Zobrazeno 1 - 10
of 132
pro vyhledávání: '"Michael Fayon"'
Autor:
Florian Lussac-Sorton, Éléna Charpentier, Sébastien Imbert, Maxime Lefranc, Stéphanie Bui, Michael Fayon, Patrick Berger, Raphaël Enaud, Laurence Delhaes
Publikováno v:
Frontiers in Cellular and Infection Microbiology, Vol 13 (2023)
The advent of CFTR modulators represents a turning point in the history of cystic fibrosis (CF) management, changing profoundly the disease’s clinical course by improving mucosal hydration. Assessing changes in airway and digestive tract microbiome
Externí odkaz:
https://doaj.org/article/1e9452f06d6041ab95eb59458fda8b3a
Autor:
Margaux Gaschignard, Fabien Beaufils, Pauline Gallet, Haude Clouzeau, Joris Menard, Aurélie Costanzo, Lucie Nouard, Laurence Delhaes, Candice Tetard, Thierry Lamireau, Michael Fayon, Stéphanie Bui, Raphaël Enaud
Publikováno v:
Frontiers in Pediatrics, Vol 11 (2023)
BackgroundMalnutrition is both a feature and major cause of morbidity in cystic fibrosis (CF). Therefore, nutritional management is an essential element of patient care. In 2016, an international guideline for nutritional management in patients with
Externí odkaz:
https://doaj.org/article/682cce7a2ef64d4d8591670f3e3482ee
Autor:
Astrid Madsen Ring, Nicolaus Schwerk, Nural Kiper, Ayse Tana Aslan, Paul Aurora, Roser Ayats, Ines Azevedo, Teresa Bandeira, Julia Carlens, Silvia Castillo-Corullon, Nazan Cobanoglu, Basil Elnazir, Nagehan Emiralioğlu, Tugba Sismanlar Eyuboglu, Michael Fayon, Tugba Ramaslı Gursoy, Claire Hogg, Karsten Kötz, Bülent Karadag, Vendula Látalová, Katarzyna Krenke, Joanna Lange, Effrosyni D. Manali, Borja Osona, Spyros Papiris, Marijke Proesmann, Philippe Reix, Lea Roditis, Sune Rubak, Nisreen Rumman, Deborah Snijders, Florian Stehling, Laurence Weiss, Ebru Yalcın, Fazilcan Zirek, Andrew Bush, Annick Clement, Matthias Griese, Frederik Fouirnaies Buchvald, Nadia Nathan, Kim Gjerum Nielsen
Publikováno v:
ERJ Open Research, Vol 9, Iss 2 (2023)
Background Paediatric diffuse alveolar haemorrhage (DAH) is a rare heterogeneous condition with limited knowledge on clinical presentation, treatment and outcome. Methods A retrospective, descriptive multicentre follow-up study initiated from the Eur
Externí odkaz:
https://doaj.org/article/583cf26a81df4619a065611a08f4083b
Autor:
Margaux Gaschignard, Fabien Beaufils, Florian Lussac-Sorton, Pauline Gallet, Haude Clouzeau, Joris Menard, Aurélie Costanzo, Lucie Nouard, Laurence Delhaes, Candice Tetard, Thierry Lamireau, Michael Fayon, Stéphanie Bui, Raphaël Enaud
Publikováno v:
Frontiers in Pediatrics, Vol 11 (2023)
BackgroundNutritional status is a major prognostic factor for breathing and the survival of patients with cystic fibrosis (CF). Since 2012, the development of CFTR modulators has considerably transformed the outcome of this disease. Indeed, both lung
Externí odkaz:
https://doaj.org/article/938f1d6cc3a24248b7994597a7e564b2
Autor:
Fabien Beaufils, Raphaël Enaud, François Gallode, Grégory Boucher, Julie Macey, Patrick Berger, Michael Fayon, Stéphanie Bui
Publikováno v:
Frontiers in Pediatrics, Vol 11 (2023)
IntroductionForced spirometry is the gold standard to assess lung function, but its accessibility may be limited. By contrast, home spirometry telemonitoring allows a multi-weekly lung function follow-up but its real-life adherence, reliability, and
Externí odkaz:
https://doaj.org/article/88adcdcea8a14f6f8f237d47468c96ed
Autor:
Abbie Oey, Matthew McClure, Julian A Symons, Sushmita Chanda, John Fry, Patrick F Smith, Kathia Luciani, Michael Fayon, Kulkanya Chokephaibulkit, Rattapon Uppala, Jolanta Bernatoniene, Kenji Furuno, Thorsten Stanley, Dymphy Huntjens, James Witek, and RSV2004 Study Groups
Publikováno v:
PLoS ONE, Vol 18, Iss 7, p e0288271 (2023)
Respiratory syncytial virus (RSV) infection is the leading cause of infant hospitalizations and mortality. Lumicitabine, an oral nucleoside analog was studied for the treatment of RSV. The phase 1b and phase 2b studies reported here assessed the safe
Externí odkaz:
https://doaj.org/article/13cf6106ec36481f850eae5b8cb9155b
Publikováno v:
Journal of Pediatric Surgery Case Reports, Vol 88, Iss , Pp 102515- (2023)
Background: Gastrointestinal (enteric) duplication consists of a tubular or cystic structure that develops along the intestinal tube, with an estimated incidence of 1/10,000 in live births and 1/4500 in necropsies of neonates and fetuses. This congen
Externí odkaz:
https://doaj.org/article/a01c54f4e65247d0a6bb875be2453857
Publikováno v:
Frontiers in Pediatrics, Vol 10 (2022)
BackgroundMany patients with cystic fibrosis (CF) wheeze, and are dubbed as having CF-asthma. Understanding the determinants of such wheezing may avoid unnecessary treatments and open newer treatment avenues.ObjectivesMain: To evaluate the prevalence
Externí odkaz:
https://doaj.org/article/26fc1c8434d649f4bdc7869ee54031c4
Autor:
Stéphanie Bui, Alexandra Masson, Raphaël Enaud, Léa Roditis, Gaël Dournes, François Galode, Cyrielle Collet, Emmanuel Mas, Jeanne Languepin, Michael Fayon, Fabien Beaufils, Marie Mittaine
Publikováno v:
Frontiers in Pediatrics, Vol 9 (2021)
Background: The combination of the CFTR corrector lumacaftor (LUM) and potentiator ivacaftor (IVA) has been labeled in France since 2015 for F508del homozygote cystic fibrosis (CF) patients over 12 years. In this real-life study, we aimed (i) to comp
Externí odkaz:
https://doaj.org/article/cf2af5d930334a16a3f31dfa40ab41d4
Autor:
Michael Fayon, Fabien Beaufils
Publikováno v:
ERJ Open Research, Vol 7, Iss 3 (2021)
Alone or in association with other lung or thorax component disorders, the airway wall (AWW) remains one of the most frequently involved elements in paediatric lung diseases. A myriad of AWW disorders will present with similar symptomatology. It is t
Externí odkaz:
https://doaj.org/article/96fb3cb7f7c24a00a6aef60c195df87d