Zobrazeno 1 - 10
of 93
pro vyhledávání: '"Luiz Vicente Ribeiro Ferreira da Silva Filho"'
Autor:
Silvia Onoda Tomikawa, Joaquim Carlos Rodrigues, Cleyde Miryam Aversa Nakaie, Luiz Vicente Ribeiro Ferreira da Silva Filho
Publikováno v:
Jornal Brasileiro de Pneumologia, Vol 50, Iss 2 (2024)
Externí odkaz:
https://doaj.org/article/dfd0a7c7ce344ee6bef0bc5bbe010586
Autor:
Luiz Vicente Ribeiro Ferreira da Silva Filho, Rodrigo Abensur Athanazio, Carolina Rodrigues Tonon, Juliana Carvalho Ferreira, Suzana Erico Tanni
Publikováno v:
Jornal Brasileiro de Pneumologia, Vol 49, Iss 6 (2024)
ABSTRACT Objective: To evaluate the effect of treatment with the combination of three cystic fibrosis transmembrane conductance regulator (CFTR) modulators-elexacaftor+tezacaftor+ivacaftor (ETI)-on important clinical endpoints in individuals with cys
Externí odkaz:
https://doaj.org/article/736000b308c24661bbbd610cf685667d
Autor:
Rodrigo Abensur Athanazio, Suzana Erico Tanni, Juliana Ferreira, Paulo de Tarso Roth Dalcin, Marcelo B de Fuccio, Concetta Esposito, Mariane Gonçalves Martynychen Canan, Liana Sousa Coelho, Mônica de Cássia Firmida, Marina Buarque de Almeida, Paulo José Cauduro Marostica, Luciana de Freitas Velloso Monte, Edna Lúcia Souza, Leonardo Araujo Pinto, Samia Zahi Rached, Verônica Stasiak Bednarczuk de Oliveira, Carlos Antonio Riedi, Luiz Vicente Ribeiro Ferreira da Silva Filho
Publikováno v:
Jornal Brasileiro de Pneumologia, Vol 49, Iss 2 (2023)
ABSTRACT Cystic fibrosis (CF) is a genetic disease that results in dysfunction of the CF transmembrane conductance regulator (CFTR) protein, which is a chloride and bicarbonate channel expressed in the apical portion of epithelial cells of various or
Externí odkaz:
https://doaj.org/article/2ee12dd8b3bd413899822534cd8fd4b1
Autor:
Fernanda Martins Dias Escaldelai, Luiz Vicente Ribeiro Ferreira da Silva Filho, Lenycia de Cassya Lopes Neri, Denise Pimentel Bergamaschi
Publikováno v:
Revista Paulista de Pediatria, Vol 41 (2023)
Abstract Objective: This study aimed to identify methodological aspects involved in determining anthropometric measurements among studies assessing the nutritional status of individuals with cystic fibrosis (CF). Methods: A search of the literature w
Externí odkaz:
https://doaj.org/article/a97058512ae948ac835a44085081dc77
Autor:
Fábio Pereira Muchão, Andréa Vieira de Souza, Juliana Miguita e Souza, Luiz Vicente Ribeiro Ferreira da Silva Filho
Publikováno v:
Einstein (São Paulo), Vol 20 (2022)
ABSTRACT Objective To investigate whether different genotypes of p.Arg16Gly, p.Gln27Glu, p.Arg19Cys and p.Thr164Ile variants interfere in response to treatment in children and adolescents with moderate to severe acute asthma. Methods This sample comp
Externí odkaz:
https://doaj.org/article/f09d0def5133437dbcea2998dee863d1
Autor:
Barbara Riquena, Luiz Vicente Ribeiro Ferreira da Silva Filho, Cleyde Myriam Aversa Nakaie, Marina Buarque de Almeida, Joaquim Carlos Rodrigues, Fabíola Villac Adde
Publikováno v:
Jornal Brasileiro de Pneumologia, Vol 46, Iss 4 (2020)
ABSTRACT Objective: Although various strategies have been proposed for eradicating Pseudomonas aeruginosa in patients with cystic fibrosis (CF), only a few employ multistep treatment in children colonized by that pathogen for the first time. The aim
Externí odkaz:
https://doaj.org/article/d8ad652967cd4f9d90e564892db2e6b9
Autor:
Lander Bosch, Barbara Bosch, Kris De Boeck, Tim Nawrot, Isabelle Meyts, Dominique Vanneste, Cleonice Alexandre Le Bourlegat, Julio Croda, Luiz Vicente Ribeiro Ferreira da Silva Filho
Publikováno v:
BMC Infectious Diseases, Vol 17, Iss 1, Pp 1-8 (2017)
Abstract Background The reason why Cystic Fibrosis (CF) is the most common fatal genetic disease among Caucasians has been incompletely studied. We aimed at deepening the hypothesis that CF carriers have a relative protection against Mycobacterium tu
Externí odkaz:
https://doaj.org/article/cc12e51c81934f9f84b7698c5f44d545
Autor:
Lenycia de Cassya Lopes Neri, Denise Pimentel Bergamaschi, Luiz Vicente Ribeiro Ferreira da Silva Filho
Publikováno v:
Revista Paulista de Pediatria, Iss 0 (2018)
RESUMO Objetivo: Avaliar o perfil nutricional da população atendida em centro de referência em fibrose cística. Métodos: Estudo transversal incluindo pacientes com fibrose cística de um centro pediátrico de referência de São Paulo, em 2014.
Externí odkaz:
https://doaj.org/article/e4788707c04e4161a888e310ca5673eb
Autor:
Adriana Della Zuana, Doroti de Oliveira Garcia, Regina Célia Turola Passos Juliani, Luiz Vicente Ribeiro Ferreira da Silva Filho
Publikováno v:
Jornal Brasileiro de Pneumologia, Vol 40, Iss 2, Pp 119-127 (2014)
OBJECTIVE: To describe the pathogens found in home nebulizers and in respiratory samples of cystic fibrosis (CF) patients, and to evaluate the effect that a standardized instruction regarding cleaning and disinfection of nebulizers has on the frequen
Externí odkaz:
https://doaj.org/article/1e69745f6e9e40d9b52ad7eff93d2e0b
Autor:
Luiz Vicente Ribeiro Ferreira da Silva Filho, Flavia de Aguiar Ferreira, Francisco Jose Caldeira Reis, Murilo Carlos Amorim de Britto, Carlos Emilio Levy, Otavio Clark, Jose Dirceu Ribeiro
Publikováno v:
Jornal Brasileiro de Pneumologia, Vol 39, Iss 4, Pp 495-512 (2013)
Evidence-based techniques have been increasingly used in the creation of clinical guidelines and the development of recommendations for medical practice. The use of levels of evidence allows the reader to identify the quality of scientific informatio
Externí odkaz:
https://doaj.org/article/74d7690595aa4306aebfc6bca7376c8e