Zobrazeno 1 - 10
of 33
pro vyhledávání: '"Hubert SM"'
Autor:
Chloe Trayford, Alissa Wilhalm, Pamela Habibovic, Hubert Smeets, Florence van Tienen, Sabine van Rijt
Publikováno v:
Discover Nano, Vol 18, Iss 1, Pp 1-16 (2023)
Abstract Mutations in nuclear and mitochondrial genes are responsible for severe chronic disorders such as mitochondrial myopathies. Gene therapy using antisense oligonucleotides is a promising strategy to treat mitochondrial DNA (mtDNA) diseases by
Externí odkaz:
https://doaj.org/article/6b700379b3cc40748148803217c097a1
Autor:
Hubert Smekal
Publikováno v:
German Law Journal, Vol 24, Pp 1555-1576 (2023)
Most scholarly writings focus on the harmful effects of informal institutions. This article explores the positive influence of informal judicial institutions on the fundamental values of judicial systems. It develops a framework for assessing such in
Externí odkaz:
https://doaj.org/article/ee10b825956e4add87c3b5fa5610f502
Publikováno v:
Časopis pro Právní Vědu a Praxi, Vol 30, Iss 2 (2022)
Článek předkládá reakci autorů knihy na příspěvky v sympoziu. Vysvětluje některé metodologické otázky a v debatě s autory ostatních textů rozvíjí zejména témata jmenování soudců, kolegiality a vztahu soudců a médií.
Externí odkaz:
https://doaj.org/article/dd15c7df84af451ba90e18b03f4d6284
Autor:
Florence van Tienen, Ruby Zelissen, Erika Timmer, Marike van Gisbergen, Patrick Lindsey, Mattia Quattrocelli, Maurilio Sampaolesi, Elvira Mulder-den Hartog, Irenaeus de Coo, Hubert Smeets
Publikováno v:
Stem Cell Research & Therapy, Vol 10, Iss 1, Pp 1-10 (2019)
Abstract Background Myopathy and exercise intolerance are prominent clinical features in carriers of a point-mutation or large-scale deletion in the mitochondrial DNA (mtDNA). In the majority of patients, the mtDNA mutation is heteroplasmic with vary
Externí odkaz:
https://doaj.org/article/71f1490be04044e4aaabbe33e24d3106
Autor:
Olivier Boyer, Gillian Butler-Browne, Hector Chinoy, Giulio Cossu, Francesco Galli, James B. Lilleker, Alessandro Magli, Vincent Mouly, Rita C. R. Perlingeiro, Stefano C. Previtali, Maurilio Sampaolesi, Hubert Smeets, Verena Schoewel-Wolf, Simone Spuler, Yvan Torrente, Florence Van Tienen, Study Group, H. Aldearee, A. Bisson, L. Bragg, V. Bridoux, R. Duelen, A. Farini, E. Gazzero, N. Giarratana, C. Giverne, L. Meggiolaro, E. Negroni, E. Porrello, R. Tonlorenzi, C. Villa, L. Yedigaryan, A. Zamboni
Publikováno v:
Frontiers in Genetics, Vol 12 (2021)
This article will review myogenic cell transplantation for congenital and acquired diseases of skeletal muscle. There are already a number of excellent reviews on this topic, but they are mostly focused on a specific disease, muscular dystrophies and
Externí odkaz:
https://doaj.org/article/e780aee03b7b42b9af7b9f07f3c2c35c
Publikováno v:
Časopis pro Právní Vědu a Praxi, Vol 29, Iss 2 (2021)
Tento příspěvek je koncipován jako odpověď autorů monografie Domestic Judicial Treatment of European Court of Human Rights Case Law: Beyond Compliance (KOSAŘ, D. et al. Routledge, 2020) na reakce komentátorů v tomto sympoziu. Rekapitulujeme
Externí odkaz:
https://doaj.org/article/0ad304a2ccc844729760920c96b78e7c
Autor:
Debora Grasso, Hyllana C. D. Medeiros, Luca X. Zampieri, Vanesa Bol, Pierre Danhier, Marike W. van Gisbergen, Caroline Bouzin, Davide Brusa, Vincent Grégoire, Hubert Smeets, Alphons P. M. Stassen, Ludwig J. Dubois, Philippe Lambin, Marie Dutreix, Pierre Sonveaux
Publikováno v:
Frontiers in Pharmacology, Vol 11 (2020)
The clinical management of head and neck squamous cell carcinoma (HNSCC) commonly involves chemoradiotherapy, but recurrences often occur that are associated with radioresistance. Using human SQD9 laryngeal squamous cell carcinoma cancer cells as a m
Externí odkaz:
https://doaj.org/article/b78719403dbc49b78722d46c6693f7ee
Autor:
Hubert Śmietanka, Przemysław Ranachowski, Zbigniew Ranachowski, Krzysztof Wieczorek, Stanislav Kudela
Publikováno v:
Energies, Vol 15, Iss 10, p 3643 (2022)
The aim of this work was to investigate the effects of the currents flowing through surge arresters on the internal insulating textolite structure. The samples were removed from high-voltage arresters that were taken out of service due to malfunction
Externí odkaz:
https://doaj.org/article/79fdd0733e2b49f8b12ecb6321a0d955
Autor:
Petr Kaniok, Hubert Smekal
Publikováno v:
Romanian Journal of European Affairs, Vol 9, Iss 4, Pp 59-78 (2009)
The text firstly briefly introduces the Presidency as an instrument or tool of the decision-making process within the EU. The article further presents the basic potential criteria for evaluating an EU Council Presidency. Then the course of the Czech
Externí odkaz:
https://doaj.org/article/0d46496182fc49d9adba6382bb8ed7f6
Autor:
Robert Plaga, Hubert Smekal
Publikováno v:
Acta Universitatis Agriculturae et Silviculturae Mendelianae Brunensis, Vol 52, Iss 3, Pp 97-106 (2004)
This working paper seeks to define perspectives of the functioning of the Stability and Growth Pact as a tool for regulation of national fiscal policies through analysis and description of legal acts regarding the Pact and through analysis and statis
Externí odkaz:
https://doaj.org/article/4ea6bd33ba8e47609b541f7529635195