Zobrazeno 1 - 10
of 19
pro vyhledávání: '"Gustavo Monteiro Viana"'
Autor:
Bruno Duarte Gomes, Givago da Silva Souza, Gustavo Monteiro Viana, Isabel Cristina Neves de Souza, Patricia do Socorro Queiroz Feio, Ida Vanessa Doederlein Schwartz, Diane Ruschel Marinho, Manoel da Silva Filho, Roberto Giugliani, Luiz Carlos de Lima Silveira, Luiz Carlos Santana da Silva
Publikováno v:
Case Reports in Ophthalmology, Vol 3, Iss 1, Pp 104-112 (2012)
Purpose: To evaluate the visual system of patients suffering from type I or VI mucopolysaccharidosis (MPS) by recording the visual evoked cortical potential (VECP). Methods: Two patients with MPS VI and 2 patients with MPS I were tested before and af
Externí odkaz:
https://doaj.org/article/651b8bfe36cb42209a5e8c02f308255c
Publikováno v:
Molecular Biology Reports. 48:363-370
Mucopolysaccharidosis type I (MPS I) is a lysosomal storage disease caused by a mutation in the IDUA gene, which codes α-L-iduronidase (IDUA), a lysosomal hydrolase that degrades two glycosaminoglycans (GAGs): heparan sulfate (HS) and dermatan sulfa
Autor:
Paula Deboni, Edwin A. Yates, Luiz Patekoski Braga, Gustavo Monteiro Viana, Marcelo A. Lima, Carlos Modesto Vera Palomino, Renan P. Cavalheiro, Helena B. Nader, Maria Cecília Zorél Meneghetti
Publikováno v:
Carbohydrate polymers. 255
The cell surface and extracellular matrix polysaccharide, heparan sulfate (HS) conveys chemical information to control crucial biological processes. HS chains are synthesized in a non-template driven process mainly in the Golgi apparatus, involving a
Autor:
Frances M. Platt, Gustavo Monteiro Viana, Shaukat Khan, David Priestman, Alexey V. Pshezhetsky, Shunji Tomatsu
Publikováno v:
Journal of Clinical Medicine; Volume 9; Issue 2; Pages: 396
Journal of Clinical Medicine, Vol 9, Iss 2, p 396 (2020)
Journal of Clinical Medicine
Journal of Clinical Medicine, Vol 9, Iss 2, p 396 (2020)
Journal of Clinical Medicine
Mucopolysaccharidoses (MPS) are the group of lysosomal storage disorders caused by deficiencies of enzymes involved in the stepwise degradation of glycosaminoglycans. To identify brain pathology common for neurological MPS, we conducted a comprehensi
Autor:
Carlos Modesto Vera Palomino, Paula Deboni, Luiz Patekoski Braga, Maria Cecília Zorél Meneghetti, Gustavo Monteiro Viana, Marcelo A. Lima, Edwin A. Yates, Renan P. Cavalheiro, Helena B. Nader
The cell surface and extracellular matrix polysaccharide, heparan sulfate (HS) conveys chemical information to control or influence crucial biological processes. Attempts to describe its structure-function relationships with HS binding proteins in a
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::a2d6569e81cf582b128393101037af25
https://doi.org/10.1101/2020.01.23.916940
https://doi.org/10.1101/2020.01.23.916940
Autor:
Guilherme Baldo, Marcelo A. Lima, Alexey V. Pshezhetsky, Vânia D'Almeida, Gustavo Monteiro Viana, Renan P. Cavalheiro, Helena B. Nader, Esteban Alberto Gonzalez, Marcela Maciel Palacio Alvarez, Cinthia Castro do Nascimento
Publikováno v:
International Journal of Molecular Sciences
International Journal of Molecular Sciences, Vol 21, Iss 4, p 1459 (2020)
Volume 21
Issue 4
International Journal of Molecular Sciences, Vol 21, Iss 4, p 1459 (2020)
Volume 21
Issue 4
Mucopolysaccharidosis type I (MPS I) is caused by genetic deficiency of &alpha
l-iduronidase and impairment of lysosomal catabolism of heparan sulfate and dermatan sulfate. In the brain, these substrates accumulate in the lysosomes of neurons an
l-iduronidase and impairment of lysosomal catabolism of heparan sulfate and dermatan sulfate. In the brain, these substrates accumulate in the lysosomes of neurons an
Autor:
Wendy Dam, Gustavo Monteiro Viana, Mirian A. F. Hayashi, Lilian Caroline Gonçalves de Oliveira, Joana D'Arc Campeiro, Jacob van den Born, Fernando Carapeto, Lucas Carvalho Porta, Marcela B. Nering, Eduardo B. Oliveira, Gabriela Guilherme Monte
Publikováno v:
Scientific Reports, 9:3312. Nature Publishing Group
Scientific Reports, Vol 9, Iss 1, Pp 1-13 (2019)
Scientific Reports
Scientific Reports, Vol 9, Iss 1, Pp 1-13 (2019)
Scientific Reports
Activated proximal tubular epithelial cells (PTECs) play a crucial role in progressive tubulo-interstitial fibrosis in native and transplanted kidneys. Targeting PTECs by non-viral delivery vectors might be useful to influence the expression of impor
Autor:
Gustavo Monteiro Viana, Marcelo A. Lima, Andrew K. Powell, Edwin A. Yates, Timothy R. Rudd, Maria Cecília Zorél Meneghetti, Renan P. Cavalheiro, Mark A. Skidmore
Publikováno v:
Glycoconjugate Journal
Studying polysaccharide-protein interactions under physiological conditions by conventional techniques is challenging. Ideally, macromolecules could be followed by both in vitro spectroscopy experiments as well as in tissues using microscopy, to enab
Autor:
Gustavo Monteiro Viana, Felipe Macedo, Luis Alberto Luévano-Martínez, Hugo Aguilaniu, Isaias Glezer, Sayuri Miyamoto, Gabriel Loureiro Martins, Alex Inague, Karin A. Riske, Marcos Yukio Yoshinaga, Fernanda Marques da Cunha
Publikováno v:
Repositório Institucional da USP (Biblioteca Digital da Produção Intelectual)
Universidade de São Paulo (USP)
instacron:USP
Universidade de São Paulo (USP)
instacron:USP
The C. elegans lipase-like 5 (lipl-5) gene is predicted to code for a lipase homologous to the human gastric acid lipase. Its expression was previously shown to be modulated by nutritional or immune cues, but nothing is known about its impact on the
Publikováno v:
Reproduction, Fertility and Development. 32:304
Mucopolysaccharidosis type I (MPS I) is a lysosomal storage disease caused by a deficiency of the lysosomal hydrolase, α-L-iduronidase (IDUA). IDUA degrades heparan and dermatan sulfates, two types of glycosaminoglycan (GAG), important signalling an