Zobrazeno 1 - 10
of 62
pro vyhledávání: '"Leonhard S. Wolfe"'
Publikováno v:
Journal of Neurochemistry. 64:733-741
Subunit c is normally present as an inner mitochondrial membrane component of the F0 section of the ATP synthase complex, but in the late infantile form of neuronal ceroid lipofuscinosis (NCL) it was also found in lysosomes in high concentrations. To
Publikováno v:
Neurochemical Research. 20:1305-1309
Subunit c is normally present as an inner mitochondrial membrane component of the Fo sector of the ATP synthase complex, but in the late infantile form of neuronal ceroid lipofuscinosis (NCL) it was also found in lysosomes in high concentrations. Mec
Autor:
Robert D. Jolly, Nicholas A. Hall, Ian M. Fearnley, Ryan Dennis Martinus, David Palmer, Matti Haltia, Brian D. Lake, John E. Walker, Leonhard S. Wolfe
Publikováno v:
American Journal of Medical Genetics. 42:561-567
The ceroid-lipofuscinoses (Batten disease) are neurodegenerative inherited lysosomal storage diseases of children and animals. A common finding is the occurrence of fluorescent storage bodies (lipopigment) in cells. These have been isolated from tiss
Autor:
Leonhard S. Wolfe, Luc Pellerin
Publikováno v:
Neurochemical Research. 16:983-989
In hippocampal slices arachidonic acid released after NMDA post-synaptic receptor activation is thought to act as a retrograde trans-synaptic messenger which facilitates the pre-synaptic release of L-glutamate to be involved in the expression of long
Publikováno v:
Journal of Inherited Metabolic Disease. 16:296-298
Autor:
Leonhard S. Wolfe
Publikováno v:
Journal of Neurochemistry. 47:1002-1003
Publikováno v:
Journal of neurochemistry. 67(4)
Previously we indicated that a specific delay in subunit c degradation causes the accumulation of mitochondrial ATP synthase subunit c in lysosomes from the cells of patients with the late infantile form of neuronal ceroid lipofuscinosis (NCL). To ex
Publikováno v:
American journal of medical genetics. 57(2)
Subunit c is normally present as an inner mitochondrial membrane component of the F0 sector of the ATP synthase complex, but in the late infantile form of neuronal ceroid-lipofuscinosis (NCL) it was also found in lysosomes in high concentrations. The
Publikováno v:
Gerontology. 41
Mechanism of lysosomal storage of mitochondrial ATP synthase subunit c in late infantile form of NCL was studied. Morphological and biochemical examinations with patient fibroblasts showed that subunit c, not other mitochondrial proteins was specific
Publikováno v:
Neuroscience letters. 115(2-3)
The effects induced by arachidonic acid upon excitatory synaptic transmission were investigated in the CA1 subfield of rat hippocampal slices. Perfusion with medium containing 50 μM of arachidonic acid induced in 12 of 19 experiments a long-lasting