Zobrazeno 1 - 10
of 39
pro vyhledávání: '"Marcelo A, Barria"'
Autor:
Jennifer Myskiw, Ben A. Bailey-Elkin, Kristen Avery, Marcelo A. Barria, Diane L. Ritchie, Mark L. Cohen, Brian S. Appleby, Stephanie A Booth
Publikováno v:
Scientific Reports, Vol 14, Iss 1, Pp 1-14 (2024)
Abstract Variably Protease Sensitive Prionopathy (VPSPr) is a rare human prion disease that, like Creutzfeldt-Jakob disease (CJD), results in the deposition of abnormally folded prion protein aggregates in the brain and is ultimately fatal. Neuropath
Externí odkaz:
https://doaj.org/article/64256f7c1612469ea8d0f61d71c293de
Autor:
Jean-Yves Douet, Alvina Huor, Hervé Cassard, Séverine Lugan, Naïma Aron, Chloé Mesic, Didier Vilette, Tomás Barrio, Nathalie Streichenberger, Armand Perret-Liaudet, Marie-Bernadette Delisle, Patrice Péran, Jean-Philippe Deslys, Emmanuel Comoy, Jean-Luc Vilotte, Katayoun Goudarzi, Vincent Béringue, Marcelo A. Barria, Diane L. Ritchie, James W. Ironside, Olivier Andréoletti
Publikováno v:
Acta Neuropathologica Communications, Vol 9, Iss 1, Pp 1-15 (2021)
Abstract Treatment with human pituitary-derived growth hormone (hGH) was responsible for a significant proportion of iatrogenic Creutzfeldt–Jakob disease (iCJD) cases. France and the UK experienced the largest case numbers of hGH-iCJD, with 122 and
Externí odkaz:
https://doaj.org/article/38331de11f744c59b42002fabad71f84
Publikováno v:
Frontiers in Aging Neuroscience, Vol 13 (2021)
Prion diseases are fatal neurodegenerative disorders that affect humans and animals, and can also be transmitted from animals to humans. A fundamental event in prion disease pathogenesis is the conversion of normal host prion protein (PrPC) to a dise
Externí odkaz:
https://doaj.org/article/60f9455d840646e99e671e8b05351369
Publikováno v:
Emerging Infectious Diseases, Vol 24, Iss 8, Pp 1482-1489 (2018)
Chronic wasting disease (CWD) is a contagious and fatal neurodegenerative disease and a serious animal health issue for deer and elk in North America. The identification of the first cases of CWD among free-ranging reindeer and moose in Europe brings
Externí odkaz:
https://doaj.org/article/f9d49d0b28bf4454bd6429fc2f9b2a52
Publikováno v:
BMC Neurology, Vol 18, Iss 1, Pp 1-7 (2018)
Abstract Background Frontotemporal dementia (FTD) and Amyotrophic Lateral Sclerosis (ALS) are incurable, progressive and fatal neurodegenerative diseases with patients variably affected clinically by motor, behavior, and cognitive deficits. The accum
Externí odkaz:
https://doaj.org/article/3ea842e4e45544a88f110bc271efc8aa
Publikováno v:
Pathogens, Vol 10, Iss 11, p 1413 (2021)
Twenty-five years has now passed since variant Creutzfeldt-Jakob disease (vCJD) was first described in the United Kingdom (UK). Early epidemiological, neuropathological and biochemical investigations suggested that vCJD represented a new zoonotic for
Externí odkaz:
https://doaj.org/article/2fc169e9f4ed4a74b10d93de7ee127ec
Publikováno v:
PLoS ONE, Vol 14, Iss 6, p e0218509 (2019)
Sporadic Creutzfeldt-Jakob disease (sCJD) is a transmissible, rapidly progressive and fatal neurodegenerative disease. The transmissible agent linked to sCJD is composed of the misfolded form of the host-encoded prion protein. The combination of hist
Externí odkaz:
https://doaj.org/article/d4a2ee5eb46949bdabb0f1f580d9693b
Autor:
Diane L. Ritchie, Marcelo A. Barria
Publikováno v:
Biomolecules, Vol 11, Iss 2, p 207 (2021)
The accumulation and propagation in the brain of misfolded proteins is a pathological hallmark shared by many neurodegenerative diseases such as Alzheimer’s disease (Aβ and tau), Parkinson’s disease (α-synuclein), and prion disease (prion prote
Externí odkaz:
https://doaj.org/article/a0362d91ed73419ba56523331044e98b
Autor:
Alexander H. Peden, Marcelo A. Barria
Publikováno v:
Prions and Diseases ISBN: 9783031205644
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_________::d60cbca9143869785feffa448315978d
https://doi.org/10.1007/978-3-031-20565-1_12
https://doi.org/10.1007/978-3-031-20565-1_12
Autor:
Marcelo A. Barria, Aru Balachandran, Masanori Morita, Tetsuyuki Kitamoto, Rona Barron, Jean Manson, Richard Knight, James W. Ironside, Mark W. Head
Publikováno v:
Emerging Infectious Diseases, Vol 20, Iss 1, Pp 88-97 (2014)
The risks posed to human health by individual animal prion diseases cannot be determined a priori and are difficult to address empirically. The fundamental event in prion disease pathogenesis is thought to be the seeded conversion of normal prion pro
Externí odkaz:
https://doaj.org/article/1b6cc059690f4c69918ffde6ba9c2414