Zobrazeno 1 - 10
of 240
pro vyhledávání: '"Frank Bridoux"'
Autor:
Giovanni Palladini, Stefan Schönland, Giampaolo Merlini, Paolo Milani, Arnaud Jaccard, Frank Bridoux, Meletios A. Dimopoulos, Sriram Ravichandran, Ute Hegenbart, Wilfried Roeloffzen, M. Teresa Cibeira, Hermine Agis, Monique C. Minnema, Rui Bergantim, Roman Hájek, Cristina João, Alexandros Leonidakis, Giorgos Cheliotis, Pieter Sonneveld, Efstathios Kastritis, Ashutosh Wechalekar
Publikováno v:
Blood Cancer Journal, Vol 13, Iss 1, Pp 1-8 (2023)
Abstract Systemic light-chain (AL) amyloidosis is a rare and debilitating disease. Advances have been made in new treatments in recent years, yet real-world data on the management of the disease are scarce. EMN23 is a retrospective, observational stu
Externí odkaz:
https://doaj.org/article/b66ddf1ad30c445e87c57bf515f577a5
Autor:
Andrea Havasi, Cihan Heybeli, Nelson Leung, Avital Angel-Korman, Vaishali Sanchorawala, Oliver Cohen, Ashutosh Wechalekar, Frank Bridoux, Insara Jaffer, Victoria Gutgarts, Hani Hassoun, Maya Levinson, Cara Rosenbaum, Paolo Milani, Giovanni Palladini, Giampaolo Merlini, Ute Hegenbart, Stefan Schönland, Kaya Veelken, Alexander Pogrebinsky, Gheorghe Doros, Heather Landau
Publikováno v:
Blood Cancer Journal, Vol 12, Iss 8, Pp 1-8 (2022)
Abstract Effective systemic therapies suppress toxic light chain production leading to an increased proportion of patients with light chain (AL) amyloidosis who survive longer albeit with end-stage renal disease. There is a critical need to identify
Externí odkaz:
https://doaj.org/article/8310aa42eeb54a7f8e5412643a28329a
Autor:
Sophie Leflot, Philippe Leroy, Nathalie Demoulin, Selda Aydin, Guy Touchard, Vincent Javaugue, Marie-Christiane Vekemans, Frank Bridoux, Johann Morelle
Publikováno v:
Kidney Medicine, Vol 4, Iss 5, Pp 100445- (2022)
The kidney is commonly involved in multiple myeloma and other disorders producing monoclonal immunoglobulins. Crystalglobulinemia is a rare condition characterized by spontaneous crystallization and deposition of monoclonal immunoglobulins within the
Externí odkaz:
https://doaj.org/article/a0b05d77d6154bfab1386368314614b9
Autor:
Samih H. Nasr, Julie A. Vrana, Surendra Dasari, Frank Bridoux, Mary E. Fidler, Sihem Kaaki, Nathalie Quellard, Alexia Rinsant, Jean Michel Goujon, Sanjeev Sethi, Fernando C. Fervenza, Lynn D. Cornell, Samar M. Said, Ellen D. McPhail, Loren P. Herrera Hernandez, Joseph P. Grande, Marie C. Hogan, John C. Lieske, Nelson Leung, Paul J. Kurtin, Mariam P. Alexander
Publikováno v:
Kidney International Reports, Vol 3, Iss 1, Pp 56-64 (2018)
Fibrillary glomerulonephritis (FGN) is a rare disease with unknown pathogenesis and a poor prognosis. Until now, the diagnosis of this disease has required demonstration of glomerular deposition of randomly oriented fibrils by electron microscopy tha
Externí odkaz:
https://doaj.org/article/5a6bfb80b6b44dfca60e41125f0467d5
Autor:
Camille Cohen, Florent Joly, Audrey Sibille, Vincent Javaugue, Estelle Desport, Jean-Michel Goujon, Guy Touchard, Jean-Paul Fermand, Christophe Sirac, Frank Bridoux
Publikováno v:
Diagnostics, Vol 11, Iss 3, p 420 (2021)
Randall-type monoclonal immunoglobulin deposition disease (MIDD) is a rare disease that belongs to the spectrum of monoclonal gammopathy of renal significance (MGRS). Renal involvement is prominent in MIDD, but extra-renal manifestations can be prese
Externí odkaz:
https://doaj.org/article/48843799de3b4089aa06b0c245abb268
Autor:
Sophie Valleix, Guglielmo Verona, Noémie Jourde-Chiche, Brigitte Nédelec, P. Patrizia Mangione, Frank Bridoux, Alain Mangé, Ahmet Dogan, Jean-Michel Goujon, Marie Lhomme, Carolane Dauteuille, Michèle Chabert, Riccardo Porcari, Christopher A. Waudby, Annalisa Relini, Philippa J. Talmud, Oleg Kovrov, Gunilla Olivecrona, Monica Stoppini, John Christodoulou, Philip N. Hawkins, Gilles Grateau, Marc Delpech, Anatol Kontush, Julian D. Gillmore, Athina D. Kalopissis, Vittorio Bellotti
Publikováno v:
Nature Communications, Vol 7, Iss 1, Pp 1-14 (2016)
Decrease in Apolipoprotein C-III (ApoC-III) yields a cardioprotective lipoprotein profile. Here, Valleix et al.reveal a novel ApoC-III variant conferring low plasma ApoC-III concentration and cardioprotection despite renal insufficiency, and, unexpec
Externí odkaz:
https://doaj.org/article/20852c4360d64aac8c27c28e258ec648
Autor:
Sébastien Bender, Maria Victoria Ayala, Vincent Javaugue, Amélie Bonaud, Michel Cogné, Guy Touchard, Arnaud Jaccard, Frank Bridoux, Christophe Sirac
Publikováno v:
Haematologica, Vol 103, Iss 11 (2018)
Externí odkaz:
https://doaj.org/article/2e139dbac2514062848bc315026993d4
Autor:
Sophie Chauvet, Lubka T. Roumenina, Pierre Aucouturier, Maria-Chiara Marinozzi, Marie-Agnès Dragon-Durey, Alexandre Karras, Yahsou Delmas, Moglie Le Quintrec, Dominique Guerrot, Noémie Jourde-Chiche, David Ribes, Pierre Ronco, Frank Bridoux, Véronique Fremeaux-Bacchi
Publikováno v:
Frontiers in Immunology, Vol 9 (2018)
C3 glomerulopathy (C3G) results from acquired or genetic abnormalities in the complement alternative pathway (AP). C3G with monoclonal immunoglobulin (MIg-C3G) was recently included in the spectrum of “monoclonal gammopathy of renal significance.
Externí odkaz:
https://doaj.org/article/45a54c4cddee40a79d7bc8371976ec81
Autor:
Arnaud Jaccard, Raymond L. Comenzo, Parameswaran Hari, Philip N. Hawkins, Murielle Roussel, Pierre Morel, Margaret Macro, Jean-Luc Pellegrin, Estibaliz Lazaro, Dania Mohty, Patrick Mercie, Olivier Decaux, Julian Gillmore, David Lavergne, Frank Bridoux, Ashutosh D. Wechalekar, Christopher P. Venner
Publikováno v:
Haematologica, Vol 99, Iss 9 (2014)
Bortezomib is an active agent in AL amyloidosis and responses to this drug in combination with cyclophosphamide and dexamethasone are both rapid and deep. Here we present an international, multicenter series of 60 patients with Mayo Clinic stage III
Externí odkaz:
https://doaj.org/article/e75c268cc06e42bea163688290dd5c2c
Autor:
Aude Mignot, Frank Bridoux, Antoine Thierry, Shaida Varnous, Myriam Pujo, Annick Delcourt, Jean Marc Gombert, Jean-Michel Goujon, Fréderic Favreau, Guy Touchard, Daniel Herpin, Arnaud Jaccard
Publikováno v:
Haematologica, Vol 93, Iss 3 (2008)
Recurrence in the allograft and progression in other organs increase mortality after cardiac transplantation in AL amyloidosis. Survival may be improved after suppression of monoclonal light chain (LC) production following high dose melphalan and aut
Externí odkaz:
https://doaj.org/article/f92d6176b51649088b8ee8736ab9d9c4