Zobrazeno 1 - 10
of 16
pro vyhledávání: '"Giacomo Monzio Compagnoni"'
Publikováno v:
Acta Neuropathologica Communications, Vol 7, Iss 1, Pp 1-12 (2019)
Abstract Multiple System Atrophy (MSA) is a severe neurodegenerative disease clinically characterized by parkinsonism, cerebellar ataxia, dysautonomia and other motor and non-motor symptoms. Although several efforts have been dedicated to understandi
Externí odkaz:
https://doaj.org/article/5468d1fb8c904336b1368a6cd207cd2e
Autor:
Giacomo Monzio Compagnoni, Giulio Kleiner, Maura Samarani, Massimo Aureli, Gaia Faustini, Arianna Bellucci, Dario Ronchi, Andreina Bordoni, Manuela Garbellini, Sabrina Salani, Francesco Fortunato, Emanuele Frattini, Elena Abati, Christian Bergamini, Romana Fato, Silvia Tabano, Monica Miozzo, Giulia Serratto, Maria Passafaro, Michela Deleidi, Rosamaria Silipigni, Monica Nizzardo, Nereo Bresolin, Giacomo P. Comi, Stefania Corti, Catarina M. Quinzii, Alessio Di Fonzo
Publikováno v:
Stem Cell Reports, Vol 11, Iss 5, Pp 1185-1198 (2018)
Summary: Multiple system atrophy (MSA) is a progressive neurodegenerative disease that affects several areas of the CNS, whose pathogenesis is still widely unclear and for which an effective treatment is lacking. We have generated induced pluripotent
Externí odkaz:
https://doaj.org/article/325f58cfb0334279a093a2fea8e263cc
Autor:
Alba Pesini, Giacomo Monzio-Compagnoni, Eliana Barriocanal-Casado, Agustin Hidalgo-Gutierrez, Giulio Kleiner, Giussepe A. Yanez, Mohamed Bakkali, Edoardo Monfrini, Yashpal S. Chhonker, Saba Tadesse, Delfina Larrea, Daryl J. Murry, Caterina Mariotti, Barbara Castellotti, Luis Lopez, Alesio Di Fonzo, Estela Area-Gomez, Catarina M. Quinzii
Publikováno v:
Thursday, April 27.
Publikováno v:
Acta Neuropathologica Communications, Vol 7, Iss 1, Pp 1-12 (2019)
Acta Neuropathologica Communications
Acta Neuropathologica Communications
Multiple System Atrophy (MSA) is a severe neurodegenerative disease clinically characterized by parkinsonism, cerebellar ataxia, dysautonomia and other motor and non-motor symptoms. Although several efforts have been dedicated to understanding the ca
Autor:
Paola Rinchetti, Sara Bonato, Giacomo P. Comi, Andreina Bordoni, Rosamaria Silipigni, Stefania Corti, Giacomo Monzio Compagnoni, Stefano Duga, Edoardo Monfrini, Robertino Dilena, Dario Ronchi, Letizia Straniero, Nereo Bresolin, Alessio Di Fonzo
Publikováno v:
Parkinsonism & Related Disorders. 63:66-72
Introduction Neurofascin, encoded by NFASC, is a transmembrane protein that plays an essential role in nervous system development and node of Ranvier function. Anti-Neurofascin autoantibodies cause a specific type of chronic inflammatory demyelinatin
Autor:
Giacomo Monzio Compagnoni, Eliezer Masliah, Giacomo P. Comi, Stefania Corti, Nereo Bresolin, Alessio Di Fonzo
Publikováno v:
Mol Neurobiol
Although the pathogenesis of neurodegenerative diseases is still widely unclear, various mechanisms have been proposed and several pieces of evidence are supportive for an important role of mitochondrial dysfunction. The present review provides a com
Autor:
Gianluca Lopez, Alessio Di Fonzo, Sara Bonato, Stefania Corti, Alessandra Pittaro, Giacomo P. Comi, Emanuele Frattini, Giacomo Bitetto, Sabrina Salani, Fulvia Milena Cribiù, Dario Ronchi, Andreina Bordoni, Giacomo Monzio Compagnoni, Nereo Bresolin
Publikováno v:
Human molecular genetics. 28(23)
Allgrove syndrome (AS) is a rare disease with broad neurological involvement. Neurodegeneration can affect spinal motor neurons, Purkinje cells, striatal neurons and the autonomic system. The mechanisms that lead to neuronal loss are still unclear. R
Autor:
Alberto Albanese, Romana Fato, Christian Bergamini, Francesco Fortunato, Barbara Garavaglia, Giulio Kleiner, Marianna Guida, Alessio Di Fonzo, Giacomo P. Comi, Francesca Del Sorbo, Maria Teresa Pellecchia, Nereo Bresolin, Giacomo Monzio Compagnoni, Corrado Corti, Annamaria Vallelunga, Catarina M. Quinzii, Antonio E. Elia, Andreina Bordoni, Irene Pichler, Sabrina Salani, Gianluca Ardolino, Filippo Cogiamanian, Stefania Corti, Gabriele Mora, Chiara Reale, Dario Ronchi
Multiple System Atrophy is a severe neurodegenerative disorder which is characterized by a variable clinical presentation and a broad neuropathological spectrum. The pathogenic mechanisms are almost completely unknown. In the present study, we establ
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::ef3210306b4ae8fcef61358b727acf89
http://hdl.handle.net/10807/154897
http://hdl.handle.net/10807/154897
Autor:
Monica Nizzardo, Maura Samarani, Alessio Di Fonzo, Rosamaria Silipigni, Giacomo P. Comi, Maria Passafaro, Emanuele Frattini, Christian Bergamini, Manuela Garbellini, Giacomo Monzio Compagnoni, Arianna Bellucci, Massimo Aureli, Catarina M. Quinzii, Romana Fato, Francesco Fortunato, Sabrina Salani, Stefania Corti, Dario Ronchi, Elena Abati, Andreina Bordoni, Giulio Kleiner, Giulia Maia Serratto, Nereo Bresolin, Monica Miozzo, Michela Deleidi, Silvia Tabano, Gaia Faustini
Publikováno v:
Stem cell reports 11(5), 1185-1198 (2018). doi:10.1016/j.stemcr.2018.09.007
Stem Cell Reports
Stem Cell Reports, Vol 11, Iss 5, Pp 1185-1198 (2018)
Stem Cell Reports
Stem Cell Reports, Vol 11, Iss 5, Pp 1185-1198 (2018)
Summary Multiple system atrophy (MSA) is a progressive neurodegenerative disease that affects several areas of the CNS, whose pathogenesis is still widely unclear and for which an effective treatment is lacking. We have generated induced pluripotent
Externí odkaz:
https://explore.openaire.eu/search/publication?articleId=doi_dedup___::c095f121b1ba906c1a6f4b4fc5d74ef9
https://pub.dzne.de/record/140336
https://pub.dzne.de/record/140336
Autor:
Giulia Franco, Anna Chiara Di Caprio, Ilaria Trezzi, Giacomo Monzio Compagnoni, Stefania Corti, Giacomo P. Comi, Emanuele Frattini, Edoardo Monfrini, Alessio Di Fonzo, Valentina Melzi, Gianluca Ardolino, Filippo Cogiamanian, Gabriele Buongarzone, Nereo Bresolin, Dario Ronchi, Linda Borellini
Publikováno v:
Parkinsonismrelated disorders. 39