Zobrazeno 1 - 9
of 9
pro vyhledávání: '"J. Manuel Pioner"'
Autor:
Beatrice Scellini, Nicoletta Piroddi, Marica Dente, J. Manuel Pioner, Cecilia Ferrantini, Corrado Poggesi, Chiara Tesi
Publikováno v:
International Journal of Molecular Sciences, Vol 25, Iss 18, p 9784 (2024)
Omecamtiv mecarbil (OM) is a small molecule that has been shown to improve the function of the slow human ventricular myosin (MyHC) motor through a complex perturbation of the thin/thick filament regulatory state of the sarcomere mediated by binding
Externí odkaz:
https://doaj.org/article/d6dae918ed444ff2b7450ae5f53d5822
Autor:
Samantha B Bremner, Christian J Mandrycky, Andrea Leonard, Ruby M Padgett, Alan R Levinson, Ethan S Rehn, J Manuel Pioner, Nathan J Sniadecki, David L Mack
Publikováno v:
Journal of Tissue Engineering, Vol 13 (2022)
Cardiomyopathy is currently the leading cause of death for patients with Duchenne muscular dystrophy (DMD), a severe neuromuscular disorder affecting young boys. Animal models have provided insight into the mechanisms by which dystrophin protein defi
Externí odkaz:
https://doaj.org/article/581a1be5350d48fab1ddd2b5784f58cf
Autor:
J. Manuel Pioner, Giulia Vitale, Lorenzo Santini, Chiara Palandri, Alfonso Bueno-Orovio, Francesca Margara, Nicoletta Piroddi, Beatrice Scellini, Chiara Tesi, Raffaele Coppini, Cecilia Ferrantini, Corrado Poggesi
Publikováno v:
Biophysical Journal. 121:435a-436a
Autor:
Cecilia Ferrantini, Beatrice Scellini, Giulia Vitale, J. Manuel Pioner, Silvia Querceto, Raffaele Coppini, Nicoletta Piroddi, Corrado Poggesi, Chiara Tesi
Publikováno v:
Biophysical Journal. 121:106a-107a
Autor:
Corrado Poggesi, Chiara Tesi, Alice Ward Racca, Michael R. Hoopmann, Cecilia Ferrantini, J. Manuel Pioner, Lil Pabon, Jordan M. Klaiman, Veronica Muskheli, Michael Regnier, Xuan Guan, Martin K. Childers, Deok Ho Kim, David L. Mack, Charles E. Murry, Robert L. Moritz, Jesse Macadangdang
Publikováno v:
Cardiovasc Res
Aims Heart failure invariably affects patients with various forms of muscular dystrophy (MD), but the onset and molecular sequelae of altered structure and function resulting from full-length dystrophin (Dp427) deficiency in MD heart tissue are poorl
Autor:
Sonette Steczina, J. Manuel Pioner, Marianna Langione, Neil Wood, Giulia Vitale, Chiara Tesi, Raffaele Coppini, Cecilia Ferrantini, Michael J. Previs, Corrado Poggesi, Michael Regnier
Publikováno v:
Biophysical Journal. 121:395a
Autor:
Marianna Langione, J. Manuel Pioner, Sonette Steczina, Giulia Vitale, Elisabetta Cerbai, Chiara Tesi, Raffaele Coppini, Michael Regnier, Corrado Poggesi, Cecilia Ferrantini
Publikováno v:
Biophysical Journal. 121:396a
Autor:
J. Manuel Pioner, Michael J. Bamshad, Anita E. Beck, Alice Ward Racca, Farid Moussavi-Harami, Yuanhua Cheng, Michael Regnier, Jordan M. Klaiman
Publikováno v:
The Journal of Physiology. 594:437-452
The contractile properties of human fetal cardiac muscle have not yet been described and functional information has been primarily obtained via studies in vivo with echocardiography. Most of what is known about the contractile properties of developin
Autor:
Patrizia Benzoni, Cecilia Ferrantini, Marianna Langione, Michael Regnier, Camilla Parmeggiani, Corrado Poggesi, Chiara Palandri, Chiara Tesi, Lorenzo Santini, Sara Landi, J. Manuel Pioner, David L. Mack, Raffaele Coppini, Andrea Barbuti, Flavia Lupi
Publikováno v:
Biophysical Journal. 116:95a