Zobrazeno 1 - 5
of 5
pro vyhledávání: '"Martha C. McKean"'
Publikováno v:
Journal of Cellular Biochemistry. 61:118-126
Constitutive expression of nuclear genes encoding mitochondrial proteins raises the question of whether these proteins are present in similar amounts in mitochondria of different tissues. We report that amounts of a single multienzyme complex can var
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_________::c999035194f7348e927c4cf8d3e06e21
https://doi.org/10.1002/(sici)1097-4644(19960401)61:1<118::aid-jcb13>3.0.co
https://doi.org/10.1002/(sici)1097-4644(19960401)61:1<118::aid-jcb13>3.0.co
Publikováno v:
Biochimica et Biophysica Acta (BBA) - Gene Structure and Expression. 1171:109-112
The 5' end including the start AUG codon has been defined for the human E1 alpha subunit of the branched chain alpha-ketoacid dehydrogenase complex by rapid amplification of cDNA ends. Considering conservative substitutions the amino acid sequence in
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::a3746375c0062ab9ede4eb0f09be973d
https://doi.org/10.1016/0167-4781(92)90149-t
https://doi.org/10.1016/0167-4781(92)90149-t
Publikováno v:
Biochemical medicine and metabolic biology. 49(3)
Maple syrup urine disease results from inherited defects in human nuclear genes for branched chain α-ketoacid dehydrogenase, a mitochondrial multienzyme complex. Thiamin pyrophosphate is necessary for complex activity and a thiamin-responsive form o
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::926d505403750d568ae5d3b721709730
https://pubmed.ncbi.nlm.nih.gov/8347380
https://pubmed.ncbi.nlm.nih.gov/8347380
Publikováno v:
Biochimica et Biophysica Acta (BBA) - Molecular Cell Research. (3):385-392
Components of the mitochondrial branched chain alpha-ketoacid dehydrogenase multienzyme complex are all encoded by nuclear genes. The functional complex is formed with a known stoichiometric relationship of subunits, but how they enter the mitochondr
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::e8dad7fe98f325782125fdcd7162833c
Publikováno v:
Biochemical and biophysical research communications. 102(4)
Summary The kinetics of reduction of the electron transfer flavoprotein were investigated by fluorimetric analysis of kinetic single progress curves. The steady state reaction was catalyzed by the general acyl CoA dehydrogenase and-butyryl CoA under
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::f3faab32c1e300741f8180ee9c7d86d5
https://pubmed.ncbi.nlm.nih.gov/7317051
https://pubmed.ncbi.nlm.nih.gov/7317051