Zobrazeno 1 - 10
of 10
pro vyhledávání: '"Joseph Gawron"'
Publikováno v:
PLoS ONE, Vol 19, Iss 12, p e0314858 (2024)
Krabbe disease (Kd) is a lysosomal storage disorder (LSD) caused by the deficiency of the lysosomal galactosylceramidase (GALC) which cleaves the myelin enriched lipid galactosylceramide (GalCer). Accumulated GalCer is catabolized into the cytotoxic
Externí odkaz:
https://doaj.org/article/117e48c4e3144f3a95391d6e05adedf1
Autor:
Lawrence Wrabetz, Nicholas Silvestri, Jordan J. S. VerPlank, Alfred L. Goldberg, Joseph Gawron, M. Laura Feltri
Publikováno v:
Brain
Agents that raise cyclic guanosine monophosphate (cGMP) by activating protein kinase G increase 26S proteasome activities, protein ubiquitination and degradation of misfolded proteins. Therefore, they may be useful in treating neurodegenerative and o
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::b6216593573507658a8be0fca0a74f11
https://doi.org/10.1093/brain/awab249
https://doi.org/10.1093/brain/awab249
Autor:
Evans, Lisa Marie P.1 (AUTHOR), Gawron, Joseph1 (AUTHOR), Sim, Fraser J.2 (AUTHOR), Feltri, M. Laura1,3 (AUTHOR), Marziali, Leandro N.1 (AUTHOR) leandrom@buffalo.edu
Publikováno v:
PLoS ONE. 12/5/2024, Vol. 19 Issue 12, p1-19. 19p.
Publikováno v:
Journal of the Peripheral Nervous System. Oct2023 Supplement 1, Vol. 28, pS3-S254. 252p.
Publikováno v:
Journal of the Peripheral Nervous System. Jul2022 Supplement S1, Vol. 27, pS4-S183. 180p.
Autor:
VerPlank, Jordan J S, Gawron, Joseph, Silvestri, Nicholas J, Feltri, M Laura, Wrabetz, Lawrence, Goldberg, Alfred L
Publikováno v:
Brain: A Journal of Neurology; Jan2022, Vol. 145 Issue 1, p168-178, 11p
Autor:
VerPlank, Jordan J. S., Lokireddy, Sudarsanareddy, Feltri, M. Laura, Goldberg, Alfred L., Wrabetz, Lawrence
Publikováno v:
Glia; Feb2018, Vol. 66 Issue 2, p379-395, 17p
Publikováno v:
Buffalo Law Journal. 2/19/2007, Vol. 79 Issue 15, p20-30. 11p.
Autor:
Gawron, Joseph
Publikováno v:
Transmission & Distribution World. Apr2001, Vol. 53 Issue 4, p87. 3p. 4 Color Photographs.