Zobrazeno 1 - 10
of 15
pro vyhledávání: '"Máté, Krausz"'
Autor:
Ole Kristian Greiner-Tollersrud, Máté Krausz, Vincent Boehler, Aikaterini Polyzou, Maximilian Seidl, Ambra Spahiu, Zeinab Abdullah, Katarzyna Andryka-Cegielski, Felix Immunuel Dominick, Katrin Huebscher, Andreas Goschin, Cristian R. Smulski, Eirini Trompouki, Regina Link, Hilmar Ebersbach, Honnappa Srinivas, Martine Marchant, Georgios Sogkas, Dieter Staab, Cathrine Vågbø, Danilo Guerini, Sebastian Baasch, Eicke Latz, Gunther Hartmann, Philippe Henneke, Roger Geiger, Xiao P. Peng, Bodo Grimbacher, Eva Bartok, Ingrun Alseth, Max Warncke, Michele Proietti
Publikováno v:
Cell Reports, Vol 43, Iss 11, Pp 114899- (2024)
Summary: Although adenosine deaminase 2 (ADA2) is considered an extracellular ADA, evidence questions the physiological relevance of this activity. Our study reveals that ADA2 localizes within the lysosomes, where it is targeted through modifications
Externí odkaz:
https://doaj.org/article/f6e14d70f0b648c3aca83261512b83d8
Autor:
Máté Krausz, Noriko Mitsuiki, Valeria Falcone, Johanna Komp, Sara Posadas-Cantera, Hanns-Martin Lorenz, Jiri Litzman, Daniel Wolff, Maria Kanariou, Anita Heinkele, Carsten Speckmann, Georg Häcker, Hartmut Hengel, Laura Gámez-Díaz, Bodo Grimbacher
Publikováno v:
Frontiers in Immunology, Vol 14 (2023)
Externí odkaz:
https://doaj.org/article/4811e267db8b4a0f951d41d027cdeb75
Autor:
Máté Krausz, Annette Uhlmann, Ina Caroline Rump, Gabriele Ihorst, Sigune Goldacker, Georgios Sogkas, Sara Posadas-Cantera, Reinhold Schmidt, Manuel Feißt, Laia Alsina, Ingunn Dybedal, Mike Recher, Klaus Warnatz, Bodo Grimbacher
Publikováno v:
Contemporary Clinical Trials Communications, Vol 30, Iss , Pp 101008- (2022)
Background: Cytotoxic T-lymphocyte-associated protein 4 (CTLA-4) insufficiency and lipopolysaccharide-responsive and beige-like anchor protein (LRBA) deficiency are both complex immune dysregulation syndromes with an underlying regulatory T cell dysf
Externí odkaz:
https://doaj.org/article/5c6b30705b4d40c9b81827a7ec4b87dd
Autor:
Máté Krausz, Noriko Mitsuiki, Valeria Falcone, Johanna Komp, Sara Posadas-Cantera, Hanns-Martin Lorenz, Jiri Litzman, Daniel Wolff, Maria Kanariou, Anita Heinkele, Carsten Speckmann, Georg Häcker, Hartmut Hengel, Laura Gámez-Díaz, Bodo Grimbacher
Publikováno v:
Frontiers in Immunology, Vol 13 (2022)
PurposeHeterozygous mutations in CTLA4 lead to an inborn error of immunity characterized by immune dysregulation and immunodeficiency, known as CTLA-4 insufficiency. Cohort studies on CTLA4 mutation carriers showed a reduced penetrance (around 70%) a
Externí odkaz:
https://doaj.org/article/64f0ae1228b94a4eaeab35fff84eeb9a
Autor:
Eileen Haring, Geoffroy Andrieux, Franziska M. Uhl, Máté Krausz, Michele Proietti, Barbara Sauer, Philipp R. Esser, Stefan F. Martin, Dietmar Pfeifer, Annette Schmitt-Graeff, Justus Duyster, Natalie Köhler, Bodo Grimbacher, Melanie Boerries, Konrad Aumann, Robert Zeiser, Petya Apostolova
Publikováno v:
Haematologica, Vol 107, Iss 7 (2021)
Acute graft-versus-host disease (GvHD) is a life-threatening complication of allogeneic hematopoietic cell transplantation (allo-HCT), a potentially curative treatment for leukemia. Endoplasmic reticulum (ER) stress occurs when the protein folding ca
Externí odkaz:
https://doaj.org/article/3798a575b63446ca8e0e75508ae07a3d
Autor:
Yoong Wearn Lim, Neftali Jose Ramirez, Michael A. Asensio, Yao Chiang, Gabriele Müller, Pavla Mrovecova, Noriko Mitsuiki, Máté Krausz, Nadezhda Camacho-Ordonez, Klaus Warnatz, Adam S. Adler, Bodo Grimbacher
Publikováno v:
Journal of Clinical Immunology.
Purpose Most individuals with antibody deficiency (hypogammaglobulinemia) need immunoglobulin replacement therapy (IgG-RT) from healthy plasma donors to stay clear of infections. However, a small subset of hypogammaglobulinemic patients do not requir
Autor:
Markus Zeisbrich, Viktoria Schindler, Máté Krausz, Michele Proietti, Pavla Mrovecova, Reinhard E. Voll, Cornelia Glaser, Fabian Röther, Klaus Warnatz, Nils Venhoff
Publikováno v:
Zeitschrift für Rheumatologie.
ZusammenfassungDas VEXAS-Syndrom (Akronym für Vacuoles, E1 enzyme, X‑linked, Autoinflammatory, Somatic) wurde Ende 2020 erstmals beschrieben und verursacht durch eine erworbene Mutation auf dem X‑Chromosom ein autoinflammatorisches Syndrom vorwi
Autor:
Paulina Staus, Stephan Rusch, Sabine El-Helou, Gabriele Müller, Máté Krausz, Ulf Geisen, Andrés Caballero-Oteyza, Renate Krüger, Shahrzad Bakhtiar, Min Ae Lee-Kirsch, Maria Fasshauer, Ulrich Baumann, Bimba Franziska Hoyer, João Farela Neves, Michael Borte, Maria Carrabba, Fabian Hauck, Stephan Ehl, Peter Bader, Horst von Bernuth, Faranaz Atschekzei, Mikko R. J. Seppänen, Klaus Warnatz, Alexandra Nieters, Gerhard Kindle, Bodo Grimbacher
Funding Information: The documentation specialist S.E-H. was funded by the Federal Ministry of Education and Research (BMBF, Support Code: 01GM1517C), by the European Society for Immunodeficiencies (ESID), 2018, by the Care-for-Rare Foundation, by PR
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::23e214c1af43f2e99ff7514cb950f136
https://hdl.handle.net/10362/152437
https://hdl.handle.net/10362/152437
Autor:
Máté Krausz, Justus Duyster, Bodo Grimbacher, Geoffroy Andrieux, Robert Zeiser, Stefan F. Martin, Franziska M. Uhl, Dietmar Pfeifer, Barbara Sauer, Natalie Köhler, Eileen Haring, Konrad Aumann, Annette Schmitt-Graeff, Petya Apostolova, Philipp R. Esser, Melanie Boerries, Michele Proietti
Publikováno v:
Haematologica. 107:1538-1554
Acute graft-versus-host disease (GvHD) is a life-threatening complication of allogeneic hematopoietic cell transplantation (allo-HCT), a potentially curative treatment for leukemia. Endoplasmic reticulum (ER) stress occurs when the protein folding ca
Autor:
Eugenia Alas, Boglarka Ujhazi, David Potts, Máté Krausz, Pia Hassunah, Priya Patel, Monica Hajirawala, Krisztian Csomos, Bodo Grimbacher, Jolan Walter
Publikováno v:
Clinical Immunology. 250:109548