected by spectrin. Here, combining chemical and genetic gain- and loss-of-function assays, we show that in rat hippocampal neurons the MPS is an actomyosin network that
Externí odkaz:
https://doaj.org/article/4602427c5eb7426abce176d9d2beeb7a
Autor:
Chálim Rebelo C; Gastroenterology Division, Divino Espírito Santo Hospital, Ponta Delgada, Portugal., Félix C; Gastroenterology Division, Western Lisbon Hospital Center, Lisbon, Portugal., Cardoso FS; Transplant Unit, Curry Cabral Hospital, Central Lisbon University Hospital Center, Nova Medical School, Nova University, Lisbon, Portugal., Bagulho L; Transplant Unit, Curry Cabral Hospital, Central Lisbon University Hospital Center, Nova Medical School, Nova University, Lisbon, Portugal., Sousa M; Transplant Unit, Curry Cabral Hospital, Central Lisbon University Hospital Center, Nova Medical School, Nova University, Lisbon, Portugal., Mendes M; Transplant Unit, Curry Cabral Hospital, Central Lisbon University Hospital Center, Nova Medical School, Nova University, Lisbon, Portugal., Glória H; Transplant Unit, Curry Cabral Hospital, Central Lisbon University Hospital Center, Nova Medical School, Nova University, Lisbon, Portugal., Mateus É; Transplant Unit, Curry Cabral Hospital, Central Lisbon University Hospital Center, Nova Medical School, Nova University, Lisbon, Portugal., Mega I; Transplant Unit, Curry Cabral Hospital, Central Lisbon University Hospital Center, Nova Medical School, Nova University, Lisbon, Portugal., Jara M; Transplant Unit, Curry Cabral Hospital, Central Lisbon University Hospital Center, Nova Medical School, Nova University, Lisbon, Portugal., Pinto Marques H; Transplant Unit, Curry Cabral Hospital, Central Lisbon University Hospital Center, Nova Medical School, Nova University, Lisbon, Portugal., Nolasco F; Transplant Unit, Curry Cabral Hospital, Central Lisbon University Hospital Center, Nova Medical School, Nova University, Lisbon, Portugal., Martins A; Transplant Unit, Curry Cabral Hospital, Central Lisbon University Hospital Center, Nova Medical School, Nova University, Lisbon, Portugal., Perdigoto R; Transplant Unit, Curry Cabral Hospital, Central Lisbon University Hospital Center, Nova Medical School, Nova University, Lisbon, Portugal.
Publikováno v:
GE Portuguese journal of gastroenterology [GE Port J Gastroenterol] 2022 Oct 17; Vol. 30 (5), pp. 343-349. Date of Electronic Publication: 2022 Oct 17 (Print Publication: 2023).