Zobrazeno 1 - 10
of 91
pro vyhledávání: '"Irmin Sternlieb"'
Autor:
Irmin Sternlieb, I. Herbert Scheinberg
Publikováno v:
Annals of the New York Academy of Sciences. 94:71-76
Autor:
Helmut Denk, M. Melter, Peter Heinz-Erian, Cord Langner, Thomas Müller, Josef Müller-Höcker, Hideaki Kikuta, Kunihiko Kobayashi, Helmut Ellemunter, Andrea Fuchsbichler, Barbara Schlenck, W Müller, Anand Pandit, Avinash M. Pradhan, Hironori Nagasaka, Irmin Sternlieb, M. Stuart Tanner, Kurt Zatloukal, Ashish Bavdekar
Publikováno v:
Hepatology. 39:963-969
Patients with Wilson's disease (WD), Indian childhood cirrhosis (ICC), and idiopathic copper toxicosis (ICT) develop severe liver disease morphologically characterized by ballooning of hepatocytes, inflammation, cytoskeletal alterations, and Mallory
Autor:
Irmin Sternlieb, Stuart Tanner, Peter Ferenci, Karel Caca, Georgios Loudianos, Diane W. Cox, G Mieli-Vergani, Michael L. Schilsky, Frieder Berr
Publikováno v:
Liver International. 23:139-142
Wilson disease is an inherited autosomal recessive disorder of hepatic copper metabolism leading to copper accumulation in hepatocytes and in extrahepatic organs such as the brain and the cornea. Originally Wilson disease was described as a neurodege
Autor:
Ellen van Binsbergen, Andreas R. Janecke, Thomas Müller, Helmut Denk, Helmut Ellemunter, Heiko Witt, Johann Deutsch, Bart van de Sluis, Ashish Bavdekar, Irmin Sternlieb, M. Stuart Tanner, Cisca Wijmenga, Alexandra Zhernakova, Helga Weirich-Schwaiger, Anand Pandit, W Müller
Publikováno v:
Journal of Hepatology, 38(2), 164-168. ELSEVIER SCIENCE BV
BACKGROUND: Non-Wilsonian hepatic copper toxicosis includes Indian childhood cirrhosis (ICC), endemic Tyrolean infantile cirrhosis (ETIC) and the non-Indian disease known as idiopathic copper toxicosis (ICT). These entities resemble the hepatic coppe
Autor:
Sukru Emre, Patricia A. Sheiner, Swan N. Thung, Michael L. Schilsky, Charles M. Miller, Irmin Sternlieb, Sebati Ozdemir, Myron Schwartz, Stephen R. Guy, E Atillasoy, C. V. R. Rathna Varma
Publikováno v:
Transplantation. 72:1232-1236
Background. Wilson's disease is an inherited disorder of copper metabolism characterized by reduced biliary copper excretion, which results in copper accumulation in tissues with liver injury and failure. Orthotopic liver transplantation (OLT) can be
Autor:
Irmin Sternlieb
Publikováno v:
Clinics in Liver Disease. 4:229-239
Concepts concerning the cause and the pathogenesis of Wilson's hepatolenticular degeneration have undergone a slow and tortuous evolution. 49 Hints regarding the presence of excess copper in the tissues of a patient were obtained as early as 1913, 1
Autor:
T C Gilliam, Michael L. Schilsky, J D Gitlin, Ronald J. Sokol, P Ferenci, Irmin Sternlieb, S Packman
Publikováno v:
Hepatology. 24:952-958
Publikováno v:
Hepatology. 22:1874-1879
Publikováno v:
Hepatology. 22:1782-1787
In an attempt to identify the cellular targets of copper toxicity, we studied the ultrastructure of hepatocytes in the livers of 23 Long-Evans Cinnamon (LEC) rats ranging in age from 10 to 89 weeks. The hepatic copper concentration ranged from 325 to