Zobrazeno 1 - 10
of 22
pro vyhledávání: '"Jordana E. Hoppe"'
Autor:
Annemarie G. Wolfe, Stephanie P. Gilley, Stephanie W. Waldrop, Christina Olson, Emma Harding, Kaitlin Widmer, Lindsey B. Gumer, Matthew Haemer, Jordana E. Hoppe
Publikováno v:
Frontiers in Pediatrics, Vol 10 (2023)
BackgroundUniversal newborn screening changed the way medical providers think about the presentation of cystic fibrosis (CF). Before implementation of universal screening, it was common for children with CF to present with failure to thrive, nutritio
Externí odkaz:
https://doaj.org/article/13a597ec996e4b08bb09b115b3fcd9ff
Publikováno v:
BMC Pulmonary Medicine, Vol 17, Iss 1, Pp 1-8 (2017)
Abstract Background Pulmonary exacerbations (PEx) in school aged children and adults with cystic fibrosis (CF) lead to increased morbidity and lung function decline. However, the effect of exacerbations in young children with CF is not fully understo
Externí odkaz:
https://doaj.org/article/aa29735116fe4a2fbbe4f669e74ee1ab
Publikováno v:
Expert Review of Respiratory Medicine. 17:97-108
Autor:
Scott D. Sagel, Oren Kupfer, Brandie D. Wagner, Stephanie D. Davis, Sharon D. Dell, Thomas W. Ferkol, Jordana E. Hoppe, Margaret Rosenfeld, Kelli M. Sullivan, Harm A. W. M. Tiddens, Michael R. Knowles, Margaret W. Leigh
Publikováno v:
Annals of the American Thoracic Society. 20:67-74
Publikováno v:
American Journal of Respiratory and Critical Care Medicine. 206:1308-1310
Autor:
Mark A. Chilvers, Jordana E. Hoppe, Caroline A. Owen, Alexandra G Cornell, Rachel Zahigian, Susanna A McColley, John McNamara, S. Tian, Felix Ratjen
Publikováno v:
The Lancet Respiratory Medicine. 9:977-988
Summary Background A previous phase 3 study showed that lumacaftor–ivacaftor was generally safe and well tolerated over 24 weeks of treatment in children aged 2–5 years with cystic fibrosis homozygous for the F508del-CFTR mutation. In this study,
Autor:
Stacey L. Martiniano, Charles R. Esther, Jordana E. Hoppe, Chelsea S Davis, Marianne S. Muhlebach, Elisabeth P. Dellon, Jennifer S. Guimbellot, Demet Toprak, Cori L. Daines
Publikováno v:
Pediatric Pulmonology. 55:2225-2232
This review briefly summarizes presentations in several major topic areas at the conference: pathophysiology and basic science of cystic fibrosis lung disease, clinical trials, clinical quality improvement, microbiology and treatment of infection, an
Autor:
Jordana E. Hoppe, Brandie D. Wagner, J. Kirk Harris, Steven M. Rowe, Sonya L Heltshe, Emily M. DeBoer, Scott D. Sagel
Publikováno v:
Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society. 21(6)
Ivacaftor is a cystic fibrosis transmembrane conductance regulator (CFTR) potentiator for people with CF and the G551D mutation. We aimed to investigate the biology of CFTR modulation and systemic effects of CFTR restoration by examining changes in c
Autor:
Sabina Sariyska, Stacey L. Martiniano, Patricia M Lenhart-Pendergrass, M. Anthony, Ashley Andrews, Heather Scavezze, Elinor Towler, Jordana E. Hoppe, Edith T. Zemanick
Publikováno v:
Pediatric pulmonologyREFERENCES. 56(7)
BACKGROUND: Collection of respiratory cultures for airway microbiology surveillance is an essential component of routine clinical care in cystic fibrosis (CF). The COVID-19 global pandemic has necessitated increased use of telehealth, but one limitat
Publikováno v:
Journal of Cystic Fibrosis
Background Pulmonary exacerbations (PEx) in children with cystic fibrosis (CF) are frequently treated in the outpatient setting with oral antibiotics. However, little is known about the characteristics of PEx managed on an outpatient basis and the ef