Zobrazeno 1 - 10
of 79
pro vyhledávání: '"Jiri Palek"'
Autor:
Michael R. Cho, Scott J. Yi, Shih-Chun Liu, David E. Golan, Yva Smockova, Manjit Hanspal, Jiri Palek
Publikováno v:
Blood. 92:329-338
Band 3, the anion transport protein of the erythrocyte membrane, exists in the membrane as a mixture of dimers (B3D) and tetramers (B3T). The dimers are not linked to the skeleton and constitute the free mobile band 3 fraction. The tetramers are link
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_________::c2fcc6bba61c20093d88e21fa5314ce6
https://doi.org/10.1182/blood.v92.1.329.413k20_329_338
https://doi.org/10.1182/blood.v92.1.329.413k20_329_338
Publikováno v:
Transfusion. 37:1179-1183
BACKGROUND: Hereditary spherocytosis (HS) is characterized by osmotically fragile spherocytic red cells (RBCs), mild to moderate hemolysis, and splenomegaly. Little is known about the safety of blood bank storage of HS RBCs. CASE REPORT: A 50-year-ol
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::aa3cdf78c3b01627dafbf2236bae273d
https://doi.org/10.1046/j.1537-2995.1997.37111298088049.x
https://doi.org/10.1046/j.1537-2995.1997.37111298088049.x
Autor:
J E Barker, Laura H. Derick, Scott J. Yi, David E. Golan, James Murray, Jiri Palek, M R Cho, Shih-Chun Liu
Publikováno v:
Biochemistry. 36:9596-9604
The role of ankyrin in the formation and stabilization of the spectrin-based skeletal meshwork and of band 3 oligomers was studied by characterizing, in nb/nb mouse red cells, the effect of ankyrin deficiency on skeletal ultrastructure, band 3-skelet
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::e0d55557d485b8c98f3d96780a5a0bcf
https://doi.org/10.1021/bi9704966
https://doi.org/10.1021/bi9704966
Autor:
Josef T. Prchal, Ladislav Chrobak, H. L. Rubin, Jiri Palek, Vaclav Brabec, J. L. Murray, LM Snyder, WD Melrose, WM Taylor, Petr Jarolim, S.K. Ballas
Publikováno v:
Blood. 88:4366-4374
Hereditary spherocytosis (HS) is a common hemolytic anemia of variable clinical expression. Pathogenesis of HS has been associated with defects of several red cell membrane proteins including erythroid band 3. We have studied erythrocyte membrane pro
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::515392f790c6722ed395723d58320652
https://doi.org/10.1182/blood.v88.11.4366.4366
https://doi.org/10.1182/blood.v88.11.4366.4366
Publikováno v:
Journal of Clinical Investigation. 98:2300-2307
We studied a patient with a severe spherocytic hemolytic anemia without family history of spherocytosis. Analysis of patient's erythrocyte membrane proteins revealed spectrin deficiency and a truncated alpha spectrin protein. We determined that the p
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::6345d34e5723e155286a3acccd6dfc44
https://doi.org/10.1172/jci119041
https://doi.org/10.1172/jci119041
Publikováno v:
Blood. 87:3462-3469
In this investigation, we have measured the invasion and growth of the malaria parasite Plasmodium falciparum into elliptocytic red blood cells (RBCs) obtained from subjects with homozygous hereditary elliptocytosis. These elliptocytic RBCs have been
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_________::913a2d165e40bac438d09d365aa4119e
https://doi.org/10.1182/blood.v87.8.3462.bloodjournal8783462
https://doi.org/10.1182/blood.v87.8.3462.bloodjournal8783462
Autor:
Jiri Palek, Hani Hassoun, Scott J. Yi, James Murray, J. N. Vassiliadis, Manjit Hanspal, Christine A. Johnson
Publikováno v:
Blood. 87:2538-2545
Red cell membrane protein analysis by sodium dodecyl sulfate- polyacrylamide gel electrophoresis (SDS-PAGE) and direct quantitation by radioimmunoassay or cytofluorometry defines four distinct subsets of patients with hereditary spherocytosis: Patien
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_________::470dfc71746516996f45f629ed989522
https://doi.org/10.1182/blood.v87.6.2538.bloodjournal8762538
https://doi.org/10.1182/blood.v87.6.2538.bloodjournal8762538
Autor:
Manjit Hanspal, Scott J. Yi, James Murray, S. S. Winter, Hani Hassoun, J. N. Vassiliadis, R. E. Ware, Jiri Palek, Shyh-Shin Chiou
Publikováno v:
Journal of Clinical Investigation. 96:2623-2629
We describe a spectrin variant characterized by a truncated beta chain and associated with hereditary spherocytosis. The clinical phenotype consists of a moderate hemolytic anemia with striking spherocytosis and mild spiculation of the red cells. We
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::975d3472e75ca3ec28cbf288e768f8ab
https://doi.org/10.1172/jci118327
https://doi.org/10.1172/jci118327
Autor:
Laura H. Derick, Pilarin E. Nichols, Dominick Amato, James D. Corbett, Jiri Palek, Shyh-Shin Chiou, Michael Cho, Shih-Chun Liu, David E. Golan, Scott J. Yi
Publikováno v:
Blood. 86:349-358
Southeast Asian ovalocytosis (SAO) is an asymptomatic trait characterized by rigid, poorly deformable red cells that resist invasion by several strains of malaria parasites. The underlying molecular genetic defect involves simple heterozygous state f
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_________::8b2bb9a7ad3c18686c90dad37287a45c
https://doi.org/10.1182/blood.v86.1.349.bloodjournal861349
https://doi.org/10.1182/blood.v86.1.349.bloodjournal861349
Publikováno v:
Blood. 85:3278-3282
Combined deficiency of ankyrin and spectrin represents the most common biochemical abnormality in hereditary spherocytosis (HS). To examine whether a decrease in ankyrin mRNA represents a frequent cause of this type of HS, we took advantage of the re
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::61e2ec28a4aea391c94cefbbae562d6f
https://doi.org/10.1182/blood.v85.11.3278.bloodjournal85113278
https://doi.org/10.1182/blood.v85.11.3278.bloodjournal85113278