External Validation of International Risk-Prediction Models of IgA Nephropathy in an Asian-Caucasian Cohort

Autor: Yuemiao Zhang, Ling Guo, Zi Wang, Jinwei Wang, Lee Er, Sean J. Barbour, Hernan Trimarchi, Jicheng Lv, Hong Zhang

Publikováno v: Kidney International Reports, Vol 5, Iss 10, Pp 1753-1763 (2020)

Introduction: Two prediction models for IgA nephropathy (IgAN) using clinical variables and the Oxford MEST scores were developed and validated in 2 multiethnic cohorts. Additional external validation is required. Methods: Biopsy-proven Chinese and A

Externí odkaz: https://doaj.org/article/4d99fbe1330e455da1deb84d5c512258

Corticosteroids and mycophenolic acid analogues in immunoglobulin A nephropathy with progressive decline in kidney function

Autor: Ana Huerta, Eva Mérida, Laura Medina, Maria Fernandez, Eduardo Gutierrez, Eduardo Hernandez, Paula López-Sánchez, Angel Sevillano, Jose Portolés, Hernan Trimarchi, Manuel Praga

Publikováno v: Clinical kidney journal. 15(4)

Background A randomized controlled trial demonstrated a beneficial effect of corticosteroids (CS) + cyclophosphamide followed by azathioprine in progressive immunoglobulin A nephropathy (IgAN). Although treatment with CS and mycophenolic acid analogu

Externí odkaz: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::8c37f77845195f48fefe5e023b5dfe30
https://pubmed.ncbi.nlm.nih.gov/35371455

Targeting the Alternative Complement Pathway With Iptacopan to Treat IgA Nephropathy: Design and Rationale of the APPLAUSE-IgAN Study

Autor: Dana V. Rizk, Brad H. Rovin, Hong Zhang, Naoki Kashihara, Bart Maes, Hernán Trimarchi, Vlado Perkovic, Matthias Meier, Dmitrij Kollins, Olympia Papachristofi, Alan Charney, Jonathan Barratt

Publikováno v: Kidney International Reports, Vol 8, Iss 5, Pp 968-979 (2023)

Introduction: Targeting the alternative complement pathway (AP) is an attractive therapeutic strategy because of its role in immunoglobulin A nephropathy (IgAN) pathophysiology. Iptacopan (LNP023), a proximal complement inhibitor that specifically bi

Externí odkaz: https://doaj.org/article/e273eb3d888049e0b8276461498c3f08

Consenso de expertos sobre recomendaciones basadas en evidencia para el diagnóstico, tratamiento y seguimiento de enfermedad de Fabry en pediatría

Autor: Richard Baquero Rodriguez, Ana Katherina Serrano Gayubo, Juan Carlos Prieto Rivera, Juan Guillermo Cardenas Aguilera, Carmen Inés Rodríguez Cuéllar, Maria Fernanda Reina Ávila, Mayra Alexandra Estévez Capacho, Heidy Mateus, Maylin Valencia González, Kelly Rocío Chacón Acevedo, Maria Paula Gutiérrez Sepúlveda, Dominique P Germain, Juan Politei, Alejandro Fabian Fainboim, Magdalena Cerón Rodríguez, Gustavo Cabrera, Edicson Rodríguez Ibarra, Martha Isabel Carrascal Guzmán, Lida Esperanza Martínez Cáceres, Sandra Yaneth Ospina Lagos, Hernán Trimarchi, Miguel Liern

Publikováno v: Revista Ciencias de la Salud, Vol 21, Iss 3 (2023)

Antecedentes: La enfermedad de Fabry (EF) es una enfermedad rara ligada a X secundaria al depósito lisosomal de glicoesfingolípidos debido a la deficiencia de la enzima alfa galactosidasa A (α-Gal A). A pesar de su baja frecuencia, es una condici�

Externí odkaz: https://doaj.org/article/af4409f518254bde91f5bf4071f9aac5

Nationwide and Long-Term Survey of Primary Glomerulonephritis in Japan as Observed in 1,850 Biopsied Cases

Autor: A.B. Cefalù, Mary Elizabeth Gellens, M. de Oña, D. Noto, José L. Ojeda, Antonio Carroccio, M. Rizzo, G. Cavera, S. Mélon, Olivero Jj, Epifanio Di Natale, A. Panizo, R. Caldarella, Yuichi Hasegawa, I. Sola, Jesus Elizalde Eguinoa, Maurizio Li Vecchi, W. Schlumberger, Hiie Maria Gussak, S. Gallo, Shigeruko Iijima, Juan M. Gonzalez, Mitsuhiro Ueno, Teiji Izumi, Han-Hsiang Chen, Taner Camsari, Jose María Onaindía Rico, Akio Koyama, Luan D. Truong, Hernan Trimarchi, David F. Grant, Fujio Otsuka, Preben Bjerregaard, Masaaki Arakawa, Giuseppe Montalto, Jui-Chi Yeh, Wadi N. Suki, C.M. Barbagallo, E. de Alava, Ali Çelik, Maurizio Soresi, M. Fooke, Hernan M. Trimarchi, M. Brack, A. Laures, Yi-Chou Chen, Manuel Benítez Sánchez, Caner Çavdar, Roberto Barrios, M.D. Lozano, Satinder S. Sarang, Banu Onvural, M. Rodríguez, Cándido Suarez Rodriguez, İlgi Şemin, R. Alvarez, C. Schroeder, A. Notarbartolo, F.J. Pardo-Mindán, Hülya Öztüre, A. Rao Camemi, Anthony J. Bleyer, E. Gómez, P. Errasti, G. Marino, Fabrizio Renda, Maria José Merino Perez, J. Alvarez-Grande, Richard G. Appel, Ihor Gussak, T. Stephen Brennan, Fernando Fernández Girón, Salih Kavukçu, Satoshi Ito, Rick G. Schnellmann, Gary W. Miller, M.R. Averna, A. Pobes, Roberto Lasso de la Vega

Publikováno v: Nephron. 82:205-213

Primary chronic glomerulonephritis is the most common cause of end-stage renal failure in Japan. The incidence in dialysis patients in Japan is about four times higher than in the United States for reason which are unclear. We conducted a nationwide

Externí odkaz: https://explore.openaire.eu/search/publication?articleId=doi_________::9ce6bc2cbc6f96124a1cea6eb140da55
https://doi.org/10.1159/000045404