Zobrazeno 1 - 10
of 22
pro vyhledávání: '"Juvenal Paiva"'
Autor:
Célia Dos Santos, Juvenal Paiva, María Lucila Romero, Mara Agazzoni, Ana Catalina Kempfer, Sabrina Rotondo, María Marta Casinelli, María Fabiana Alberto, Analía Sánchez‐Luceros
Publikováno v:
eJHaem, Vol 2, Iss 2, Pp 149-156 (2021)
Abstract Introduction Introduction: Thrombotic microangiopathies (TMAs) are rare disorders associated with fatal outcomes if left uncared for. However, healthcare problems in developing countries tend to limit medical assistance to patients. Methods
Externí odkaz:
https://doaj.org/article/5c89136facd644a0964cd9b1a60d206b
Autor:
Marina Sol Lopez, Juvenal Paiva, Adriana Woods, María Soledad Saez, Luis Horacio Barrera, Verónica Privitera, Fernando Chuliber, Maximiliano Villagra Iturre, Diana Penchasky, Patricia Sorroche, Marta Martinuzzo, Analia Sánchez Luceros
Publikováno v:
Revista Hematología. 26:9-19
La enfermedad de von Willebrand (VWD) es el desorden hemorrágico congénito más frecuente y se produce por la deficiencia y/o alteración del factor von Willebrand (VWF). El VWF es una glicoproteí-na multimérica que se sintetiza en las células e
Autor:
Adriana Inés Woods, Juvenal Paiva, Celia Dos Santos, María Fabiana Alberto, Analía Sánchez-Luceros
Publikováno v:
Seminars in thrombosis and hemostasis.
ADAMTS13 (a disintegrin-like metalloprotease domain with thrombospondin type 1 motif, member 13) is a protease of crucial importance in the regulation of the size of von Willebrand factor multimers. Very low ADAMTS13 activity levels result in thrombo
Von Willebrand disease type 2M: Correlation between genotype and phenotype: Comment from Woods et al
Autor:
Adriana I. Woods, Juvenal Paiva, Debora M. Primrose, Alicia N. Blanco, Analia Sanchez‐Luceros
Publikováno v:
Journal of Thrombosis and Haemostasis. 20:1022-1023
Autor:
Débora Marina Primrose, Adriana I. Woods, Alicia N. Blanco, Analía Sánchez-Luceros, Juvenal Paiva
Publikováno v:
Seminars in thrombosis and hemostasis. 47(7)
Type 2A and 2M von Willebrand disease (VWD) broadly show similar phenotypic parameters, but involve different pathophysiological mechanisms. This report presents the clinical and laboratory profiles of type 2A and type 2M patients genotypically diagn
Autor:
Juvenal Paiva, María Marta Casinelli, Célia Dos Santos, Ana Catalina Kempfer, Sabrina Rotondo, Maria Fabiana Alberto, Analía Sánchez-Luceros, María Lucila Romero, Mara Agazzoni
Publikováno v:
CONICET Digital (CONICET)
Consejo Nacional de Investigaciones Científicas y Técnicas
instacron:CONICET
Consejo Nacional de Investigaciones Científicas y Técnicas
instacron:CONICET
Introduction: Thrombotic microangiopathies (TMAs) are rare disorders associated with fatal outcomes if left uncared for. However, healthcare problems in developing countries tend to limit medical assistance to patients. Methods: We prospectively stud
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::ae4e85861591f09f28de03ad7a870260
Wiley Online Library
Wiley Online Library
Autor:
Adriana Ines Woods, Liliana Carmen Rossetti, Carlos Daniel de Brasi, María Marta Casinelli, Alicia N. Blanco, Juvenal Paiva, María Lucila Romero, Analía Sánchez-Luceros
Publikováno v:
Thrombosis research. 198
Autor:
Ana Catalina Kempfer, Adriana I. Woods, Maria A. Lazzari, Alicia N. Blanco, Juvenal Paiva, Analía Sánchez-Luceros, Débora Marina Primrose
Publikováno v:
Research and Practice in Thrombosis and Haemostasis
CONICET Digital (CONICET)
Consejo Nacional de Investigaciones Científicas y Técnicas
instacron:CONICET
CONICET Digital (CONICET)
Consejo Nacional de Investigaciones Científicas y Técnicas
instacron:CONICET
Background: Type 2M von Willebrand disease (VWD2M) is usually characterized byVWF:RCo/VWF:Ag