Zobrazeno 1 - 10
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pro vyhledávání: '"Hemophilias"'
Akademický článek
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Publikováno v:
Pediatrics In Review. 42:672-683
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::74e3d75022762ddfe3b4444788e7f470
https://doi.org/10.1542/pir.2020-004143
https://doi.org/10.1542/pir.2020-004143
Autor:
Ahmed Ali Ali Assem, Mahmoud Mohammed Mousa Bazeed, Mahmoud Abdeirashed Abdelkhalek, Mohammed Khalil Mohammed Abdalla
Publikováno v:
Al-Azhar Medical Journal. 50:3011-3022
Background: Hemophilia is an X-linked heritable coagulopathy with an overall prevalence of approximately 1 in 10,000 individuals. Hemophilias are rare X linked hereditary bleeding disorders. Platelets may be among the determinants of variability in b
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_________::8b46a9ec165b6f94eef903b26a870994
https://doi.org/10.21608/amj.2021.196438
https://doi.org/10.21608/amj.2021.196438
Autor:
Emmanuel J. Favaloro, Giuseppe Lippi
Publikováno v:
Blood Coagulation & Fibrinolysis. 31:237-242
Hemophilia comprises two distinct genetic disorders caused by missing or defective clotting factor VIII (hemophilia A) or clotting factor IX (hemophilia B). The management of these conditions has been for long based on replacement therapies, but emer
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::efef7fb34db23027f5d7a1bb642a0a50
https://doi.org/10.1097/mbc.0000000000000905
https://doi.org/10.1097/mbc.0000000000000905
Autor:
Charles T. Esmon, Usha R. Pendurthi, L. Vijaya Mohan Rao, Vijay Kondreddy, Shabbir A. Ansari, Kaushik Das, Shiva Keshava, John H. Griffin
Publikováno v:
Blood. 137:3428-3442
Recombinant factor FVIIa (rFVIIa) is used as a hemostatic agent to treat bleeding disorders in hemophilia patients with inhibitors and other groups of patients. Our recent studies showed that FVIIa binds endothelial cell protein C receptor (EPCR) and
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::d88ed033ebf717637c8edaddc65784c1
https://doi.org/10.1182/blood.2020008417
https://doi.org/10.1182/blood.2020008417
Autor:
Irina Murakhovskaya, Kafui A. Demasio
Publikováno v:
NeoReviews. 22:e95-e103
Hematologic conditions in reproductive-age women can complicate pregnancy and the neonatal period. Affected pregnancies have a higher risk of severe morbidity and mortality. Coagulation factor changes that occur in the normal state of pregnancy can d
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::38d19c7687d2f6073b748b1f51e45d3b
https://doi.org/10.1542/neo.22-2-e95
https://doi.org/10.1542/neo.22-2-e95
Publikováno v:
Medicine - Programa de Formación Médica Continuada Acreditado. 13:1231-1241
espanolLa hemostasia es un proceso complejo en el que participan multitud de agentes (endotelio, proteinas, plaquetas, etc.) para conseguir un estado de homeostasis y evitar las hemorragias espontaneas y limitar el sangrado ante una lesion. El conoci
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_________::9745efa63044e49db43df3ca8d8414b0
https://doi.org/10.1016/j.med.2020.12.001
https://doi.org/10.1016/j.med.2020.12.001
Autor:
Nicoletta Machin, Margaret V. Ragni
Publikováno v:
Blood Adv
von Willebrand disease (VWD) is a congenital bleeding disorder characterized by deficient or defective von Willebrand factor (VWF). Among women with VWD, postpartum hemorrhage (PPH) is common. Treatment options at delivery include plasma-derived VWF
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::7ffa5b7c77b35cf953c8ea52ec65d76b
https://doi.org/10.1182/bloodadvances.2020002046
https://doi.org/10.1182/bloodadvances.2020002046
Publikováno v:
Blood. 135:2211-2223
We recently showed that clotting factor VIIa (FVIIa) binding to endothelial cell protein C receptor (EPCR) induces anti-inflammatory signaling and protects vascular barrier integrity. Inflammation and vascular permeability are thought to be major con
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_________::65a461c8a217534534627fe14dc543e0
https://doi.org/10.1182/blood.2019003824
https://doi.org/10.1182/blood.2019003824
Autor:
Krista Fischer, Irene C. van der Schaaf, Willem P.Th.M. Mali, Frederik J. A. Beek, Wouter Foppen
Publikováno v:
Blood Advances. 4:113-121
Magnetic resonance imaging (MRI) is considered as the reference standard to assess early joint changes in hemophilia. However, the clinical relevance of MRI findings is still unknown. The aim of this prospective study was to assess the predictive val
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::84f0f27257de9271943b91ca092b9722
https://doi.org/10.1182/bloodadvances.2019001238
https://doi.org/10.1182/bloodadvances.2019001238