Zobrazeno 1 - 10
of 11
pro vyhledávání: '"Marion Malphette"'
Autor:
Filippo Consonni, Solange Moreno, Blanca Vinuales Colell, Marie-Claude Stolzenberg, Alicia Fernandes, Mélanie Parisot, Cécile Masson, Nathalie Neveux, Jérémie Rosain, Sarah Bamberger, Marie-Gabrielle Vigue, Marion Malphettes, Pierre Quartier, Capucine Picard, Frédéric Rieux-Laucat, Aude Magerus
Publikováno v:
Cell Death and Disease, Vol 15, Iss 5, Pp 1-8 (2024)
Abstract Autoimmune lymphoproliferative syndrome (ALPS) is a primary disorder of lymphocyte homeostasis, leading to chronic lymphoproliferation, autoimmune cytopenia, and increased risk of lymphoma. The genetic landscape of ALPS includes mutations in
Externí odkaz:
https://doaj.org/article/5165021b955642a8b654e38c4a24da9d
Autor:
Heba M. Bintalib, Annick van de Ven, Joseph Jacob, Jesper Rømhild Davidsen, Børre Fevang, Leif G. Hanitsch, Marion Malphettes, Joris van Montfrans, Paul J. Maglione, Cinzia Milito, John Routes, Klaus Warnatz, John R. Hurst
Publikováno v:
Frontiers in Immunology, Vol 14 (2023)
IntroductionCommon variable immunodeficiency related interstitial lung disease (CVID-ILD, also referred to as GLILD) is generally considered a manifestation of systemic immune dysregulation occurring in up to 20% of people with CVID. There is a lack
Externí odkaz:
https://doaj.org/article/d8800fa1ddb14578bcf8cfe3598dc115
Autor:
Thomas Ballul, Nabil Belfeki, Adèle deMasson, Véronique Meignin, Paul‐Louis Woerther, Antoine Martin, Elsa Poullot, Alain Wargnier, Jehane Fadlallah, Margaux Garzaro, Marion Malphettes, Claire Fieschi, Lucas Maisonobe, Hayat Bensekhri, Hélène Guillot, Rémi Bertinchamp, Marie Jachiet, Justine Poirot, Lionel Galicier, Eric Oksenhendler, David Boutboul
Publikováno v:
eJHaem, Vol 3, Iss 1, Pp 175-179 (2022)
Abstract Idiopathic multicentric Castleman disease (iMCD) is a lymphoproliferative disease of unknown etiology. Deciphering mechanisms involved in CD pathogenesis may help improving patients’ care. Six cases of stereotyped sub‐diaphragmatic iMCD
Externí odkaz:
https://doaj.org/article/b4f732957dcd4b52b76435837b644497
Autor:
John R. Hurst, S. Hamza Abbas, Heba M. Bintalib, Tiago M. Alfaro, Ulrich Baumann, Siobhan O. Burns, Alison Condliffe, Jesper R. Davidsen, Børre Fevang, Andrew R. Gennery, Filomeen Haerynck, Joseph Jacob, Stephen Jolles, Olivia Lamers, Anne Bergeron, Marion Malphettes, Véronique Meignin, Cinzia Milito, Tomas Milota, Martine Pergent, Antje Prasse, Isabella Quinti, Elisabetta Renzoni, Anna Sediva, Daiana Stolz, Bas Smits, Friedolin Strauss, Annick A.J.M. van de Ven, Joris van Montfrans, Klaus Warnatz
Publikováno v:
ERJ Open Research, Vol 7, Iss 4 (2021)
Externí odkaz:
https://doaj.org/article/7084a0aa8f714798a22a64d7160cde09
Autor:
Annick A. J. M. van de Ven, Tiago M. Alfaro, Alexandra Robinson, Ulrich Baumann, Anne Bergeron, Siobhan O. Burns, Alison M. Condliffe, Børre Fevang, Andrew R. Gennery, Filomeen Haerynck, Joseph Jacob, Stephen Jolles, Marion Malphettes, Véronique Meignin, Tomas Milota, Joris van Montfrans, Antje Prasse, Isabella Quinti, Elisabetta Renzoni, Daiana Stolz, Klaus Warnatz, John R. Hurst
Publikováno v:
Frontiers in Immunology, Vol 11 (2020)
BackgroundGranulomatous–lymphocytic interstitial lung disease (GLILD) is a rare, potentially severe pulmonary complication of common variable immunodeficiency disorders (CVID). Informative clinical trials and consensus on management are lacking.Aim
Externí odkaz:
https://doaj.org/article/625d212677e24968b931601b81cbe36d
Autor:
Mathilde Bahuaud, Hélène Bodilis, Marion Malphettes, Anaïs Maugard Landre, Caroline Matondo, Didier Bouscary, Frédéric Batteux, Odile Launay, Jean-Paul Fermand
Publikováno v:
Heliyon, Vol 3, Iss 11, Pp e00441- (2017)
Smoldering multiple myeloma (SMM) is an asymptomatic clonal plasma cell disorder that frequently progress to multiple myeloma (MM), a disease at high risk of pneumococcal infections. Moreover, if the polysaccharide vaccine is poorly immunogenic in MM
Externí odkaz:
https://doaj.org/article/426eacf929be477588f7749c9ee4d393
Autor:
Marion Malphettes, Pauline Bonnet, Pierre Schneider, Marguerite Vignon, Marine Baron, Jean-David Bouaziz, Maxime Battistella
Publikováno v:
Acta Dermato-Venereologica, Vol 98, Iss 1, Pp 140-141 (2017)
Externí odkaz:
https://doaj.org/article/7fde1acd21d04cd797022f2064b95656
Autor:
Tom Le Voyer, Adrian Gervais, Jérémie Rosain, Audrey Parent, Axel Cederholm, Darawan Rinchai, Lucy Bizien, Gonca Hancioglu, Quentin Philippot, Mame Sokhna Gueye, Majistor Raj Luxman, Maglorius Renkilaraj, Masato Ogishi, Camille Soudée, Mélanie Migaud, Flore Rozenberg, Mana Momenilandi, Quentin Riller, Luisa Imberti, Ottavia Delmonte, Gabriele Müller, Bärbel Keller, Julio Orrego, William Alexander Gallego, Tamar Rubin, Melike Emiroglu, Nima Parvaneh, Daniel Eriksson, Maribel Aranda-Guillen, David I Berrios, Linda Vong, Connie H Katelaris, Peter Mustillo, Johannes Rädler, Jonathan Bohlen, Jale Bengi Celik, Camila Astudillo, Sarah Winter, Audrey Guichard, Vivien Béziat, Jacinta Bustamante, Qiang Pan-Hammarström, Yu Zhang, Lindsey B Rosen, Steve M Holland, Heather Kenney, Kaan Boztuğ, Nizar Mahlaoui, Sylvain Latour, Roshini Abraham, Vassilios Lougaris, Fabian Hauck, Anna Sediva, Faranaz Atschekzei, M Cecilia Poli, Mary A Slatter, Boaz Palterer, Michael D Keller, Alberto Pinzon-Charry, Anna Sullivan, Luke Droney, Daniel Suan, Nathalie Aladjidi, Miguel Hie, Estibaliz Lazaro, Jose Franco, Sevgi Keles, Marion Malphette, Marlene Pasquet, Maria Elena Maccari, Andrea Meinhardt, Aydan Ikinciogullari, Mohammad Shahrooei, Fatih Celmeli, Patrick Frosk, Christopher C Goodnow, Paul E Gray, Alexandre Belot, Hye Sun Kuehn, Sergio D Rosenzweig, Francesco Licciardi, Amélie Servettaz, Vincent Barlogis, Guillaume Le Guenno, Vera-Maria Herrmann, Taco Kuijpers, Grégoire Ducoux, Françoise Sarrot-Reynauld, Catharina Schuetz, Charlotte Cunningham-Rundles, Frédéric Rieux-Laucat, Stuart G Tangye, Cristina Sobacchi, Rainer Doffinger, Klaus Warnatz, Bodo Grimbacher, Claire Fieschi, Laureline Berteloot, Vanessa Bryant, Sophie Trouillet Assant, Luigi D Notarangelo, Helen Su, Benedicte Neven, Laurent Abel, Qian Zhang, Bertrand Boisson, Aurélie Cobat, Emmanuelle Jouanguy, Olle Kampe, Paul Bastard, Chaim Roifman, Nils Landegren, Mark S Anderson, Jean-Laurent Casanova, Anne Puel
Patients with inborn errors of the alternative NF-κB pathway have low thymic AIRE expression, leading to the development of auto-Abs neutralizing type I IFNs, and severe viral diseases.
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_________::eb3fe31795f551fbeac7e72b123ffd53
https://doi.org/10.22541/au.167330741.18394805/v1
https://doi.org/10.22541/au.167330741.18394805/v1
Autor:
Raphael Szalat, Régis Peffault de Latour, Gérard Socié, Bertrand Arnulf, Lionel Karlin, Sylvie Chevret, Lionel Ades, Sophie Bernard, Jean Paul Fermand, Marion Malphette, Stephanie Harel, Marie Robin, Bouchra Asli
Publikováno v:
Blood. 120:2035-2035
Abstract 2035 Background: We previously reported 23 MM patients, treated in first relapse by a sequential autologous-allogeneic tandem transplantation (aATT) approach. Data from this series compared favorably with a non allografted control population
Autor:
Marie Sarah Dilhuydy, Pierre Morel, Caroline Dartigeas, Julie Lejeune, John F. Seymour, Olivier Tournilhac, Bruno Royer, Marion Malphette, Véronique Leblond, S. A. Johnson, Sylvie Chevret, Roger G. Owen
Publikováno v:
Blood. 118:776-776
Abstract 776 Background: Waldenstrom's macroglobulinemia (WM) and related-disorders (Marginal Zone Lymphoma: MZL, and non immunoglobulin IgM lymphoplasmacytic lymphoma: LPL) are rare diseases Very few randomized trials were reported in this setting.