Zobrazeno 1 - 8
of 8
pro vyhledávání: '"Liliana S, Mendonça"'
Autor:
Liliana S. Mendonça, Daniel Henriques, Vanessa Fernandes, Ricardo Moreira, João Brás, Sónia Duarte, Jens C. Schwamborn, Luís Pereira de Almeida
Publikováno v:
Scientific Reports, Vol 14, Iss 1, Pp 1-20 (2024)
Abstract Machado-Joseph disease (MJD) is a neurodegenerative disorder characterized by widespread neuronal death affecting the cerebellum. Cell therapy can trigger neuronal replacement and neuroprotection through bystander effects providing a therape
Externí odkaz:
https://doaj.org/article/eebb23be8ea44faba711dd7c8d7931da
Autor:
João Brás, Daniel Henriques, Ricardo Moreira, Magda M. Santana, Rita Silva-Pedrosa, Diana Adão, Sandra Braz, Ana Rita Álvaro, Luís Pereira de Almeida, Liliana S. Mendonça
Publikováno v:
Scientific Reports, Vol 12, Iss 1, Pp 1-15 (2022)
Abstract The establishment of robust human brain organoids to model cerebellar diseases is essential to study new therapeutic strategies for cerebellum-associated disorders. Machado-Joseph disease (MJD) is a cerebellar hereditary neurodegenerative di
Externí odkaz:
https://doaj.org/article/123767972da844c2aee9d5a361e465c6
Autor:
David Rufino-Ramos, Patrícia R. Albuquerque, Kevin Leandro, Vitor Carmona, Inês M. Martins, Rita Fernandes, Carina Henriques, Diana Lobo, Rosário Faro, Rita Perfeito, Liliana S. Mendonça, Dina Pereira, Célia M. Gomes, Rui Jorge Nobre, Luís Pereira de Almeida
Publikováno v:
Molecular Therapy. 31:1275-1292
Autor:
Daniel Henriques, Ricardo Moreira, Jens Schwamborn, Luís Pereira de Almeida, Liliana S. Mendonça
Publikováno v:
Frontiers in Neuroscience, Vol 13 (2019)
Brain regenerative strategies through the transplantation of stem cells hold the potential to promote functional rescue of brain lesions caused either by trauma or neurodegenerative diseases. Most of the positive modulations fostered by stem cells ar
Externí odkaz:
https://doaj.org/article/d8ce19e71e5e4e608b8fad612ed17383
Publikováno v:
International Journal of Molecular Sciences, Vol 22, Iss 22, p 12288 (2021)
Recent research demonstrated pathological spreading of the disease-causing proteins from one focal point across other brain regions for some neurodegenerative diseases, such as Parkinson’s and Alzheimer’s disease. Spreading mediated by extracellu
Externí odkaz:
https://doaj.org/article/a9746ba5c6a24757a36db0ba0819bcde
Autor:
Maria Francisca Coutinho, Juliana Inês Santos, Liliana S. Mendonça, Liliana Matos, Maria João Prata, Amália S. Jurado, Maria C. Pedroso de Lima, Sandra Alves
Publikováno v:
International Journal of Molecular Sciences, Vol 21, Iss 16, p 5732 (2020)
More than two thirds of Lysosomal Storage Diseases (LSDs) present central nervous system involvement. Nevertheless, only one of the currently approved therapies has an impact on neuropathology. Therefore, alternative approaches are under development,
Externí odkaz:
https://doaj.org/article/db790f417c684e1ab5487cc98d9a6322
Autor:
Pedro M Costa, Ana L Cardoso, Liliana S Mendonça, Angelo Serani, Carlos Custódia, Mariana Conceição, Sérgio Simões, João N Moreira, Luís Pereira de Almeida, Maria C Pedroso de Lima
Publikováno v:
Molecular Therapy: Nucleic Acids, Vol 2, Iss C (2013)
The present work aimed at the development and application of a lipid-based nanocarrier for targeted delivery of nucleic acids to glioblastoma (GBM). For this purpose, chlorotoxin (CTX), a peptide reported to bind selectively to glioma cells while sho
Externí odkaz:
https://doaj.org/article/66ac7cd847d140d19c87aab6c7cc7aeb
Autor:
Liliana S, Mendonça, Isabel, Onofre, Catarina Oliveira, Miranda, Rita, Perfeito, Clévio, Nóbrega, Luís Pereira, de Almeida
Publikováno v:
Advances in experimental medicine and biology. 1049
Polyglutamine (polyQ) diseases are a family of neurodegenerative disorders with very heterogeneous clinical presentations, although with common features such as progressive neuronal death. Thus, at the time of diagnosis patients might present an exte