Zobrazeno 1 - 10
of 12
pro vyhledávání: '"Monia Souidi"'
Autor:
Monia Souidi, Jessica Resta, Haikel Dridi, Yvonne Sleiman, Steve Reiken, Karina Formoso, Sarah Colombani, Pascal Amédro, Pierre Meyer, Azzouz Charrabi, Marie Vincenti, Yang Liu, Rajesh Kumar Soni, Frank Lezoualc'h, D.V.M. Stéphane Blot, François Rivier, Olivier Cazorla, Angelo Parini, Andrew R. Marks, Jeanne Mialet‐Perez, Alain Lacampagne, Albano C. Meli
Publikováno v:
Journal of Cachexia, Sarcopenia and Muscle, Vol 15, Iss 2, Pp 536-551 (2024)
Abstract Background Duchenne muscular dystrophy (DMD) is an X‐linked disorder characterized by progressive muscle weakness due to the absence of functional dystrophin. DMD patients also develop dilated cardiomyopathy (DCM). We have previously shown
Externí odkaz:
https://doaj.org/article/86cf946208c7405482fdfb4f8454571b
Autor:
Monia Souidi, Pascal Amédro, Pierre Meyer, Romain Desprat, Jean-Marc Lemaître, François Rivier, Alain Lacampagne, Albano C. Meli
Publikováno v:
Stem Cell Research, Vol 49, Iss , Pp 102094- (2020)
Duchenne Muscular Dystrophy (DMD) is a X-linked degenerative pathology with a prevalence of 1/3600–6000 boys due to the absence of functional dystrophin in muscles. This muscular disease leads to skeletal muscle damages, respiratory failure and in
Externí odkaz:
https://doaj.org/article/e27431ff0bcd438bbf860c396382d7e4
Autor:
Yvonne Sleiman, Monia Souidi, Ritu Kumar, Ellen Yang, Fabrice Jaffré, Ting Zhou, Albin Bernardin, Steve Reiken, Olivier Cazorla, Andrey V. Kajava, Adrien Moreau, Jean-Luc Pasquié, Andrew R. Marks, Bruce B. Lerman, Shuibing Chen, Jim W. Cheung, Todd Evans, Alain Lacampagne, Albano C. Meli
Publikováno v:
EBioMedicine, Vol 60, Iss , Pp 103024- (2020)
Background: While mutations in the cardiac type 2 ryanodine receptor (RyR2) have been linked to exercise-induced or catecholaminergic polymorphic ventricular tachycardia (CPVT), its association with polymorphic ventricular tachycardia (PMVT) occurrin
Externí odkaz:
https://doaj.org/article/43897e975f1f4812a71897ef8bcbdfee
Autor:
Monia Souidi, Yvonne Sleiman, Ivana Acimovic, Jan Pribyl, Azzouz Charrabi, Volker Baecker, Valerie Scheuermann, Martin Pesl, Sarka Jelinkova, Petr Skladal, Petr Dvorak, Alain Lacampagne, Vladimir Rotrekl, Albano C. Meli
Publikováno v:
International Journal of Molecular Sciences, Vol 22, Iss 2, p 662 (2021)
Numerous protocols of cardiac differentiation have been established by essentially focusing on specific growth factors on human pluripotent stem cell (hPSC) differentiation efficiency. However, the optimal environmental factors to obtain cardiac myoc
Externí odkaz:
https://doaj.org/article/805299a630e143abb10d726383edcbf9
Autor:
Ivana Acimovic, Marwan M. Refaat, Adrien Moreau, Anton Salykin, Steve Reiken, Yvonne Sleiman, Monia Souidi, Jan Přibyl, Andrey V. Kajava, Sylvain Richard, Jonathan T. Lu, Philippe Chevalier, Petr Skládal, Petr Dvořak, Vladimir Rotrekl, Andrew R. Marks, Melvin M. Scheinman, Alain Lacampagne, Albano C. Meli
Publikováno v:
Journal of Clinical Medicine, Vol 7, Iss 11, p 423 (2018)
Background: Sarcoplasmic reticulum Ca2+ leak and post-translational modifications under stress have been implicated in catecholaminergic polymorphic ventricular tachycardia (CPVT), a highly lethal inherited arrhythmogenic disorder. Human induced plur
Externí odkaz:
https://doaj.org/article/0df57a5a2a95455da2b7be940e229047
Autor:
Volker Baecker, Azzouz Charrabi, Valérie Scheuermann, Albano C. Meli, Jan Pribyl, Martin Pešl, Alain Lacampagne, Vladimír Rotrekl, Šárka Jelínková, Petr Dvorak, Ivana Aćimović, Yvonne Sleiman, Petr Skládal, Monia Souidi
Introduction Human induced pluripotent stem cells (hiPSC) have the ability to differentiate theoritically into any cell type. The development of organoid systems exhibiting the essential features of human organ such as liver and heart is of high inte
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::5e90f3290a3590060266616890726481
https://is.muni.cz/publication/1825817
https://is.muni.cz/publication/1825817
Autor:
Jan Pribyl, Volker Baecker, Šárka Jelínková, Azzouz Charrabi, Valérie Scheuermann, Ivana Aćimović, Petr Dvorak, Alain Lacampagne, Albano C. Meli, Martin Pešl, Vladimír Rotrekl, Yvonne Sleiman, Monia Souidi, Petr Skládal
Publikováno v:
International Journal of Molecular Sciences
Volume 22
Issue 2
International Journal of Molecular Sciences, MDPI, 2021, 22 (2), pp.662. ⟨10.3390/ijms22020662⟩
International Journal of Molecular Sciences, Vol 22, Iss 662, p 662 (2021)
Volume 22
Issue 2
International Journal of Molecular Sciences, MDPI, 2021, 22 (2), pp.662. ⟨10.3390/ijms22020662⟩
International Journal of Molecular Sciences, Vol 22, Iss 662, p 662 (2021)
Numerous protocols of cardiac differentiation have been established by essentially focusing on specific growth factors on human pluripotent stem cell (hPSC) differentiation efficiency. However, the optimal environmental factors to obtain cardiac myoc
Autor:
Jim W. Cheung, Ting Zhou, Todd Evans, Alain Lacampagne, Olivier Cazorla, Ritu Kumar, Ellen Yang, Andrew R. Marks, Fabrice Jaffré, Albano C. Meli, Bruce B. Lerman, Andrey V. Kajava, Albin Bernardin, Shuibing Chen, Steve Reiken, Jean-Luc Pasquié, Adrien Moreau, Monia Souidi, Yvonne Sleiman
Publikováno v:
EBioMedicine
EBioMedicine, Elsevier, 2020, 60, pp.103024. ⟨10.1016/j.ebiom.2020.103024⟩
EBioMedicine, Vol 60, Iss, Pp 103024-(2020)
EBioMedicine, 2020, 60, pp.103024. ⟨10.1016/j.ebiom.2020.103024⟩
EBioMedicine, Elsevier, 2020, 60, pp.103024. ⟨10.1016/j.ebiom.2020.103024⟩
EBioMedicine, Vol 60, Iss, Pp 103024-(2020)
EBioMedicine, 2020, 60, pp.103024. ⟨10.1016/j.ebiom.2020.103024⟩
Background While mutations in the cardiac type 2 ryanodine receptor (RyR2) have been linked to exercise-induced or catecholaminergic polymorphic ventricular tachycardia (CPVT), its association with polymorphic ventricular tachycardia (PMVT) occurring
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::57ec7fa18c6b39543ccb4bfc5e2e65a5
https://hal.archives-ouvertes.fr/hal-03089303/file/PIIS235239642030400X.pdf
https://hal.archives-ouvertes.fr/hal-03089303/file/PIIS235239642030400X.pdf
Autor:
Alain Lacampagne, Albin Bernardin, Andrew R. Marks, Ellen Yang, Ritu Kumar, Jim W. Cheung, Adrien Moreau, Fabrice Jaffré, Ting Zhou, Andrey V. Kajava, Jean-Luc Pasquié, Todd Evans, Yvonne Sleiman, Shuibing Chen, Steve Reiken, Albano C. Meli, Bruce B. Lerman, Monia Souidi, Olivier Cazorla
Publikováno v:
Archives of Cardiovascular Diseases Supplements. 14:89
Introduction Polymorphic ventricular tachycardia (PMVT) can occur in patients with structurally normal hearts and in 8% of cases can lead to sudden cardiac death, typically exercise-induced. The role of the cardiac type 2 ryanodine receptor (RyR2) in
Autor:
A Lacampagne, A Moreau, Yvonne Sleiman, Pascal Amedro, Monia Souidi, François Rivier, A Meli, P Meyer
Publikováno v:
European Heart Journal. 40
Introduction Duchenne Muscular Dystrophy (DMD) is a X-linked degenerative pathology with a prevalence of 1/3500 boys due to absence of functional dystrophin in muscles. In a late stage of DMD, patients developed a dilated cardiomyopathy (DCM) which c