Zobrazeno 1 - 10
of 23
pro vyhledávání: '"Janusz Ksiażyk"'
Autor:
Agnieszka Budka-Chrzęszczyk, Agnieszka Szlagatys-Sidorkiewicz, Ewa Bień, Ninela Irga-Jaworska, Anna Borkowska, Małgorzata Anna Krawczyk, Katarzyna Popińska, Hanna Romanowska, Ewa Toporowska-Kowalska, Magdalena Świder, Jan Styczyński, Tomasz Szczepański, Janusz Książyk
Publikováno v:
Nutrients, Vol 16, Iss 9, p 1327 (2024)
“Managing Undernutrition in Pediatric Oncology” is a collaborative consensus statement of the Polish Society for Clinical Nutrition of Children and the Polish Society of Pediatric Oncology and Hematology. The early identification and accurate man
Externí odkaz:
https://doaj.org/article/3708cba4b8e04444b806ac5492a74680
Autor:
Hanna Romanowska, Aleksandra Wilk, Mikołaj Danko, Anna Borkowska, Katarzyna Popińska, Marta Sibilska, Joanna Żydak, Wojciech Marciniak, Agnieszka Szlagatys-Sidorkiewicz, Janusz Książyk
Publikováno v:
Nutrients, Vol 16, Iss 8, p 1179 (2024)
This study continues the research in which we determined the concentration of aluminum in children receiving long-term parenteral nutrition (LPN). Since our results were interesting, we decided to assay arsenic (As) and cobalt (Co) in the collected m
Externí odkaz:
https://doaj.org/article/4a243397764d45768351bfbf678572e0
Autor:
Kacper Toczyłowski, Joanna Łasecka-Zadrożna, Ilona Pałyga-Bysiecka, Kamila Maria Ludwikowska, Magdalena Okarska-Napierała, Natalia Dudek, Aneta Afelt, Catherine Suski, Miron Bartosz Kursa, Teresa Jackowska, Ernest Kuchar, Leszek Szenborn, Katarzyna Mazur-Melewska, Marta Barszcz, Elżbieta BerdejSzczot, Sebastian Brzuszkiewicz, Piotr Buda, Alicja Czajka, Agnieszka Czech, Ewa Czerwińska, Magdalena Figlerowicz, Małgorzata FirekPędras, Aneta Gawlik, Ewelina Gowin, Olga Izdebska, Danuta JanuszkiewiczLewandowska, Justyna Kiepuszka, Agnieszka Koczwara, Danuta Koszałko, Magdalena KośmiderŻurawska, Janusz Książyk, Beata Kucińska, Martyna Kukawska, Anita Lackowska, Katarzyna Łapacz, Agnieszka Maliszak, Anna Mania, Joanna Mańdziuk, Artur Mazur, Cezary Niszczota, Paulina OpalińskaZielonka, Katarzyna Rojewska, Anna RożnowskaWójtowicz, Bartosz Siewert, Paulina Sobiczewska, Lidia Stopyra, Agnieszka StrobaŻelek, Joanna StryczyńskaKazubska, Tomasz Szatkowski, Barbara Szczepańska, Maciej Szczukocki, Robert Szylo, Filip Tyc, Katarzyna Wielgos, Ewa Wołowska, Jacek Wysocki, Anna Zacharzewska, Marcin Zaniew, Marzena Zielińska, Katarzyna ZiębaGlonek
Publikováno v:
International Journal of Infectious Diseases, Vol 122, Iss , Pp 703-709 (2022)
Objectives: Multisystem inflammatory syndrome in children (MIS-C) is the result of an immune response triggered by a previous exposure to SARS-CoV-2. The clinical presentation of MIS-C overlaps with other life-threatening bacterial infections, in whi
Externí odkaz:
https://doaj.org/article/089a6910da5e4862b80962097520ae35
Autor:
Magdalena Kaczor, Milena Greczan, Karolina Kierus, Ewa Ehmke vel Emczyńska‐Seliga, Elżbieta Ciara, Barbara Piątosa, Dariusz Rokicki, Janusz Książyk, Dorota Wesół‐Kucharska
Publikováno v:
JIMD Reports, Vol 63, Iss 3, Pp 199-206 (2022)
Abstract Glycogen storage disease type 1b (GSD 1b) is an inherited metabolic defect caused by biallelic mutations in the SLC37A4 gene encoding microsomal glucose‐6‐phosphate (G6P) transporter in the endoplasmic reticulum (ER) membrane. Ineffectiv
Externí odkaz:
https://doaj.org/article/7b1d9a5cd1ba434da70d48b846a85109
Autor:
Piotr Buda, Ewa Strauss, Danuta Januszkiewicz-Lewandowska, Ewa Czerwinska, Kamila Ludwikowska, Leszek Szenborn, Ewelina Gowin, Magdalena Okarska-Napierała, Ernest Kuchar, Janusz Ksia̧zyk
Publikováno v:
Frontiers in Pediatrics, Vol 10 (2022)
BackgroundMacrophage activation syndrome (MAS) is a potentially life-threatening complication of various inflammatory disorders, including multisystem inflammatory syndrome in children (MIS-C). MIS-C refractory to treatment should raise suspicion of
Externí odkaz:
https://doaj.org/article/795491e5ca924e6593c2a106e8832aef
Autor:
Magdalena Okarska-Napierała, Kamila Ludwikowska, Teresa Jackowska, Janusz Książyk, Piotr Buda, Artur Mazur, Leszek Szenborn, Bożena Werner, Jacek Wysocki, Ernest Kuchar
Publikováno v:
Pediatria Polska, Vol 96, Iss 2, Pp 121-128 (2021)
Multisystem Inflammatory Syndrome in Children (MIS-C) is a new clinical entity occurring in children and young adults, which is associated with the SARS-CoV-2 infection. The first cases of MIS-C were diagnosed in Poland in May 2020. Since October 202
Externí odkaz:
https://doaj.org/article/63306eb1d187483bb7fef668894bfcc9
Autor:
Ewa Bernatowska, Małgorzata Pac, Edyta Heropolitańska-Pliszka, Barbara Pietrucha, Nel Dąbrowska-Leonik, Małgorzata Skomska-Pawliszak, Katarzyna Bernat-Sitarz, Katarzyna Krzysztopa-Grzybowska, Beata Wolska-Kuśnierz, Nadia Bohynikova, Ewa Augustynowicz, Ewa Augustynowicz-Kopeć, Maria Korzeniewska-Koseła, Anna Wieteska-Klimczak, Janusz Książyk, Teresa Jackowska, Mirjam van den Burg, Jean-Laurent Casanova, Capucine Picard, Bożena Mikołuć
Publikováno v:
Frontiers in Pediatrics, Vol 10 (2022)
ObjectiveWe aimed to assess BCG (Bacillus Calmette-Guérin) complications in patients with Inborn Errors of Immunity (IEI), according to the inherited disorders and associated immunological defects, as well as the different BCG substrains.MaterialWe
Externí odkaz:
https://doaj.org/article/9b346cafab36422a8915fa2ddf6637ff
Publikováno v:
Diagnostics, Vol 10, Iss 5, p 297 (2020)
Background: The published data on the long-term outcomes of glycogen storage disease (GSD) patients is sparse in the literature. The aim of this study was to analyze the long-term (over 20 years) follow-up of patients with hepatic types of GSD-I, III
Externí odkaz:
https://doaj.org/article/734de8208c2c4086a51dc544e684defe
Autor:
Agnieszka Rusińska, Paweł Płudowski, Mieczysław Walczak, Maria K. Borszewska-Kornacka, Artur Bossowski, Danuta Chlebna-Sokół, Justyna Czech-Kowalska, Anna Dobrzańska, Edward Franek, Ewa Helwich, Teresa Jackowska, Maria A. Kalina, Jerzy Konstantynowicz, Janusz Książyk, Andrzej Lewiński, Jacek Łukaszkiewicz, Ewa Marcinowska-Suchowierska, Artur Mazur, Izabela Michałus, Jarosław Peregud-Pogorzelski, Hanna Romanowska, Marek Ruchała, Piotr Socha, Mieczysław Szalecki, Mirosław Wielgoś, Danuta Zwolińska, Arkadiusz Zygmunt
Publikováno v:
Frontiers in Endocrinology, Vol 9 (2018)
IntroductionVitamin D deficiency is an important public health problem worldwide. Vitamin D deficiency confers a significant risk for both skeletal and non-skeletal disorders and a number of lifelong negative health outcomes. The objectives of this e
Externí odkaz:
https://doaj.org/article/1e7adc0910754ccdbee1ead3c13dc35d
Autor:
Yvan Vandenplas, Bernard Berger, Virgilio Paolo Carnielli, Janusz Ksiazyk, Hanna Lagström, Manuel Sanchez Luna, Nathalia Migacheva, Jean-Marc Mosselmans, Jean-Charles Picaud, Mike Possner, Atul Singhal, Martin Wabitsch
Publikováno v:
Nutrients, Vol 10, Iss 9, p 1161 (2018)
The authors reviewed the published evidence on the presence of oligosaccharides in human milk (HMO) and their benefits in in vitro and in vivo studies. The still limited data of trials evaluating the effect of mainly 2′-fucosyllactose (2′-FL) on
Externí odkaz:
https://doaj.org/article/21dbe45ed8c9437e99ddf92c3a773879