Zobrazeno 1 - 10
of 38
pro vyhledávání: '"Jan Chlumsky"'
Autor:
Marc Miravitlles, Alice M. Turner, María Torres-Duran, Hanan Tanash, Carlota Rodríguez-García, José Luis López-Campos, Jan Chlumsky, Catarina Guimaraes, Juan Luis Rodríguez-Hermosa, Angelo Corsico, Cristina Martinez-González, José María Hernández-Pérez, Ana Bustamante, David G. Parr, Francisco Casas-Maldonado, Ana Hecimovic, Wim Janssens, Beatriz Lara, Miriam Barrecheguren, Cruz González, Jan Stolk, Cristina Esquinas, Christian F. Clarenbach
Publikováno v:
Respiratory Research, Vol 23, Iss 1, Pp 1-12 (2022)
Abstract Background Alpha-1 antitrypsin deficiency (AATD) is a rare disease that is associated with an increased risk of pulmonary emphysema. The European AATD Research Collaboration (EARCO) international registry was founded with the objective of ch
Externí odkaz:
https://doaj.org/article/c5edbf93afe94b6694247eb722b879fc
Autor:
Marc Miravitlles, Alice M. Turner, María Torres-Duran, Hanan Tanash, Carlota Rodríguez-García, José Luis López-Campos, Jan Chlumsky, Catarina Guimaraes, Juan Luis Rodríguez-Hermosa, Angelo Corsico, Cristina Martinez-González, José María Hernández-Pérez, Ana Bustamante, David G. Parr, Francisco Casas-Maldonado, Ana Hecimovic, Wim Janssens, Beatriz Lara, Miriam Barrecheguren, Cruz González, Jan Stolk, Cristina Esquinas, Christian F. Clarenbach
Publikováno v:
Respiratory Research, Vol 24, Iss 1, Pp 1-2 (2023)
Externí odkaz:
https://doaj.org/article/5fd972f5b5d54f009858f9ee9712bb04
Autor:
Miriam Barrecheguren, Karen O'Hara, Marion Wilkens, Jeanette Boyd, Ewa Kolda, Beatriz Lara, Joanna Chorostowska-Wynimko, Ilaria Ferrarotti, Jan Chlumský, Christian Clarenbach, Timm Greulich, Marc Miravitlles, Maria Sucena, Members of EARCO CRC Timm Greulich (Germany, co-chair) Marc Miravitlles (Spain co-chair). Steering committee:, Joanna Chorostowska-Wymiko (Poland), Ilaria Ferrarotti (Italy), Noel G. McElvaney (Ireland), Karen O'Hara (UKpatients' representative), Jan Stolk (Netherlands), Robert A. Stockley, Alice Turner (UK), Marion Wilkens (Germany patients' representative), EARCO members:, Angelo Corsico, Luciano Corda (Italy), Maria Sucena (Portugal), Miriam Barrecheguren (Spain ERS early career representative), Cristina Esquinas (Spain), David Parr, Ravi Mahadeva (UK), Jan Chlumsky (Czech Republic), Sabina Janciauskiene, Robert Bals (Germany), Jens Ulrik Jensen (Denmark), Kostas Kostikas (Greece), Malcolm Kohler, Christian Clarenbach (Switzerland), Alan Altraja (Estonia), Wim Jenssens, Silvia Pérez-Bogerd (Belgium), Caroline Gouder (Malta), Ana Hecimovic (Croatia), Aleksandra Dudvarski (Serbia), Alvils Krams (Latvia), Ruxandra Ulmeanu, Ana Zaharie (Rumania), Jean-François Mornex (France), Arzu Yorgancioglu (Tukey), Karin Schmid-Scherzer (Austria), Hanan Tanash, Eeva Piitulainen (Sweden), Oleksandr Mazulov (Ukraine), Yavor Ivanov (Bulgaria)
Publikováno v:
ERJ Open Research, Vol 6, Iss 4 (2020)
α1-antitrypsin deficiency (AATD) is a rare and under-recognised genetic condition. Owing to its low prevalence, international initiatives are key for conducting high-quality research in the field. From July 2018 to December 2019, the European Alpha-
Externí odkaz:
https://doaj.org/article/3dc0881f12aa43ff84cc6643d3544e50
Autor:
Timm Greulich, Alan Altraja, Miriam Barrecheguren, Robert Bals, Jan Chlumsky, Joanna Chorostowska-Wynimko, Christian Clarenbach, Luciano Corda, Angelo Guido Corsico, Ilaria Ferrarotti, Cristina Esquinas, Caroline Gouder, Ana Hećimović, Aleksandra Ilic, Yavor Ivanov, Sabina Janciauskiene, Wim Janssens, Malcolm Kohler, Alvils Krams, Beatriz Lara, Ravi Mahadeva, Gerry McElvaney, Jean-François Mornex, Karen O'Hara, David Parr, Eava Piitulainen, Karin Schmid-Scherzer, Niels Seersholm, Robert A. Stockley, Jan Stolk, Maria Sucena, Hanan Tanash, Alice Turner, Ruxandra Ulmeanu, Marion Wilkens, Arzu Yorgancioğlu, Ana Zaharie, Marc Miravitlles
Publikováno v:
ERJ Open Research, Vol 6, Iss 1 (2020)
Rationale and objectives Alpha-1 antitrypsin deficiency (AATD) is a genetic condition that leads to an increased risk of emphysema and liver disease. Despite extensive investigation, there remain unanswered questions concerning the natural history, p
Externí odkaz:
https://doaj.org/article/19427942e70f4ec99e35aebb5bcf081f
Autor:
Marc Miravitlles, Alice M. Turner, María Torres-Duran, Hanan Tanash, Carlota Rodríguez-García, José Luis López-Campos, Jan Chlumsky, Catarina Guimaraes, Juan Luis Rodríguez-Hermosa, Angelo Corsico, Cristina Martinez-González, José María Hernández-Pérez, Ana Bustamante, David G. Parr, Francisco Casas-Maldonado, Ana Hecimovic, Wim Janssens, Beatriz Lara, Miriam Barrecheguren, Cruz González, Jan Stolk, Cristina Esquinas, Christian F. Clarenbach
Publikováno v:
European Respiratory Journal. 61:2201949
Autor:
Katerina Kusalova, Jan Chlumsky
Publikováno v:
Monitoring airway disease.
Autor:
Ravi Mahadeva, Christian F. Clarenbach, Ilaria Ferrarotti, Aleksandra Ilic, Jan Stolk, Angelo Corsico, Robert A. Stockley, Alvils Krams, Malcolm Kohler, Jean-François Mornex, Maria Sucena, Alice M Turner, Eava Piitulainen, Cristina Esquinas, Beatriz Lara, Yavor Ivanov, Marc Miravitlles, Caroline Gouder, Gerry McElvaney, Karen O'Hara, Arzu Yorgancioglu, Ana Hećimović, Ana Zaharie, Robert Bals, Alan Altraja, Ruxandra Ulmeanu, Sabina Janciauskiene, Luciano Corda, Niels Seersholm, Karin Schmid-Scherzer, Jan Chlumsky, Timm Greulich, Wim Janssens, Marion Wilkens, Joanna Chorostowska-Wynimko, Miriam Barrecheguren, Hanan A Tanash, David G. Parr
Publikováno v:
ERJ Open Research, Vol 6, Iss 1 (2020)
ERJ Open Research, 6(1). EUROPEAN RESPIRATORY SOC JOURNALS LTD
ERJ Open Research
ERJ Open Research, European Respiratory Society, 2020, 6 (1), pp.00181-2019. ⟨10.1183/23120541.00181-2019⟩
ERJ Open Research, 6(1). EUROPEAN RESPIRATORY SOC JOURNALS LTD
ERJ Open Research
ERJ Open Research, European Respiratory Society, 2020, 6 (1), pp.00181-2019. ⟨10.1183/23120541.00181-2019⟩
Rationale and objectives Alpha-1 antitrypsin deficiency (AATD) is a genetic condition that leads to an increased risk of emphysema and liver disease. Despite extensive investigation, there remain unanswered questions concerning the natural history, p
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::31db799d18d787e6508162520d5dca7a
https://hdl.handle.net/1887/3184048
https://hdl.handle.net/1887/3184048
Autor:
Oliver Vit, Thomas Chung, Claus Vogelmeier, Timm Greulich, Jan Chlumsky, Kenneth R. Chapman, Noel G. McElvaney, Marion Wencker, Michael Fries
Publikováno v:
Clinical Problems Others.
Introduction: Infusion of human alpha-1 proteinase inhibitor (A1-PI) effectively slows the progression of emphysema in patients with alpha-1 antitrypsin deficiency (AATD). Nonetheless, weekly infusions of 60 mg/kg body weight are time consuming, cost
Autor:
Jana Klosova, Petr Vanik, Jaromir Zatloukal, Olga Ruzickova-Kirchnerova, Irena Krčmová, Eva Vernerova, Dagmar Kindlová, Jan Chlumsky, Vratislav Sedlák, Milan Terl, Petr Pohunek, Jaromir Bystron, Bronislava Novotná, Beata Hutyrova, Petr Panzner, Martina Vasakova
Publikováno v:
Allergy and immunology.
Introduction: Omalizumab is indicated for the treatment of severe allergic bronchial asthma and chronic spontaneous urticaria, although number of studies confirmed the efficacy of this therapy also on other IgE-mediated diseases. The aim of this stud
Publikováno v:
Clinical Respiratory Physiology, Exercise and Functional Imaging.
In patients with idiopatic pulmonary fibrosis (IPF), the exercise limitation has been associated with mechanical constrain of ventilation and oxygen desaturation during cardiopulmonary exercise test (CPET). Furthermore V/Q disbalance has been describ